Defective expression of p561ck in an infant with severe combined immunodeficiency

Journal of Clinical Investigation

Volumn 102, Issue 2, 1998, Pages 421-429

  Goldman, Frederick D ^a,c   Ballas, Zuhair K ^a   Schutte, Brian C ^a   Kemp, John ^a   Hollenback, Clay ^a   Noraz, Nelly ^b   Taylor, Naomi ^b  

^a UNIVERSITY OF IOWA   (United States)

^b INSTITUT DE GÉNÉTIQUE MOLÉCULAIRE DE MONTPELLIER   (France)

^c UNIVERSITY OF IOWA HOSPITALS AND CLINICS   (United States)

Author keywords

Lck; Severe combined immune deficiency; Signal transduction; T lymphocytes; Tyrosine kinases

Indexed keywords

CD28 ANTIGEN; CD3 ANTIGEN; CD69 ANTIGEN; LEUKOCYTE ANTIGEN; LYMPHOCYTE ANTIGEN RECEPTOR; PROTEIN KINASE LCK; T LYMPHOCYTE ANTIGEN; TYROSINE;

ANTIGEN EXPRESSION; ARTICLE; CALCIUM MOBILIZATION; COMBINED IMMUNODEFICIENCY; CONTROLLED STUDY; HUMAN; HUMAN CELL; LYMPHOCYTOPENIA; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN PHOSPHORYLATION; BIOSYNTHESIS; BLOOD; CASE REPORT; CD4 CD8 RATIO; CD4+ T LYMPHOCYTE; CELL DIVISION; CYTOLOGY; ENZYME SPECIFICITY; ENZYMOLOGY; EXON; GENETICS; INFANT; MALE; METABOLISM; PHENOTYPE; PHOSPHORYLATION; T LYMPHOCYTE;

ANTIGENS, CD; ANTIGENS, CD3; ANTIGENS, DIFFERENTIATION, T-LYMPHOCYTE; CD4-CD8 RATIO; CD4-POSITIVE T-LYMPHOCYTES; CELL DIVISION; EXONS; HUMANS; INFANT; LYMPHOCYTE SPECIFIC PROTEIN TYROSINE KINASE P56(LCK); LYMPHOPENIA; MALE; PHENOTYPE; PHOSPHORYLATION; RECEPTORS, ANTIGEN, T-CELL; SEVERE COMBINED IMMUNODEFICIENCY; SUBSTRATE SPECIFICITY; T-LYMPHOCYTES; TYROSINE;

EID: 0032527136     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI3205     Document Type: Article

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