Glutaric aciduria type I: Pathomechanisms of neurodegeneration

Journal of Inherited Metabolic Disease

Volumn 22, Issue 4, 1999, Pages 392-403

  Ullrich, K ^a   Flott Rahmel, B ^b   Schluff, P ^b   Musshoff, U ^b   Das, A ^b   Lucke T ^b   Steinfeld, R ^b   Christensen, E ^b   Jakobs, C ^b   Ludolph, A ^b   Neu, A ^b   Roper R ^b  

^a Universitasklin Hamburg Eppendorf   (Germany)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

3 HYDROXYGLUTARIC ACID; 6 CYANO 7 NITRO 2,3 QUINOXALINEDIONE; ADENOSINE TRIPHOSPHATE; AMPA RECEPTOR; CARRIER PROTEIN; DIZOCILPINE; EXCITOTOXIN; GLUTACONIC ACID; GLUTAMATE DECARBOXYLASE; GLUTAMATE RECEPTOR; GLUTAMATE RECEPTOR AGONIST; GLUTARIC ACID; GLUTARIC ACID DERIVATIVE; GLUTARYL COENZYME A DEHYDROGENASE; GLYCINE; GUANINE NUCLEOTIDE BINDING PROTEIN; KAINIC ACID; MAGNESIUM ION; N METHYL DEXTRO ASPARTIC ACID RECEPTOR; N METHYL DEXTRO ASPARTIC ACID RECEPTOR BLOCKING AGENT; UNCLASSIFIED DRUG;

ANIMAL TISSUE; BRAIN CORTEX; BRAIN MATURATION; BRAIN SLICE; CELL CULTURE; CELL DAMAGE; CELL DENSITY; CONFERENCE PAPER; CONTROLLED STUDY; CORPUS STRIATUM; ELECTROPHYSIOLOGY; ENERGY METABOLISM; ENZYME ACTIVATION; GAS CHROMATOGRAPHY; GLIA CELL; GLUTARIC ACIDURIA TYPE I; HIPPOCAMPUS; HISTOLOGY; IMMUNOHISTOCHEMISTRY; MASS SPECTROMETRY; MEMBRANE CURRENT; METABOLIC DISORDER; NERVE DEGENERATION; NEUROTOXICITY; NEUROTRANSMISSION; NONHUMAN; OOCYTE; PROTEIN EXPRESSION; PROTEIN INTERACTION; RAT; RESPIRATORY CHAIN; SIGNAL TRANSDUCTION; TISSUE LEVEL; XENOPUS LAEVIS;

ANIMALS; CEREBRAL CORTEX; CULTURE TECHNIQUES; GLUTARATES; HIPPOCAMPUS; HUMANS; RATS; RATS, WISTAR; RECEPTORS, N-METHYL-D-ASPARTATE;

EID: 0032969951     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005595921323     Document Type: Conference Paper

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