Aggregate formation inhibits proteasomal degradation of polyglutamine proteins

Human Molecular Genetics

Volumn 11, Issue 22, 2002, Pages 2689-2700

  Weinhofer, Isabelle ^a   Forss Petter, Sonja ^a   Žigman, Mihaela ^a   Berger, Johannes ^a  

^a UNIVERSITY OF VIENNA   (Austria)

Author keywords

[No Author keywords available]

Indexed keywords

MUTANT PROTEIN; POLYGLUTAMINE; PROTEASOME; UBIQUITIN;

ARTICLE; CELL NUCLEUS INCLUSION BODY; CONTROLLED STUDY; CYTOTOXICITY; DEGENERATIVE DISEASE; ENZYME SUBSTRATE; HUMAN; HUMAN CELL; HUMAN TISSUE; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; PROTEIN TARGETING; SIGNAL TRANSDUCTION; SOLUBILITY;

BIODEGRADATION, ENVIRONMENTAL; CYSTEINE ENDOPEPTIDASES; DRUG STABILITY; GREEN FLUORESCENT PROTEINS; HELA CELLS; HUMANS; LUMINESCENT PROTEINS; MACROMOLECULAR SUBSTANCES; MULTIENZYME COMPLEXES; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDES; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN SORTING SIGNALS; RECOMBINANT FUSION PROTEINS; REPETITIVE SEQUENCES, AMINO ACID; SOLUBILITY; TRANSFECTION; UBIQUITIN;

EID: 0037108725     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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