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note
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We thank T. Siddique (for tissue samples from the human cases of FALS described in Fig. 1), M. Lee, P. Wong, A. Markowska, G. Thinakaran, N. Jenkins, N. Copeland, D. Cleveland, C. Ross, G. Schilling, C. Pardo, and J. Rothstein for their contributions to some of the work mentioned in this text. Supported by grants from the U.S. Public Health Service (NIH NS 20471, NS 10580, NS 37145, AG 05146, AG 07914, AG 14248), as well as the Metropolitan Life Foundation, the Adler Foundation, the Alzheimer's Association (Temple Award, Zenith Award), the DeVelbiss fund, the American Health Assistance Foundation, the Amyotrophic Lateral Sclerosis Association, the Hereditary Disease Foundation, and the Huntington's Disease Society of America.
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