Intrinsic mitochondrial dysfunction in ATM-deficient lymphoblastoid cells

Human Molecular Genetics

Volumn 16, Issue 18, 2007, Pages 2154-2164

  Ambrose, Mark ^a   Goldstine, Jimena V ^a   Gatti, Richard A ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATM PROTEIN; CELL NUCLEUS DNA; DNA DIRECTED DNA POLYMERASE GAMMA; DNA TOPOISOMERASE; MANGANESE SUPEROXIDE DISMUTASE; MITOCHONDRIAL DNA; PEROXIREDOXIN; PEROXIREDOXIN 3; REACTIVE OXYGEN METABOLITE; SMALL INTERFERING RNA; THIOCTIC ACID; UNCLASSIFIED DRUG;

ARTICLE; ATAXIA TELANGIECTASIA; CELL STRUCTURE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DNA REPAIR; GENE EXPRESSION REGULATION; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; LYMPHOBLASTOID CELL; MEMBRANE POTENTIAL; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; OXIDATIVE STRESS; PHENOTYPIC VARIATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN TARGETING; SCAVENGING SYSTEM; UPREGULATION; WILD TYPE;

ANTIOXIDANTS; ATAXIA TELANGIECTASIA; CELL CYCLE PROTEINS; CELL LINE; DNA-BINDING PROTEINS; HUMANS; MEMBRANE POTENTIAL, MITOCHONDRIAL; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MITOCHONDRIAL PROTEINS; OXIDATIVE STRESS; OXYGEN CONSUMPTION; PROTEIN-SERINE-THREONINE KINASES; THIOCTIC ACID; TUMOR SUPPRESSOR PROTEINS;

ATAXIA TELANGIECTASIA;

EID: 34548430918     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddm166     Document Type: Article

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