Maturation-dependent neurotoxicity of 3-hydroxyglutaric and glutaric acids in vitro: A new pathophysiologic approach to glutaryl-CoA dehydrogenase deficiency

Pediatric Research

Volumn 47, Issue 4, 2000, Pages 495-503

  Klker, Stefan ^a   Ahlemeyer, Barbara ^a   Krieglstein, Josef ^a   Hoffmann, Georg F ^b  

^a PHILIPPS UNIVERSITY MARBURG   (Germany)

^b UNIVERSITY OF HEIDELBERG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA AMINO 3 HYDROXY 5 METHYL 4 ISOXAZOLEPROPIONIC ACID; GLUTARIC ACID DERIVATIVE; GLUTARYL COENZYME A DEHYDROGENASE; METABOTROPIC RECEPTOR; N METHYL DEXTRO ASPARTIC ACID RECEPTOR; NEUROTRANSMITTER;

AGE; ANIMAL CELL; ARTICLE; BRAIN DISEASE; BRAIN INJURY; BRAIN NECROSIS; CELL VIABILITY; CONTROLLED STUDY; GENE EXPRESSION; METABOLIC DISORDER; NEUROLOGIC DISEASE; NEUROTOXICITY; NEUROTRANSMISSION; NONHUMAN; ONTOGENY; PRIORITY JOURNAL;

ANIMALS; ANTIBODIES; BRAIN DISEASES, METABOLIC, INBORN; CELLS, CULTURED; CHICK EMBRYO; DIZOCILPINE MALEATE; GLUTARATES; GLUTARYL-COA DEHYDROGENASE; NEURONS; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; PIPERIDINES; RATS;

EID: 0342424353     PISSN: 00313998     EISSN: 15300447     Source Type: Journal    
DOI: 10.1203/00006450-200004000-00014     Document Type: Article

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