Partial defects of T-cell development associated with poor T-cell function

Journal of Allergy and Clinical Immunology

Volumn 131, Issue 5, 2013, Pages 1297-1305

  Notarangelo, Luigi D ^a  

^a BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

autoimmunity; Immunodeficiency; T cell development; thymus; tolerance

Indexed keywords

CARRIER PROTEIN; CD4 ANTIGEN; CORONIN 1A; DEDICATOR OF CYTOKINESIS 8; GUANINE NUCLEOTIDE EXCHANGE FACTOR; INTERLEUKIN 2; KHELLIN; MACROPHAGE STIMULATING 1 PROTEIN; MAGNESIUM TRANSPORTER 1; PROTEIN KINASE LCK; PROTEIN KINASE ZAP 70; PROTEIN SERINE THREONINE KINASE; RAS PROTEIN; STROMAL INTERACTION MOLECULE 1; T LYMPHOCYTE RECEPTOR ALPHA CHAIN; T LYMPHOCYTE RECEPTOR BETA CHAIN; UNCLASSIFIED DRUG;

ARTICLE; CELL FUNCTION; CELL MATURATION; COMBINED IMMUNODEFICIENCY; CYTOKINESIS; GENE MUTATION; HUMAN; HUMORAL IMMUNITY; IMMUNE DYSREGULATION; INTRACELLULAR SIGNALING; LOSS OF FUNCTION MUTATION; LYMPHOCYTOPENIA; MACROPHAGE; NONHUMAN; OMENN SYNDROME; PRIORITY JOURNAL; PROTEIN DEFECT; PROTEIN DEFICIENCY; SEVERE COMBINED IMMUNODEFICIENCY; STRUCTURAL HOMOLOGY; T LYMPHOCYTE;

CELL DIFFERENTIATION; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; SEVERE COMBINED IMMUNODEFICIENCY; T-LYMPHOCYTES;

EID: 84876944936     PISSN: 00916749     EISSN: 10976825     Source Type: Journal    
DOI: 10.1016/j.jaci.2013.01.020     Document Type: Article

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