A low expressor line of transgenic mice carrying a mutant human Cu,Zn superoxide dismutase (SOD1) gene develops pathological changes that most closely resemble those in human amyotrophic lateral sclerosis

Acta Neuropathologica

Volumn 93, Issue 6, 1997, Pages 537-550

  Dal Canto, Mauro C ^a   Gurney, Mark E ^b  

^a NORTHWESTERN UNIVERSITY   (United States)

^b PFIZER INC   (United States)

Author keywords

Amyotrophic lateral sclerosis; Cu,Zn superoxide dismutase; Transgenic mice

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL TISSUE; ANTERIOR HORN CELL; ARTICLE; LEWY BODY; MISSENSE MUTATION; MOTONEURON; MOUSE; NERVE CELL DEGENERATION; NEUROPATHOLOGY; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; DISEASE MODELS, ANIMAL; HUMANS; MICE; MICE, TRANSGENIC; MUTATION; SUPEROXIDE DISMUTASE;

EID: 0030916609     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010050650     Document Type: Article

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