Molecular chaperones enhance the degradation of expanded polyglutamine repeat androgen receptor in a cellular model of spinal and bulbar muscular atrophy

Human Molecular Genetics

Volumn 11, Issue 5, 2002, Pages 515-523

  Bailey, Christine K ^a,b   Andriola, Isabella F M ^a   Kampinga, Harm H ^c   Merry, Diane E ^a  

^a THOMAS JEFFERSON UNIVERSITY   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c UNIVERSITY OF GRONINGEN   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ADENINE; ANDROGEN RECEPTOR; CHAPERONE; CYTOSINE; GLUTAMINE; HEAT SHOCK PROTEIN 40; HEAT SHOCK PROTEIN 70; POLYGLUTAMINE; PROTEASOME;

ANIMAL CELL; ARTICLE; CELL CULTURE; CELL NUCLEUS INCLUSION BODY; CONTROLLED STUDY; CYTOTOXICITY; DEGENERATIVE DISEASE; DISEASE MODEL; EXON; GENE OVEREXPRESSION; GENE TARGETING; GENETIC CODE; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN DEGRADATION; QUANTITATIVE ANALYSIS; RECEPTOR GENE; SPINAL MUSCULAR ATROPHY; TRINUCLEOTIDE REPEAT;

ANIMALIA;

EID: 0036501074     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/11.5.515     Document Type: Article

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