The roles of the ubiquitin-proteasome and autophagy-lysosome pathways in Huntington's disease and related conditions

Clinical Neuroscience Research

Volumn 3, Issue 3, 2003, Pages 141-148

  Ravikumar, Brinda ^a   Sarkar, Sovan ^a   Berger, Zdenek ^a   Rubinsztein, David C ^a  

^a ADDENBROOKE S HOSPITAL   (United Kingdom)

Author keywords

Autophagy; Huntington's disease; Lysosome; Oculopharyngeal muscular dystrophy; Polyglutamine disease; Proteasome; Ubiquitin

Indexed keywords

ADENINE; CYTOSINE; GUANINE; HUNTINGTIN; MUTANT PROTEIN; POLYGLUTAMINE; PROTEASOME; UBIQUITIN;

AUTOPHAGY; CELL INCLUSION; CELL NUCLEUS; CLEARANCE; CYTOPATHOLOGY; DENTATORUBROPALLIDOLUYSIAN ATROPHY; EXON; GENE MUTATION; GENETIC ANALYSIS; HUMAN; HUNTINGTON CHOREA; KENNEDY DISEASE; LYSOSOME; NERVE CELL; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN FUNCTION; REVIEW; SPINOCEREBELLAR DEGENERATION; TRINUCLEOTIDE REPEAT;

EID: 0141493680     PISSN: 15662772     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1566-2772(03)00056-2     Document Type: Article

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