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Volumn 277, Issue 17, 2002, Pages 14674-14680

Neurodegeneration in methylmalonic aciduria involves inhibition of complex II and the tricarboxylic acid cycle, and synergistically acting excitotoxicity

(10) Okun, Jürgen G a,c Hörster, Friederike a Farkas, Lilla M b Feyh, Patrik a Hinz, Angela b Sauer, Sven a Hoffmann, Georg F b Unsicker, Klaus a Mayatepek, Ertan b Kölker, Stefan a

a Department of Pediatrics (Germany)

b UNIVERSITY OF HEIDELBERG (Germany)

c UNIVERSITY HOSPITAL HEIDELBERG (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CELLS; NEUROLOGY; PATIENT MONITORING; TOXICITY;

TOXIC ORGANIC ACIDS;

BIOCHEMISTRY;

2 METHYL CITRATE; ANTIOXIDANT; CITRIC ACID; EXCITOTOXIN; IONOTROPIC RECEPTOR ANTAGONIST; MALONIC ACID; SUCCINATE DEHYDROGENASE (UBIQUINONE); SUCCINIC ACID; TRICARBOXYLIC ACID; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; BASAL GANGLION; CELL CULTURE; CELL DAMAGE; CITRIC ACID CYCLE; CONCENTRATION RESPONSE; CONTROLLED STUDY; CORPUS STRIATUM; CYTOTOXICITY; HEART MITOCHONDRION; METHYLMALONIC ACIDURIA; NERVE CELL LESION; NERVE DEGENERATION; NEUROPATHOLOGY; NEUROTOXICITY; NONHUMAN; PATHOGENESIS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RAT; RESPIRATORY CHAIN; TIME;

ANIMALS; CELLS, CULTURED; CITRATES; CITRIC ACID CYCLE; CORPUS STRIATUM; ELECTRON TRANSPORT COMPLEX II; FEMALE; MALONATES; METABOLISM, INBORN ERRORS; METHYLMALONIC ACID; MULTIENZYME COMPLEXES; N-METHYLASPARTATE; NEURONS; OXIDOREDUCTASES; PREGNANCY; RATS; RATS, WISTAR; SUCCINATE DEHYDROGENASE;

ANIMALIA; BOVINAE;

EID: 0037177804 PISSN: 00219258 EISSN: None Source Type: Journal
DOI: 10.1074/jbc.M200997200 Document Type: Article

Times cited : (147)

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