A rat model of ataxia-telangiectasia: Evidence for a neurodegenerative phenotype

Human Molecular Genetics

Volumn 26, Issue 1, 2017, Pages 109-123

  Quek, Hazel ^a,b   Luff, John ^a   Cheung, Kageen ^a,b   Kozlov, Sergei ^a   Gatei, Magtouf ^a   Lee, C Soon ^c   Bellingham, Mark C ^a   Noakes, Peter G ^a   Lim, Yi Chieh ^b   Barnett, Nigel L ^a,d,e   Dingwall, Steven ^a,b   Wolvetang, Ernst ^a   Mashimo, Tomoji ^f   Roberts, Tara L ^a,b,c   Lavin, Martin F ^a  

^a UNIVERSITY OF QUEENSLAND   (Australia)

^b QIMR BERGHOFER MEDICAL RESEARCH INSTITUTE   (Australia)

^c UNIVERSITY OF WESTERN SYDNEY   (Australia)

^d QUEENSLAND EYE INSTITUTE   (Australia)

^e QUEENSLAND UNIVERSITY OF TECHNOLOGY   (Australia)

^f OSAKA UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIINFLAMMATORY AGENT; ATM PROTEIN; BETAMETHASONE;

ANIMAL; ATAXIA TELANGIECTASIA; BRAIN; CELL CULTURE; COMPLICATION; DISEASE MODEL; DRUG EFFECTS; HUMAN; INFLAMMATION; METABOLISM; MICROGLIA; MUTANT RAT STRAIN; NERVE CELL; NEURODEGENERATIVE DISEASES; PATHOLOGY; PHENOTYPE; PHYSIOLOGY; RAT;

ANIMALS; ANTI-INFLAMMATORY AGENTS; ATAXIA TELANGIECTASIA; ATAXIA TELANGIECTASIA MUTATED PROTEINS; BETAMETHASONE; BRAIN; CELLS, CULTURED; DISEASE MODELS, ANIMAL; HUMANS; INFLAMMATION; MICROGLIA; NEURODEGENERATIVE DISEASES; NEURONS; PHENOTYPE; RATS; RATS, MUTANT STRAINS;

EID: 85030442082     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddw371     Document Type: Article

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