-
1
-
-
35448950741
-
Cardiofaciocutaneous (CFC) syndrome associated with muscular coenzyme Q10 deficiency
-
Aeby A, Sznajer Y, Cave H, et al. 2007. Cardiofaciocutaneous (CFC) syndrome associated with muscular coenzyme Q10 deficiency. J Inherit Metab Dis 30:827.
-
(2007)
J Inherit Metab Dis
, vol.30
, pp. 827
-
-
Aeby, A.1
Sznajer, Y.2
Cave, H.3
-
2
-
-
37749039120
-
dAtaxin-2 mediates expanded Ataxin-1-induced neurodegeneration in a Drosophila model of SCA1
-
Al-Ramahi I, Perez AM, Lim J, et al. 2007. dAtaxin-2 mediates expanded Ataxin-1-induced neurodegeneration in a Drosophila model of SCA1. PLoS Genet 3:e234.
-
(2007)
PLoS Genet
, vol.3
-
-
Al-Ramahi, I.1
Perez, A.M.2
Lim, J.3
-
3
-
-
0027377058
-
Involvement of mitochondrial contact sites in the subcellular compartmentalization of phospholipid biosynthetic enzymes
-
Ardail D, Gasnier F, Lerme F, et al. 1993. Involvement of mitochondrial contact sites in the subcellular compartmentalization of phospholipid biosynthetic enzymes. J Biol Chem 268:25985-25992. (Pubitemid 23358220)
-
(1993)
Journal of Biological Chemistry
, vol.268
, Issue.34
, pp. 25985-25992
-
-
Ardail, D.1
Gasnier, F.2
Lerme, F.3
Simonot, C.4
Louisot, P.5
Gateau-Roesch, O.6
-
5
-
-
0031793773
-
Molecular genetics of the genus Paracoccus: Metabolically versatile bacteria with bioenergetic flexibility
-
Baker SC, Ferguson SJ, Ludwig B, et al. 1998. Molecular genetics of the genus Paracoccus: metabolically versatile bacteria with bioenergetic flexibility. Microbiol Mol Biol Rev 62:1046-1078.
-
(1998)
Microbiol Mol Biol Rev
, vol.62
, pp. 1046-1078
-
-
Baker, S.C.1
Ferguson, S.J.2
Ludwig, B.3
-
6
-
-
34547096741
-
Single particle analysis confirms distal location of subunits NuoL and NuoM in Escherichia coli complex I
-
Baranova EA, Morgan DJ, Sazanor LA. 2007. Single particle analysis confirms distal location of subunits NuoL and NuoM in Escherichia coli complex I. J Struct Biol 159:238-242.
-
(2007)
J Struct Biol
, vol.159
, pp. 238-242
-
-
Baranova, E.A.1
Morgan, D.J.2
Sazanor, L.A.3
-
7
-
-
0037660510
-
Yeast models of human mitochondrial diseases
-
Barrientos A. 2003. Yeast models of human mitochondrial diseases. IUBMB Life 55:83-95.
-
(2003)
IUBMB Life
, vol.55
, pp. 83-95
-
-
Barrientos, A.1
-
8
-
-
0020974404
-
An X-linked mitochondrial disease affecting cardiac muscle, skeletal muscle and neutrophil leucocytes
-
Barth PG, Scholte HR, Berden JA, et al. 1983. An X-linked mitochondrial disease affecting cardiac muscle, skeletal muscle and neutrophil leucocytes. J Neurol Sci 62:327-355.
-
(1983)
J Neurol Sci
, vol.62
, pp. 327-355
-
-
Barth, P.G.1
Scholte, H.R.2
Berden, J.A.3
-
10
-
-
3142686745
-
The BDGP gene disruption project: Single transposon insertions associated with 40% of Drosophila genes
-
Bellen HJ, Levis RW, Liao G, et al. 2004. The BDGP gene disruption project: single transposon insertions associated with 40% of Drosophila genes. Genetics 167:761-781.
-
(2004)
Genetics
, vol.167
, pp. 761-781
-
-
Bellen, H.J.1
Levis, R.W.2
Liao, G.3
-
11
-
-
0015227656
-
From the gene to behavior
-
Benzer S. 1971. From the gene to behavior. JAMA 218:1015-1022.
-
(1971)
JAMA
, vol.218
, pp. 1015-1022
-
-
Benzer, S.1
-
12
-
-
66449086494
-
Identification of a cardiolipin-specific phospholipase encoded by the gene CLD1 (YGR110W) in yeast
-
Beranek A, Rechberger G, Knauer H, et al. 2009. Identification of a cardiolipin-specific phospholipase encoded by the gene CLD1 (YGR110W) in yeast. J Biol Chem 284:11572-11578.
-
(2009)
J Biol Chem
, vol.284
, pp. 11572-11578
-
-
Beranek, A.1
Rechberger, G.2
Knauer, H.3
-
14
-
-
0029963145
-
A novel X-linked gene, G4.5. is responsible for Barth syndrome
-
DOI 10.1038/ng0496-385
-
Bione S, D'Adamo P, Maestrini E, et al. 1996. A novel X-linked gene, G4.5. is responsible for Barth syndrome. Nat Genet 12:385-389. (Pubitemid 26106250)
-
(1996)
Nature Genetics
, vol.12
, Issue.4
, pp. 385-389
-
-
Bione, S.1
D'Adamo, P.2
Maestrini, E.3
Gedeon, A.K.4
Bolhuis, P.A.5
Toniolo, D.6
-
15
-
-
0026768816
-
Genetic approaches to the study of mitochondrial biogenesis in yeast
-
Bolotin-Fukuhara M, Grivell LA. 1992. Genetic approaches to the study of mitochondrial biogenesis in yeast. Antonie van Leeuwenhoek 62:131-153.
-
(1992)
Antonie Van Leeuwenhoek
, vol.62
, pp. 131-153
-
-
Bolotin-Fukuhara, M.1
Grivell, L.A.2
-
16
-
-
70350560063
-
Complete mitochondrial genome sequences of three Nakaseomyces species reveal invasion by palindromic GC clusters and considerable size expansion
-
Bouchier C, Ma L, Creno S, et al. 2009. Complete mitochondrial genome sequences of three Nakaseomyces species reveal invasion by palindromic GC clusters and considerable size expansion. FEMS Yeast Res 9: 1283-1292.
-
(2009)
FEMS Yeast Res
, vol.9
, pp. 1283-1292
-
-
Bouchier, C.1
Ma, L.2
Creno, S.3
-
17
-
-
0027160708
-
Targeted gene expression as a means of altering cell fates and generating dominant phenotypes
-
Brand AH, Perrimon N. 1993. Targeted gene expression as a means of altering cell fates and generating dominant phenotypes. Development 118:401-415.
-
(1993)
Development
, vol.118
, pp. 401-415
-
-
Brand, A.H.1
Perrimon, N.2
-
18
-
-
33746329868
-
Energy converting NADH:quinone oxidoreductase (complex I)
-
DOI 10.1146/annurev.biochem.75.103004.142539
-
Brandt U. 2006. Energy converting NADH:quinone oxidoreductase (complex I). Annu Rev Biochem 75:69-92. (Pubitemid 44118026)
-
(2006)
Annual Review of Biochemistry
, vol.75
, pp. 69-92
-
-
Brandt, U.1
-
19
-
-
0016063911
-
The genetics of Caenorhabditis elegans
-
Brenner S. 1974. The genetics of Caenorhabditis elegans. Genetics 77:71-94.
-
(1974)
Genetics
, vol.77
, pp. 71-94
-
-
Brenner, S.1
-
20
-
-
0028882573
-
Import of phosphatidylethanolamine for the assembly of rat brain mitochondrial membranes
-
Camici O, Corazzi L. 1995. Import of phosphatidylethanolamine for the assembly of rat brain mitochondrial membranes. J Membr Biol 148:169-176.
-
(1995)
J Membr Biol
, vol.148
, pp. 169-176
-
-
Camici, O.1
Corazzi, L.2
-
22
-
-
33751574953
-
Bovine complex I is a complex of 45 different subunits
-
Carroll J, Fearnley IM, Skehel JM, et al. 2006. Bovine complex I is a complex of 45 different subunits. J Biol Chem 281:32724-32727.
-
(2006)
J Biol Chem
, vol.281
, pp. 32724-32727
-
-
Carroll, J.1
Fearnley, I.M.2
Skehel, J.M.3
-
23
-
-
32544439499
-
Mitochondrial encephalomyopathy in Drosophila
-
Celotto AM, Frank AC, McGrath SW, et al. 2006. Mitochondrial encephalomyopathy in Drosophila. J Neurosci 26:810-820.
-
(2006)
J Neurosci
, vol.26
, pp. 810-820
-
-
Celotto, A.M.1
Frank, A.C.2
McGrath, S.W.3
-
24
-
-
68749112707
-
Importing mitochondrial proteins: Machineries and mechanisms
-
Chacinska A, Koehler CM, Milenkovic D, et al. 2009. Importing mitochondrial proteins: machineries and mechanisms. Cell 138:628-644.
-
(2009)
Cell
, vol.138
, pp. 628-644
-
-
Chacinska, A.1
Koehler, C.M.2
Milenkovic, D.3
-
25
-
-
0031450907
-
The NuoI subunit of the Rhodobacter capsulatus respiratory complex I (equivalent to the bovine TYKY subunit) is required for proper assembly of the membranous and peripheral domains of the enzyme
-
Chevallet M, Dupuis A, Lunardi J, et al. 1997. The NuoI subunit of the Rhodobacter capsulatus respiratory complex I (equivalent to the bovine TYKY subunit) is required for proper assembly of the membranous and peripheral domains of the enzyme. Eur J Biochem 250:451-458.
-
(1997)
Eur J Biochem
, vol.250
, pp. 451-458
-
-
Chevallet, M.1
Dupuis, A.2
Lunardi, J.3
-
26
-
-
33846272138
-
Role of cardiolipin alterations in mitochondrial dysfunction and disease
-
DOI 10.1152/ajpcell.00243.2006
-
Chicco AJ, Sparagna GC. 2007. Role of cardiolipin alterations in mitochondrial dysfunction and disease. Am J Physiol Cell Physiol 292:C33-C44. (Pubitemid 46115119)
-
(2007)
American Journal of Physiology - Cell Physiology
, vol.292
, Issue.1
-
-
Chicco, A.J.1
Sparagna, G.C.2
-
27
-
-
68749097261
-
Application of dual-genome oligonucleotidearray- Based comparative genomic hybridization to the molecular diagnosis of mitochondrial DNA deletion and depletion syndromes
-
Chinault AC, Shaw CA, Brundage EK, et al. 2009. Application of dual-genome oligonucleotidearray- based comparative genomic hybridization to the molecular diagnosis of mitochondrial DNA deletion and depletion syndromes. Genet Med 11:518-526.
-
(2009)
Genet Med
, vol.11
, pp. 518-526
-
-
Chinault, A.C.1
Shaw, C.A.2
Brundage, E.K.3
-
28
-
-
33745095012
-
Mitochondrial one-carbon metabolism is adapted to the specific needs of yeast, plants and mammals
-
Christensen KE, MacKenzie RE. 2006. Mitochondrial one-carbon metabolism is adapted to the specific needs of yeast, plants and mammals. Bioessays 28:595-605.
-
(2006)
Bioessays
, vol.28
, pp. 595-605
-
-
Christensen, K.E.1
MacKenzie, R.E.2
-
29
-
-
33745589773
-
Drosophila pink1 is required for mitochondrial function and interacts genetically with parkin
-
Clark IE, Dodson MW, Jiang C, et al. 2006. Drosophila pink1 is required for mitochondrial function and interacts genetically with parkin. Nature 441:1162-1166.
-
(2006)
Nature
, vol.441
, pp. 1162-1166
-
-
Clark, I.E.1
Dodson, M.W.2
Jiang, C.3
-
30
-
-
0009453969
-
Expression of green fluorescent protein from a recoded gene inserted into Saccharomyces cerevisiae mitochondrial DNA
-
Cohen JS, Fox TD. 2001. Expression of green fluorescent protein from a recoded gene inserted into Saccharomyces cerevisiae mitochondrial DNA. Mitochondrion 1:181-189.
-
(2001)
Mitochondrion
, vol.1
, pp. 181-189
-
-
Cohen, J.S.1
Fox, T.D.2
-
31
-
-
0034122608
-
Maintenance and integrity of the mitochondrial genome: A plethora of nuclear genes in the budding yeast
-
Contamine V, Picard M. 2000. Maintenance and integrity of the mitochondrial genome: a plethora of nuclear genes in the budding yeast. Microbiol Mol Biol Rev 64:281-315. (Pubitemid 30412676)
-
(2000)
Microbiology and Molecular Biology Reviews
, vol.64
, Issue.2
, pp. 281-315
-
-
Contamine, V.1
Picard, M.2
-
32
-
-
33750976371
-
Progress towards understanding disease mechanisms in small vertebrate models of neuronal ceroid lipofuscinosis
-
Cooper JD, Russell C, Mitchiso HM. 2006. Progress towards understanding disease mechanisms in small vertebrate models of neuronal ceroid lipofuscinosis. Biochim Biophys Acta 1762:873-889.
-
(2006)
Biochim Biophys Acta
, vol.1762
, pp. 873-889
-
-
Cooper, J.D.1
Russell, C.2
Mitchiso, H.M.3
-
33
-
-
0344966647
-
An association between mitochondria and the endoplasmic reticulum in cells of the pseudobranch gland of a teleost
-
Copeland DE, Dalton AJ. 1959. An association between mitochondria and the endoplasmic reticulum in cells of the pseudobranch gland of a teleost. J Biophys Biochem Cytol 5:393-396.
-
(1959)
J Biophys Biochem Cytol
, vol.5
, pp. 393-396
-
-
Copeland, D.E.1
Dalton, A.J.2
-
34
-
-
0003499443
-
-
Cold Spring Harbor, NY: Cold Spring Harbor Laboratory Press
-
Demerec M. 1994. Biology of Drosophila. Cold Spring Harbor, NY: Cold Spring Harbor Laboratory Press.
-
(1994)
Biology of Drosophila
-
-
Demerec, M.1
-
35
-
-
0024404324
-
Pyrimidine biosynthesis in Saccharomyces cerevisiae: The ura2 cluster gene, its multifunctional enzyme product, and other structural or regulatory genes involved in de novo UMP synthesis
-
Denis-Duphil M. 1989. Pyrimidine biosynthesis in Saccharomyces cerevisiae: the ura2 cluster gene, its multifunctional enzyme product, and other structural or regulatory genes involved in de novo UMP synthesis. Biochem Cell Biol 67:612-631.
-
(1989)
Biochem Cell Biol
, vol.67
, pp. 612-631
-
-
Denis-Duphil, M.1
-
36
-
-
34447530305
-
A genome-wide transgenic RNAi library for conditional gene inactivation in Drosophila
-
Dietzl G, Chen D, Schnorrer F, et al. 2007. A genome-wide transgenic RNAi library for conditional gene inactivation in Drosophila. Nature 448:151-156.
-
(2007)
Nature
, vol.448
, pp. 151-156
-
-
Dietzl, G.1
Chen, D.2
Schnorrer, F.3
-
37
-
-
0037147103
-
Rates of behavior and aging specified by mitochondrial function during development
-
Dillin A, Hsu AL, Arantes-Oliveira N, et al. 2002. Rates of behavior and aging specified by mitochondrial function during development. Science 298:2398-2401.
-
(2002)
Science
, vol.298
, pp. 2398-2401
-
-
Dillin, A.1
Hsu, A.L.2
Arantes-Oliveira, N.3
-
39
-
-
0037972522
-
Mitochondrial respiratory- Chain diseases
-
DiMauro S, Schon EA. 2003. Mitochondrial respiratory- chain diseases. N Engl J Med 348:2656-2668.
-
(2003)
N Engl J Med
, vol.348
, pp. 2656-2668
-
-
DiMauro, S.1
Schon, E.A.2
-
40
-
-
0036198860
-
Genetic basis of mitochondrial function and morphology in Saccharomyces cerevisiae
-
Dimmer KS, Fritz S, Fuchs F, et al. 2002. Genetic basis of mitochondrial function and morphology in Saccharomyces cerevisiae. Mol Biol Cell 13:847-853.
-
(2002)
Mol Biol Cell
, vol.13
, pp. 847-853
-
-
Dimmer, K.S.1
Fritz, S.2
Fuchs, F.3
-
41
-
-
76049115685
-
Mitochondrial respiratory chain dysfunction variably increases oxidant stress in Caenorhabditis elegans
-
Dingley S, Polyak E, Lightfoot R, et al. 2010. Mitochondrial respiratory chain dysfunction variably increases oxidant stress in Caenorhabditis elegans. Mitochondrion 10:125-136.
-
(2010)
Mitochondrion
, vol.10
, pp. 125-136
-
-
Dingley, S.1
Polyak, E.2
Lightfoot, R.3
-
43
-
-
77952979824
-
The architecture of respiratory complex I
-
Efremov RG, Baradaran R, Sazanor LA. 2010. The architecture of respiratory complex I. Nature 465:441-445.
-
(2010)
Nature
, vol.465
, pp. 441-445
-
-
Efremov, R.G.1
Baradaran, R.2
Sazanor, L.A.3
-
44
-
-
0035157544
-
Genome-wide responses to mitochondrial dysfunction
-
Epstein CB, Waddle JA, Hale WT, et al. 2001. Genome-wide responses to mitochondrial dysfunction. Mol Biol Cell 12:297-308.
-
(2001)
Mol Biol Cell
, vol.12
, pp. 297-308
-
-
Epstein, C.B.1
Waddle, J.A.2
Hale, W.T.3
-
45
-
-
33747174906
-
Mitochondrial complex I function modulates volatile anesthetic sensitivity in C. elegans
-
Falk MJ, Kayser EB, Morgan PG, et al. 2006. Mitochondrial complex I function modulates volatile anesthetic sensitivity in C. elegans. Curr Biol 16:1641-1645.
-
(2006)
Curr Biol
, vol.16
, pp. 1641-1645
-
-
Falk, M.J.1
Kayser, E.B.2
Morgan, P.G.3
-
46
-
-
68949158950
-
Subcomplex Ilambda specifically controls integrated mitochondrial functions in Caenorhabditis elegans
-
Falk MJ, Rosenjack JR, Polyak E, et al. 2009. Subcomplex Ilambda specifically controls integrated mitochondrial functions in Caenorhabditis elegans. PLoS One 4:e6607.
-
(2009)
PLoS One
, vol.4
-
-
Falk, M.J.1
Rosenjack, J.R.2
Polyak, E.3
-
47
-
-
40849113097
-
Metabolic pathway profiling of mitochondrial respiratory chain mutants in C. elegans
-
Falk MJ, Zhang Z, Rosenjack JR, et al. 2008. Metabolic pathway profiling of mitochondrial respiratory chain mutants in C. elegans. Mol Genet Metab 93:388-397.
-
(2008)
Mol Genet Metab
, vol.93
, pp. 388-397
-
-
Falk, M.J.1
Zhang, Z.2
Rosenjack, J.R.3
-
48
-
-
0037441390
-
External alternative NADH dehydrogenase of Saccharomyces cerevisiae: A potential source of superoxide
-
DOI 10.1016/S0891-5849(02)01328-X
-
Fang J, Beattie DS. 2003. External alternative NADH dehydrogenase of Saccharomyces cerevisiae: a potential source of superoxide. Free Radic Biol Med 34:478-488. (Pubitemid 36140172)
-
(2003)
Free Radical Biology and Medicine
, vol.34
, Issue.4
, pp. 478-488
-
-
Fang, J.1
Beattie, D.S.2
-
49
-
-
0033118981
-
CLK-1 controls respiration, behavior and aging in the nematode Caenorhabditis elegans
-
Felkai S, Ewbank JJ, Lemieux J, et al. 1999. CLK-1 controls respiration, behavior and aging in the nematode Caenorhabditis elegans. EMBO J 18:1783-1792. (Pubitemid 29158522)
-
(1999)
EMBO Journal
, vol.18
, Issue.7
, pp. 1783-1792
-
-
Felkai, S.1
Ewbank, J.J.2
Lemieux, J.3
Labbe, J.-C.4
Brown, G.G.5
Hekimi, S.6
-
50
-
-
0035515923
-
Mitochondrial electron transport is a key determinant of life span in Caenorhabditis elegans
-
Feng J, Bussiere F, Hekimi S. 2001. Mitochondrial electron transport is a key determinant of life span in Caenorhabditis elegans. Dev Cell 1:633-644.
-
(2001)
Dev Cell
, vol.1
, pp. 633-644
-
-
Feng, J.1
Bussiere, F.2
Hekimi, S.3
-
51
-
-
33746384132
-
Metabolic disruption in Drosophila bang-sensitive seizure mutants
-
Fergestad T, Bostwick B, Ganetzky B. 2006. Metabolic disruption in Drosophila bang-sensitive seizure mutants. Genetics 173:1357-1364.
-
(2006)
Genetics
, vol.173
, pp. 1357-1364
-
-
Fergestad, T.1
Bostwick, B.2
Ganetzky, B.3
-
52
-
-
77649085555
-
Gene expression in a Drosophila model of mitochondrial disease
-
Fernandez-Ayala DJ, Chen S, Kemppainen E, et al. 2010. Gene expression in a Drosophila model of mitochondrial disease. PLoS One 5:e8549.
-
(2010)
PLoS One
, vol.5
-
-
Fernandez-Ayala, D.J.1
Chen, S.2
Kemppainen, E.3
-
53
-
-
0034597833
-
Identification of genes that modify ataxin-1-induced neurodegeneration
-
Fernandez-Funez P, Nino-Rosales ML, de Gouyon B, et al. 2000. Identification of genes that modify ataxin-1-induced neurodegeneration. Nature 408:101-106.
-
(2000)
Nature
, vol.408
, pp. 101-106
-
-
Fernandez-Funez, P.1
Nino-Rosales, M.L.2
De Gouyon, B.3
-
54
-
-
0347481386
-
Iron-Sulfur Cluster N2 of the Escherichia coli NADH:Ubiquinone Oxidoreductase (Complex I) Is Located on Subunit NuoB
-
DOI 10.1074/jbc.M308967200
-
Flemming D, Schlitt A, Spehr V, et al. 2003. Iron-sulfur cluster N2 of the Escherichia coli NADH:ubiquinone oxidoreductase (complex I) is located on subunit NuoB. J Biol Chem 278:47602-47609. (Pubitemid 37523204)
-
(2003)
Journal of Biological Chemistry
, vol.278
, Issue.48
, pp. 47602-47609
-
-
Flemming, D.1
Schlitt, A.2
Spehr, V.3
Bischof, T.4
Friedrich, T.5
-
55
-
-
70349908008
-
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using yeast models of OXPHOS deficiencies
-
Fontanesi F, Diaz F, Barrientos A. 2009. Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using yeast models of OXPHOS deficiencies. Curr Protoc Hum Genet 19:15.
-
(2009)
Curr Protoc Hum Genet
, vol.19
, pp. 15
-
-
Fontanesi, F.1
Diaz, F.2
Barrientos, A.3
-
57
-
-
0036468956
-
Yeast mitochondrial biogenesis: A model system for humans?
-
Foury F, Kucej M. 2002. Yeast mitochondrial biogenesis: a model system for humans? Curr Opin Chem Biol 6:106-111.
-
(2002)
Curr Opin Chem Biol
, vol.6
, pp. 106-111
-
-
Foury, F.1
Kucej, M.2
-
58
-
-
0032490117
-
The NADH:ubiquinone oxidoreductase (complex I) from Escherichia coli
-
DOI 10.1016/S0005-2728(98)00024-3, PII S0005272898000243
-
Friedrich T. 1998. The NADH:ubiquinone oxidoreductase (complex I) from Escherichia coli. Biochim Biophys Acta 1364:134-146. (Pubitemid 28291836)
-
(1998)
Biochimica et Biophysica Acta - Bioenergetics
, vol.1364
, Issue.2
, pp. 134-146
-
-
Friedrich, T.1
-
60
-
-
0028916511
-
Characterization of a microsomal subfraction associated with mitochondria of the yeast, Saccharomyces cerevisiae. Involvement in synthesis and import of phospholipids into mitochondria
-
Gaigg B, Simbeni R, Hrastnik C, et al. 1995. Characterization of a microsomal subfraction associated with mitochondria of the yeast, Saccharomyces cerevisiae. Involvement in synthesis and import of phospholipids into mitochondria. Biochim Biophys Acta 1234:214-220.
-
(1995)
Biochim Biophys Acta
, vol.1234
, pp. 214-220
-
-
Gaigg, B.1
Simbeni, R.2
Hrastnik, C.3
-
61
-
-
34248171499
-
The myopathic form of coenzyme Q10 deficiency is caused by mutations in the electron-transferring-flavoprotein dehydrogenase (ETFDH) gene
-
Gempel K, Topaloglu H, Talim B, et al. 2007. The myopathic form of coenzyme Q10 deficiency is caused by mutations in the electron-transferring- flavoprotein dehydrogenase (ETFDH) gene. Brain 130:2037-2044.
-
(2007)
Brain
, vol.130
, pp. 2037-2044
-
-
Gempel, K.1
Topaloglu, H.2
Talim, B.3
-
62
-
-
77952327043
-
Defective complex I assembly due to C20orf7 mutations as a new cause of Leigh syndrome
-
in press
-
Gerards M, Sluiter W, van den Bosch BJ, et al. Defective complex I assembly due to C20orf7 mutations as a new cause of Leigh syndrome. J Med Genet (in press).
-
J Med Genet
-
-
Gerards, M.1
Sluiter, W.2
Van Den Bosch, B.J.3
-
63
-
-
0842330598
-
Acyl-CoA dehydrogenases - A mechanistic overview
-
Ghisla S, Thorpe C. 2004. Acyl-CoA dehydrogenases - a mechanistic overview. Eur J Biochem 271:494-508.
-
(2004)
Eur J Biochem
, vol.271
, pp. 494-508
-
-
Ghisla, S.1
Thorpe, C.2
-
64
-
-
51249103626
-
Drosophila is an inclusive model for human diseases, growth and development
-
Gilbert LI. 2008. Drosophila is an inclusive model for human diseases, growth and development. Mol Cell Endocrinol 293:25-31.
-
(2008)
Mol Cell Endocrinol
, vol.293
, pp. 25-31
-
-
Gilbert, L.I.1
-
65
-
-
69049098806
-
Structural and functional link between the mitochondrial network and the endoplasmic reticulum
-
Giorgi C, De Stefani D, Bononi A, et al. 2009. Structural and functional link between the mitochondrial network and the endoplasmic reticulum. Int J Biochem Cell Biol 41:1817-1827.
-
(2009)
Int J Biochem Cell Biol
, vol.41
, pp. 1817-1827
-
-
Giorgi, C.1
De Stefani, D.2
Bononi, A.3
-
66
-
-
10744223145
-
Late-onset cerebellar ataxia with hypogonadism and muscle coenzyme Q10 deficiency
-
Gironi M, Lamperti C, Nemni R, et al. 2004. Late-onset cerebellar ataxia with hypogonadism and muscle coenzyme Q10 deficiency. Neurology 62:818-820.
-
(2004)
Neurology
, vol.62
, pp. 818-820
-
-
Gironi, M.1
Lamperti, C.2
Nemni, R.3
-
67
-
-
1042268861
-
Mitochondrial complex I mutations in Caenorhabditis elegans produce cytochrome c oxidase deficiency, oxidative stress and vitamin-responsive lactic acidosis
-
Grad LI, Lemire BD. 2004. Mitochondrial complex I mutations in Caenorhabditis elegans produce cytochrome c oxidase deficiency, oxidative stress and vitamin-responsive lactic acidosis. Hum Mol Genet 13:303-314.
-
(2004)
Hum Mol Genet
, vol.13
, pp. 303-314
-
-
Grad, L.I.1
Lemire, B.D.2
-
68
-
-
33645001946
-
Riboflavin enhances the assembly of mitochondrial cytochrome c oxidase in C. elegans NADH-ubiquinone oxidoreductase mutants
-
Grad LI, Lemire BD. 2006. Riboflavin enhances the assembly of mitochondrial cytochrome c oxidase in C. elegans NADH-ubiquinone oxidoreductase mutants. Biochim Biophys Acta 1757:115-122.
-
(2006)
Biochim Biophys Acta
, vol.1757
, pp. 115-122
-
-
Grad, L.I.1
Lemire, B.D.2
-
69
-
-
29444454373
-
Introduction of an additional pathway for lactate oxidation in the treatment of lactic acidosis and mitochondrial dysfunction in Caenorhabditis elegans
-
Grad LI, Sayles LC, Lemire BD. 2005. Introduction of an additional pathway for lactate oxidation in the treatment of lactic acidosis and mitochondrial dysfunction in Caenorhabditis elegans. Proc Natl Acad Sci USA 102:18367-18372.
-
(2005)
Proc Natl Acad Sci USA
, vol.102
, pp. 18367-18372
-
-
Grad, L.I.1
Sayles, L.C.2
Lemire, B.D.3
-
70
-
-
40949125215
-
Isolation and functional analysis of mitochondria from the nematode Caenorhabditis elegans
-
Grad LI, Sayles LC, Lemire BD. 2007. Isolation and functional analysis of mitochondria from the nematode Caenorhabditis elegans. Methods Mol Biol 372:51-66.
-
(2007)
Methods Mol Biol
, vol.372
, pp. 51-66
-
-
Grad, L.I.1
Sayles, L.C.2
Lemire, B.D.3
-
71
-
-
23044441770
-
Mitochondrial voltage-dependent anion channel gene family in Drosophila melanogaster: Complex patterns of evolution, genomic organization, and developmental expression
-
Graham BH, Craigen WJ. 2005. Mitochondrial voltage-dependent anion channel gene family in Drosophila melanogaster: complex patterns of evolution, genomic organization, and developmental expression. Mol Genet Metab 85:308-317.
-
(2005)
Mol Genet Metab
, vol.85
, pp. 308-317
-
-
Graham, B.H.1
Craigen, W.J.2
-
72
-
-
77951243014
-
Neurologic dysfunction and male infertility in Drosophila porin mutants: A new model for mitochondrial dysfunction and disease
-
Graham BH, Li Z, Alesii EP, et al. 2010. Neurologic dysfunction and male infertility in Drosophila porin mutants: a new model for mitochondrial dysfunction and disease. J Biol Chem 285:11143-11153.
-
(2010)
J Biol Chem
, vol.285
, pp. 11143-11153
-
-
Graham, B.H.1
Li, Z.2
Alesii, E.P.3
-
73
-
-
0037386532
-
Mitochondrial pathology and apoptotic muscle degeneration in Drosophila parkin mutants
-
DOI 10.1073/pnas.0737556100
-
Greene JC, Whitworth AJ, Kuo I, et al. 2003. Mitochondrial pathology and apoptotic muscle degeneration in Drosophila parkin mutants. Proc Natl Acad Sci USA 100:4078-4083. (Pubitemid 36418160)
-
(2003)
Proceedings of the National Academy of Sciences of the United States of America
, vol.100
, Issue.7
, pp. 4078-4083
-
-
Greene, J.C.1
Whitworth, A.J.2
Kuo, I.3
Andrews, L.A.4
Feany, M.B.5
Pallanck, L.J.6
-
74
-
-
34249750383
-
Evidence for a trade-off between survival and fitness caused by resveratrol treatment of Caenorhabditis elegans
-
Gruber J, Tang SY, Halliwell B. 2007. Evidence for a trade-off between survival and fitness caused by resveratrol treatment of Caenorhabditis elegans. Ann NY Acad Sci 1100:530-542.
-
(2007)
Ann NY Acad Sci
, vol.1100
, pp. 530-542
-
-
Gruber, J.1
Tang, S.Y.2
Halliwell, B.3
-
75
-
-
0347595327
-
Aberrant cardiolipin metabolism in the yeast taz1 mutant: A model for Barth syndrome
-
Gu Z, Valianpour F, Chen S, et al. 2004. Aberrant cardiolipin metabolism in the yeast taz1 mutant: a model for Barth syndrome. Mol Microbiol 51:149-158.
-
(2004)
Mol Microbiol
, vol.51
, pp. 149-158
-
-
Gu, Z.1
Valianpour, F.2
Chen, S.3
-
78
-
-
0034994933
-
Mitochondrial mutations differentially affect aging, mutability and anesthetic sensitivity in Caenorhabditis elegans
-
DOI 10.1016/S0047-6374(01)00259-7, PII S0047637401002597
-
Hartman PS, Ishii N, Kayser EB, et al. 2001. Mitochondrial mutations differentially affect aging, mutability and anesthetic sensitivity in Caenorhabditis elegans. Mech Ageing Dev 122:1187-1201. (Pubitemid 32522851)
-
(2001)
Mechanisms of Ageing and Development
, vol.122
, Issue.11
, pp. 1187-1201
-
-
Hartman, P.S.1
Ishii, N.2
Kayser, E.-B.3
Morgan, P.G.4
Sedensky, M.M.5
-
79
-
-
73449114300
-
Nicotinamide adenine dinucleotide extends the lifespan of Caenorhabditis elegans mediated by sir-2.1 and daf-16
-
Hashimoto T, Horikawa M, Nomura T, et al. 2009. Nicotinamide adenine dinucleotide extends the lifespan of Caenorhabditis elegans mediated by sir-2.1 and daf-16. Biogerontology 11:31-43.
-
(2009)
Biogerontology
, vol.11
, pp. 31-43
-
-
Hashimoto, T.1
Horikawa, M.2
Nomura, T.3
-
80
-
-
0031774294
-
Electrochemically induced FT-IR difference spectra of the two- and four-subunit cytochrome c oxidase from P. denitrificans reveal identical conformational changes upon redox transitions
-
Hellwig P, Ostermeier C, Michel H, et al. 1998. Electrochemically induced FT-IR difference spectra of the two- and four-subunit cytochrome c oxidase from P. denitrificans reveal identical conformational changes upon redox transitions. Biochim Biophys Acta 1409:107-112.
-
(1998)
Biochim Biophys Acta
, vol.1409
, pp. 107-112
-
-
Hellwig, P.1
Ostermeier, C.2
Michel, H.3
-
81
-
-
33847153121
-
Missense mutations in the BCS1L gene as a cause of the Bjornstad syndrome
-
Hinson JT, Fantin VR, Schonberger J, et al. 2007. Missense mutations in the BCS1L gene as a cause of the Bjornstad syndrome. N Engl J Med 356:809-819.
-
(2007)
N Engl J Med
, vol.356
, pp. 809-819
-
-
Hinson, J.T.1
Fantin, V.R.2
Schonberger, J.3
-
82
-
-
0038771142
-
The nuclear encoded subunits of complex I from bovine heart mitochondria
-
Hirst J, Carroll J, Fearnley IM, et al. 2003. The nuclear encoded subunits of complex I from bovine heart mitochondria. Biochim Biophys Acta 1604:135-150.
-
(2003)
Biochim Biophys Acta
, vol.1604
, pp. 135-150
-
-
Hirst, J.1
Carroll, J.2
Fearnley, I.M.3
-
83
-
-
0038787792
-
Brenner, the worm and the prize
-
Hoffenberg R. 2003. Brenner, the worm and the prize. Clin Med 3:285-286.
-
(2003)
Clin Med
, vol.3
, pp. 285-286
-
-
Hoffenberg, R.1
-
84
-
-
0242322000
-
The location of NuoL and NuoM subunits in the membrane domain of the Escherichia coli complex I: Implications for the mechanism of proton pumping
-
Holt PJ, Morgan DJ, Sazanov LA. 2003. The location of NuoL and NuoM subunits in the membrane domain of the Escherichia coli complex I: implications for the mechanism of proton pumping. J Biol Chem 278: 43114-43120.
-
(2003)
J Biol Chem
, vol.278
, pp. 43114-43120
-
-
Holt, P.J.1
Morgan, D.J.2
Sazanov, L.A.3
-
85
-
-
0017737868
-
Mutants of Drosophila melanogaster. II. Behavioral analysis and focus mapping
-
Homyk T Jr. 1977. Mutants of Drosophila melanogaster. II. Behavioral analysis and focus mapping. Genetics 87:105-128.
-
(1977)
Genetics
, vol.87
, pp. 105-128
-
-
Homyk Jr., T.1
-
86
-
-
0018873084
-
Behavioral mutants of Drosophila melanogaster. III. Isolation and mapping of mutations by direct visual observations of behavioral phenotypes
-
Homyk T Jr, Szidonya J, Suzuki DT. 1980. Behavioral mutants of Drosophila melanogaster. III. Isolation and mapping of mutations by direct visual observations of behavioral phenotypes. Mol Gen Genet 177:553-565.
-
(1980)
Mol Gen Genet
, vol.177
, pp. 553-565
-
-
Homyk Jr., T.1
Szidonya, J.2
Suzuki, D.T.3
-
87
-
-
0036233808
-
Oxidative stress and life span determination in the nematode Caenorhabditis elegans
-
Honda Y, Honda S. 2002. Oxidative stress and life span determination in the nematode Caenorhabditis elegans. Ann NYAcad Sci 959:466-474. (Pubitemid 34457586)
-
(2002)
Annals of the New York Academy of Sciences
, vol.959
, pp. 466-474
-
-
Honda, Y.1
Honda, S.2
-
89
-
-
0025944560
-
Leber hereditary optic neuropathy: Identification of the same mitochondrial NDI mutation in six pedigrees
-
Howell N, Bindoff LA, et al. 1991. Leber hereditary optic neuropathy: identification of the same mitochondrial ND1 mutation in six pedigrees. Am J Hum Genet 49:939-950. (Pubitemid 21891740)
-
(1991)
American Journal of Human Genetics
, vol.49
, Issue.5
, pp. 939-950
-
-
Howell, N.1
Bindoff, L.A.2
McCullough, D.A.3
Kubacka, I.4
Poulton, J.5
Mackey, D.6
Taylor, L.7
Turnbull, D.M.8
-
90
-
-
62049086087
-
Mutations in the C. elegans succinate dehydrogenase iron-sulfur subunit promote superoxide generation and premature aging
-
Huang J, Lemire BD. 2009. Mutations in the C. elegans succinate dehydrogenase iron-sulfur subunit promote superoxide generation and premature aging. J Mol Biol 387:559-569.
-
(2009)
J Mol Biol
, vol.387
, pp. 559-569
-
-
Huang, J.1
Lemire, B.D.2
-
91
-
-
0034467469
-
Oxidative stress and aging in Caenorhabditis elegans
-
Ishii N. 2000. Oxidative stress and aging in Caenorhabditis elegans. Free Radic Res 33:857-864.
-
(2000)
Free Radic Res
, vol.33
, pp. 857-864
-
-
Ishii, N.1
-
92
-
-
0032514466
-
A mutation in succinate dehydrogenase cytochrome b causes oxidative stress and ageing in nematodes
-
Ishii N, Fujii M, Hartman PS, et al. 1998. A mutation in succinate dehydrogenase cytochrome b causes oxidative stress and ageing in nematodes. Nature 394:694-697.
-
(1998)
Nature
, vol.394
, pp. 694-697
-
-
Ishii, N.1
Fujii, M.2
Hartman, P.S.3
-
93
-
-
0037007114
-
The accessory subunit of DNA polymerase gamma is essential for mitochondrial DNA maintenance and development in Drosophila melanogaster
-
Iyengar B, Luo N, Farr CL, et al. 2002. The accessory subunit of DNA polymerase gamma is essential for mitochondrial DNA maintenance and development in Drosophila melanogaster. Proc Natl Acad Sci USA 99:4483-4488.
-
(2002)
Proc Natl Acad Sci USA
, vol.99
, pp. 4483-4488
-
-
Iyengar, B.1
Luo, N.2
Farr, C.L.3
-
94
-
-
0032728444
-
The tamas gene, identified as a mutation that disrupts larval behavior in Drosophila melanogaster, codes for the mitochondrial DNA polymerase catalytic subunit (DNApol-gamma125)
-
Iyengar B, Roote J, Campos AR. 1999. The tamas gene, identified as a mutation that disrupts larval behavior in Drosophila melanogaster, codes for the mitochondrial DNA polymerase catalytic subunit (DNApol-gamma125). Genetics 153:1809-1824.
-
(1999)
Genetics
, vol.153
, pp. 1809-1824
-
-
Iyengar, B.1
Roote, J.2
Campos, A.R.3
-
95
-
-
23644443813
-
The retrograde response links metabolism with stress responses, chromatin-dependent gene activation, and genome stability in yeast aging
-
Jazwinski SM. 2005. The retrograde response links metabolism with stress responses, chromatin-dependent gene activation, and genome stability in yeast aging. Gene 354:22-27.
-
(2005)
Gene
, vol.354
, pp. 22-27
-
-
Jazwinski, S.M.1
-
96
-
-
0035229245
-
Effectiveness of specific RNA-mediated interference through ingested double-stranded RNA in Caenorhabditis elegans
-
RESEARCH0002
-
Kamath RS, Martinez-Campos M, Zipperlen P, et al. 2001. Effectiveness of specific RNA-mediated interference through ingested double-stranded RNA in Caenorhabditis elegans. Genome Biol 2:RESEARCH0002.
-
(2001)
Genome Biol
, vol.2
-
-
Kamath, R.S.1
Martinez-Campos, M.2
Zipperlen, P.3
-
97
-
-
14644386835
-
Characterization of the membrane domain subimit NuoJ (ND6) of the NADH-quinone oxidoreductase from Escherichia coli by chromosomal DNA manipulation
-
DOI 10.1021/bi0476477
-
Kao MC, Di Bernardo S, Nakamaru-Ogiso E, et al. 2005. Characterization of the membrane domain subunit NuoJ (ND6) of the NADH-quinone oxidoreductase from Escherichia coli by chromosomal DNA manipulation. Biochemistry 44:3562-3571. (Pubitemid 40322025)
-
(2005)
Biochemistry
, vol.44
, Issue.9
, pp. 3562-3571
-
-
Kao, M.-C.1
Di Bernardo, S.2
Nakamaru-Ogiso, E.3
Miyoshi, H.4
Matsuno-Yagi, A.5
Yagi, T.6
-
98
-
-
33646109080
-
The presequence of fumarase is exposed to the cytosol during import into mitochondria
-
Karniely S, Regev-Rudzki N, Pines O. 2006. The presequence of fumarase is exposed to the cytosol during import into mitochondria. J Mol Biol 358:396-405.
-
(2006)
J Mol Biol
, vol.358
, pp. 396-405
-
-
Karniely, S.1
Regev-Rudzki, N.2
Pines, O.3
-
99
-
-
0034604506
-
Role of adenine nucleotide translocator 1 in mtDNA maintenance
-
Kaukonen J, Juselius JK, Tiranti V, et al. 2000. Role of adenine nucleotide translocator 1 in mtDNA maintenance. Science 289:782-785.
-
(2000)
Science
, vol.289
, pp. 782-785
-
-
Kaukonen, J.1
Juselius, J.K.2
Tiranti, V.3
-
100
-
-
0035827706
-
Mitochondrial Expression and Function of GAS-1 in Caenorhabditis elegans
-
DOI 10.1074/jbc.M011066200
-
Kayser EB, Morgan PG, Hoppel CL, et al. 2001. Mitochondrial expression and function of GAS-1 in Caenorhabditis elegans. J Biol Chem 276:20551-20558. (Pubitemid 37411140)
-
(2001)
Journal of Biological Chemistry
, vol.276
, Issue.23
, pp. 20551-20558
-
-
Kayser, E.-B.1
Morgan, P.G.2
Hoppel, C.L.3
Sedensky, M.M.4
-
101
-
-
2942598255
-
Effects of complex I function and oxidative damage on lifespan and anesthetic sensitivity in Caenorhabditis elegans
-
Kayser EB, Sedensky MM, Morgan PG. 2004. effects of complex I function and oxidative damage on lifespan and anesthetic sensitivity in Caenorhabditis elegans. Mech Ageing Dev 125:455-464.
-
(2004)
Mech Ageing Dev
, vol.125
, pp. 455-464
-
-
Kayser, E.B.1
Sedensky, M.M.2
Morgan, P.G.3
-
102
-
-
0034663640
-
Diversity and origin of alternative NADH:ubiquinone oxidoreductases
-
Kerscher SJ. 2000. Diversity and origin of alternative NADH:ubiquinone oxidoreductases. Biochim Biophys Acta 1459:274-283.
-
(2000)
Biochim Biophys Acta
, vol.1459
, pp. 274-283
-
-
Kerscher, S.J.1
-
103
-
-
33947520506
-
Inhibition of hypoxia-inducible factor (HIF) hydroxylases by citric acid cycle intermediates: Possible links between cell metabolism and stabilization of HIF
-
Koivunen P, Hirsila M, Remes AM, et al. 2007. Inhibition of hypoxia-inducible factor (HIF) hydroxylases by citric acid cycle intermediates: possible links between cell metabolism and stabilization of HIF. J Biol Chem 282:4524-4532.
-
(2007)
J Biol Chem
, vol.282
, pp. 4524-4532
-
-
Koivunen, P.1
Hirsila, M.2
Remes, A.M.3
-
104
-
-
34250369119
-
Protein degradation within mitochondria: Versatile activities of AAA proteases and other peptidases
-
Koppen M, Langer T. 2007. Protein degradation within mitochondria: versatile activities of AAA proteases and other peptidases. Crit Rev Biochem Mol Biol 42:221-242.
-
(2007)
Crit Rev Biochem Mol Biol
, vol.42
, pp. 221-242
-
-
Koppen, M.1
Langer, T.2
-
105
-
-
0034194189
-
Oxidative phosphorylation in cardiolipin-lacking yeast mitochondria
-
DOI 10.1042/0264-6021:3470687
-
Koshkin V, Greenberg ML. 2000. Oxidative phosphorylation in cardiolipin-lacking yeast mitochondria. Biochem J 347:687-691. (Pubitemid 30260957)
-
(2000)
Biochemical Journal
, vol.347
, Issue.3
, pp. 687-691
-
-
Koshkin, V.1
Greenberg, M.L.2
-
106
-
-
0037093493
-
Cardiolipin prevents rate-dependent uncoupling and provides osmotic stability in yeast mitochondria
-
Koshkin V, Greenberg ML. 2002. Cardiolipin prevents rate-dependent uncoupling and provides osmotic stability in yeast mitochondria. Biochem J 364:317-322.
-
(2002)
Biochem J
, vol.364
, pp. 317-322
-
-
Koshkin, V.1
Greenberg, M.L.2
-
107
-
-
0034029917
-
Identification of novel human genes evolutionarily conserved in Caenorhabditis elegans by comparative proteomics
-
Lai CH, Chou CY, Ch'ang LY, et al. 2000. Identification of novel human genes evolutionarily conserved in Caenorhabditis elegans by comparative proteomics. Genome Res 10):703-713.
-
(2000)
Genome Res
, vol.10
, pp. 703-713
-
-
Lai, C.H.1
Chou, C.Y.2
Ch'Ang, L.Y.3
-
108
-
-
33845657872
-
ATAXIN-1 interacts with the repressor Capicua in its native complex to cause SCA1 neuropathology
-
Lam YC, Bowman AB, Jafar-Nejad P, et al. 2006. ATAXIN-1 interacts with the repressor Capicua in its native complex to cause SCA1 neuropathology. Cell 127:1335-1347.
-
(2006)
Cell
, vol.127
, pp. 1335-1347
-
-
Lam, Y.C.1
Bowman, A.B.2
Jafar-Nejad, P.3
-
109
-
-
0035853166
-
Inherited susceptibility to uterine leiomyomas and renal cell cancer
-
Launonen V, Vierimaa O, Kiuru M, et al. 2001. Inherited susceptibility to uterine leiomyomas and renal cell cancer. Proc Natl Acad Sci USA 98:3387-3392.
-
(2001)
Proc Natl Acad Sci USA
, vol.98
, pp. 3387-3392
-
-
Launonen, V.1
Vierimaa, O.2
Kiuru, M.3
-
110
-
-
33745587285
-
A functional hybrid between the cytochrome bc1 complex and its physiological membrane-anchored electron acceptor cytochrome cy in Rhodobacter capsulatus
-
Lee DW, Ozturk Y, Mamedova A, et al. 2006. A functional hybrid between the cytochrome bc1 complex and its physiological membrane-anchored electron acceptor cytochrome cy in Rhodobacter capsulatus. Biochim Biophys Acta 1757:346-352.
-
(2006)
Biochim Biophys Acta
, vol.1757
, pp. 346-352
-
-
Lee, D.W.1
Ozturk, Y.2
Mamedova, A.3
-
111
-
-
46649119960
-
Cytochrome bc1-cy fusion complexes reveal the distance constraints for functional electron transfer between photosynthesis components
-
Lee DW, Ozturk Y, Osyczka A, et al. 2008. Cytochrome bc1-cy fusion complexes reveal the distance constraints for functional electron transfer between photosynthesis components. J Biol Chem 283:13973-13982.
-
(2008)
J Biol Chem
, vol.283
, pp. 13973-13982
-
-
Lee, D.W.1
Ozturk, Y.2
Osyczka, A.3
-
112
-
-
0037228016
-
A systematic RNAi screen identifies a critical role for mitochondria in C. elegans longevity
-
Lee SS, Lee RY, Fraser AG, et al. 2003. A systematic RNAi screen identifies a critical role for mitochondria in C. elegans longevity. Nat Genet 33:40-48.
-
(2003)
Nat Genet
, vol.33
, pp. 40-48
-
-
Lee, S.S.1
Lee, R.Y.2
Fraser, A.G.3
-
113
-
-
0033652821
-
Overexpression of the catalytic subunit of DNA polymerase gamma results in depletion of mitochondrial DNA in Drosophila melanogaster
-
Lefai E, Calleja M, Ruiz de Mena I, et al. 2000. Overexpression of the catalytic subunit of DNA polymerase gamma results in depletion of mitochondrial DNA in Drosophila melanogaster. Mol Gen Genet 264:37-46.
-
(2000)
Mol Gen Genet
, vol.264
, pp. 37-46
-
-
Lefai, E.1
Calleja, M.2
Ruiz De Mena, I.3
-
114
-
-
67349229199
-
C. elegans longevity pathways converge to decrease mitochondrial membrane potential
-
Lemire BD, Behrendt M, DeCorby A, et al. 2009. C. elegans longevity pathways converge to decrease mitochondrial membrane potential. Mech Ageing Dev 130:461-465.
-
(2009)
Mech Ageing Dev
, vol.130
, pp. 461-465
-
-
Lemire, B.D.1
Behrendt, M.2
DeCorby, A.3
-
115
-
-
33748909136
-
An efficient genetic screen in Drosophila to identify nuclear-encoded genes with mitochondrial function
-
Liao TS, Call GB, Guptan P, et al. 2006. An efficient genetic screen in Drosophila to identify nuclear-encoded genes with mitochondrial function. Genetics 174:525-533.
-
(2006)
Genetics
, vol.174
, pp. 525-533
-
-
Liao, T.S.1
Call, G.B.2
Guptan, P.3
-
116
-
-
67650868959
-
Mitochondrial dynamics in mammalian health and disease
-
Liesa M, Palacin M, Zorzano A. 2009. Mitochondrial dynamics in mammalian health and disease. Physiol Rev 89:799-845.
-
(2009)
Physiol Rev
, vol.89
, pp. 799-845
-
-
Liesa, M.1
Palacin, M.2
Zorzano, A.3
-
117
-
-
34250716562
-
Mutations in cytochrome c oxidase subunit VIa cause neurodegeneration and motor dysfunction in Drosophila
-
DOI 10.1534/genetics.107.071688
-
Liu W, Gnanasambandam R, Benjamin J, et al. 2007. Mutations in cytochrome c oxidase subunit VIa cause neurodegeneration and motor dysfunction in Drosophila. Genetics 176:937-946. (Pubitemid 46961097)
-
(2007)
Genetics
, vol.176
, Issue.2
, pp. 937-946
-
-
Liu, W.1
Gnanasambandam, R.2
Benjamin, J.3
Kaur, G.4
Getman, P.B.5
Siegel, A.J.6
Shortridge, R.D.7
Singh, S.8
-
118
-
-
66149135641
-
Drosophila models of neurodegenerative diseases
-
Lu B, Vogel H. 2009. Drosophila models of neurodegenerative diseases. Annu Rev Pathol 4:315-342.
-
(2009)
Annu Rev Pathol
, vol.4
, pp. 315-342
-
-
Lu, B.1
Vogel, H.2
-
119
-
-
0032516550
-
The nuoM arg368his mutation in NADH:ubiquinone oxidoreductase from Rhodobacter capsulatus: A model for the human nd4-11778 mtDNA mutation associated with Leber's hereditary optic neuropathy
-
Lunardi J, Darrouzet E, Dupuis A, et al. 1998. The nuoM arg368his mutation in NADH:ubiquinone oxidoreductase from Rhodobacter capsulatus: a model for the human nd4-11778 mtDNA mutation associated with Leber's hereditary optic neuropathy. Biochim Biophys Acta 1407:114-124.
-
(1998)
Biochim Biophys Acta
, vol.1407
, pp. 114-124
-
-
Lunardi, J.1
Darrouzet, E.2
Dupuis, A.3
-
120
-
-
71949103162
-
Novel interactions of CLN5 support molecular networking between neuronal ceroid lipofuscinosis proteins
-
Lyly A, von Schantz C, Heine C, et al. 2009. Novel interactions of CLN5 support molecular networking between neuronal ceroid lipofuscinosis proteins. BMC Cell Biol 10:83.
-
(2009)
BMC Cell Biol
, vol.10
, pp. 83
-
-
Lyly, A.1
Von Schantz, C.2
Heine, C.3
-
121
-
-
0032877617
-
Acylation of monolysocardiolipin in rat heart
-
Ma BJ, Taylor WA, Dolinsky VW, et al. 1999. Acylation of monolysocardiolipin in rat heart. J Lipid Res 40:1837-1845.
-
(1999)
J Lipid Res
, vol.40
, pp. 1837-1845
-
-
Ma, B.J.1
Taylor, W.A.2
Dolinsky, V.W.3
-
122
-
-
7244224978
-
The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Delta mutant. Implications for Barth syndrome
-
Ma L, Vaz FM, Gu Z, et al. 2004. The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Delta mutant. Implications for Barth syndrome. J Biol Chem 279:44394-44399.
-
(2004)
J Biol Chem
, vol.279
, pp. 44394-44399
-
-
Ma, L.1
Vaz, F.M.2
Gu, Z.3
-
123
-
-
60549086949
-
Role of calcium-independent phospholipase A2 in the pathogenesis of Barth syndrome
-
Malhotra A, Edelman-Novemsky I, Xu Y, et al. 2009. Role of calcium-independent phospholipase A2 in the pathogenesis of Barth syndrome. Proc Natl Acad Sci USA 106:2337-2341.
-
(2009)
Proc Natl Acad Sci USA
, vol.106
, pp. 2337-2341
-
-
Malhotra, A.1
Edelman-Novemsky, I.2
Xu, Y.3
-
124
-
-
70449084874
-
Modeling of human pathogenic mutations in Escherichia coli complex I reveals a sensitive region in the fourth inside loop of NuoH
-
Maliniemi P, Kervinen M, Hassinen IE. 2009. Modeling of human pathogenic mutations in Escherichia coli complex I reveals a sensitive region in the fourth inside loop of NuoH. Mitochondrion 9:394-401.
-
(2009)
Mitochondrion
, vol.9
, pp. 394-401
-
-
Maliniemi, P.1
Kervinen, M.2
Hassinen, I.E.3
-
125
-
-
57649178662
-
The yeast Coq4 polypeptide organizes a mitochondrial protein complex essential for coenzyme Q biosynthesis
-
Marbois B, Gin P, Gulmezian M, et al. 2009. The yeast Coq4 polypeptide organizes a mitochondrial protein complex essential for coenzyme Q biosynthesis. Biochim Biophys Acta 1791:69-75.
-
(2009)
Biochim Biophys Acta
, vol.1791
, pp. 69-75
-
-
Marbois, B.1
Gin, P.2
Gulmezian, M.3
-
127
-
-
50649095537
-
Reactive oxygen species act remotely to cause synapse loss in a Drosophila model of developmental mitochondrial encephalopathy
-
Mast JD, Tomalty KM, Vogel H, et al. 2008. Reactive oxygen species act remotely to cause synapse loss in a Drosophila model of developmental mitochondrial encephalopathy. Development 135:2669-2679.
-
(2008)
Development
, vol.135
, pp. 2669-2679
-
-
Mast, J.D.1
Tomalty, K.M.2
Vogel, H.3
-
128
-
-
33646543714
-
Normal mitochondrial dynamics requires rhomboid-7 and affects Drosophila lifespan and neuronal function
-
McQuibban GA, Lee JR, Zheng L, et al. 2006. Normal mitochondrial dynamics requires rhomboid-7 and affects Drosophila lifespan and neuronal function. Curr Biol 16:982-989.
-
(2006)
Curr Biol
, vol.16
, pp. 982-989
-
-
McQuibban, G.A.1
Lee, J.R.2
Zheng, L.3
-
130
-
-
0036139795
-
HIF-1 and AP-1 cooperate to increase gene expression in hypoxia: Role of MAP kinases
-
Michiels C, Minet E, Michel G, et al. 2001. HIF-1 and AP-1 cooperate to increase gene expression in hypoxia: role of MAP kinases. IUBMB Life 52:49-53. (Pubitemid 33769669)
-
(2001)
IUBMB Life
, vol.52
, Issue.1-2
, pp. 49-53
-
-
Michiels, C.1
Minet, E.2
Michel, G.3
Mottet, D.4
Piret, J.-P.5
Raes, M.6
-
131
-
-
0142057173
-
Expression of Barstar as a selectable marker in yeast mitochondria
-
Mireau H, Arnal N, Fox TD. 2003. Expression of Barstar as a selectable marker in yeast mitochondria. Mol Genet Genomics 270:1-8.
-
(2003)
Mol Genet Genomics
, vol.270
, pp. 1-8
-
-
Mireau, H.1
Arnal, N.2
Fox, T.D.3
-
132
-
-
41149134880
-
CABC1 gene mutations cause ubiquinone deficiency with cerebellar ataxia and seizures
-
Mollet J, Delahodde A, Serre V, et al. 2008. CABC1 gene mutations cause ubiquinone deficiency with cerebellar ataxia and seizures. Am J Hum Genet 82:623-630.
-
(2008)
Am J Hum Genet
, vol.82
, pp. 623-630
-
-
Mollet, J.1
Delahodde, A.2
Serre, V.3
-
133
-
-
0035836740
-
Familial cerebellar ataxia with muscle coenzyme Q10 deficiency
-
Musumeci O, Naini A, Slonim AE, et al. 2001. Familial cerebellar ataxia with muscle coenzyme Q10 deficiency. Neurology 56:849-855.
-
(2001)
Neurology
, vol.56
, pp. 849-855
-
-
Musumeci, O.1
Naini, A.2
Slonim, A.E.3
-
134
-
-
0032972509
-
PSORT: A program for detecting sorting signals in proteins and predicting their subcellular localization
-
DOI 10.1016/S0968-0004(98)01336-X, PII S096800049801336X
-
Nakai K, Horton P. 1999. PSORT: a program for detecting sorting signals in proteins and predicting their subcellular localization. Trends Biochem Sci 24:34-36. (Pubitemid 29074461)
-
(1999)
Trends in Biochemical Sciences
, vol.24
, Issue.1
, pp. 34-35
-
-
Nakai, K.1
Horton, P.2
-
135
-
-
54449087539
-
Iron-sulfur cluster N5 is coordinated by an HXXXCXXCXXXXXC motif in the NuoG subunit of Escherichia coli NADH:quinone oxidoreductase (complex I)
-
Nakamaru-Ogiso E, Matsuno-Yagi A, Yoshikawa S, et al. 2008. Iron-sulfur cluster N5 is coordinated by an HXXXCXXCXXXXXC motif in the NuoG subunit of Escherichia coli NADH:quinone oxidoreductase (complex I). J Biol Chem 283:25979-25987.
-
(2008)
J Biol Chem
, vol.283
, pp. 25979-25987
-
-
Nakamaru-Ogiso, E.1
Matsuno-Yagi, A.2
Yoshikawa, S.3
-
136
-
-
0037127215
-
Characterization of the iron-sulfur cluster coordinated by a cysteine cluster motif (CXXCXXXCX27C) in the Nqo3 subunit in the proton-translocating NADH-quinone oxidoreductase (NDH-1) of Thermus thermophilus HB-8
-
Nakamaru-Ogiso E, Yano T, Ohnishi T, et al. 2002. Characterization of the iron-sulfur cluster coordinated by a cysteine cluster motif (CXXCXXXCX27C) in the Nqo3 subunit in the proton-translocating NADH-quinone oxidoreductase (NDH-1) of Thermus thermophilus HB-8. J Biol Chem 277:1680-1688.
-
(2002)
J Biol Chem
, vol.277
, pp. 1680-1688
-
-
Nakamaru-Ogiso, E.1
Yano, T.2
Ohnishi, T.3
-
137
-
-
12844249400
-
Characterization of the iron-sulfur cluster N7 (N1c) in the subunit NuoG of the proton-translocating NADH-quinone oxidoreductase from Escherichia coli
-
DOI 10.1074/jbc.M410377200
-
Nakamaru-Ogiso E, Yano T, Yagi T, et al. 2005. Characterization of the iron-sulfur cluster N7 (N1c) in the subunit NuoG of the proton-translocating NADH-quinone oxidoreductase from Escherichia coli. J Biol Chem 280:301-307. (Pubitemid 40164993)
-
(2005)
Journal of Biological Chemistry
, vol.280
, Issue.1
, pp. 301-307
-
-
Nakamaru-Ogiso, E.1
Yano, T.2
Yagi, T.3
Ohnishi, T.4
-
138
-
-
0031204998
-
Barth syndrome may be due to an acyltransferase deficiency
-
Neuwald AF. 1997. Barth syndrome may be due to an acyltransferase deficiency. Curr Biol 7:R465-R466.
-
(1997)
Curr Biol
, vol.7
-
-
Neuwald, A.F.1
-
139
-
-
26444488636
-
A molecular chaperone for mitochondrial complex I assembly is mutated in a progressive encephalopathy
-
Ogilvie I, Kennaway NG, Shoubridge EA. 2005. A molecular chaperone for mitochondrial complex I assembly is mutated in a progressive encephalopathy. J Clin Invest 115: 2784-2792.
-
(2005)
J Clin Invest
, vol.115
, pp. 2784-2792
-
-
Ogilvie, I.1
Kennaway, N.G.2
Shoubridge, E.A.3
-
140
-
-
39749104169
-
Distinct mitochondrial retrograde signals control the G1-S cell cycle checkpoint
-
Owusu-Ansah E, Yavari A, Mandal S, et al. 2008. Distinct mitochondrial retrograde signals control the G1-S cell cycle checkpoint. Nat Genet 40356-361.
-
(2008)
Nat Genet
, pp. 40356-40361
-
-
Owusu-Ansah, E.1
Yavari, A.2
Mandal, S.3
-
141
-
-
46349103594
-
A mitochondrial protein compendium elucidates complex I disease biology
-
Pagliarini DJ, Calvo SE, Chang B, et al. 2008. A mitochondrial protein compendium elucidates complex I disease biology. Cell 134:112-123.
-
(2008)
Cell
, vol.134
, pp. 112-123
-
-
Pagliarini, D.J.1
Calvo, S.E.2
Chang, B.3
-
142
-
-
27544494568
-
Complete loss-of-function of the heart/muscle-specific adenine nucleotide translocator is associated with mitochondrial myopathy and cardiomyopathy
-
Palmieri L, Alberio S, Pisano I, et al. 2005. Complete loss-of-function of the heart/muscle-specific adenine nucleotide translocator is associated with mitochondrial myopathy and cardiomyopathy. Hum Mol Genet 14:3079-3088.
-
(2005)
Hum Mol Genet
, vol.14
, pp. 3079-3088
-
-
Palmieri, L.1
Alberio, S.2
Pisano, I.3
-
143
-
-
8644224853
-
A Robust toolkit for functional profiling of the yeast genome
-
Pan X, Yuan DS, Xiang D, et al. 2004. A Robust toolkit for functional profiling of the yeast genome. Mol Cell 16:487-496.
-
(2004)
Mol Cell
, vol.16
, pp. 487-496
-
-
Pan, X.1
Yuan, D.S.2
Xiang, D.3
-
144
-
-
70349783430
-
Mitochondrial dysfunction and Parkinson's disease genes: Insights from Drosophila
-
Park J, Kim Y, Chung J. 2009. Mitochondrial dysfunction and Parkinson's disease genes: insights from Drosophila. Dis Model Mech 2:336-340.
-
(2009)
Dis Model Mech
, vol.2
, pp. 336-340
-
-
Park, J.1
Kim, Y.2
Chung, J.3
-
145
-
-
33745602748
-
Mitochondrial dysfunction in Drosophila PINK1 mutants is complemented by parkin
-
Park J, Lee SB, Lee S, et al. 2006. Mitochondrial dysfunction in Drosophila PINK1 mutants is complemented by parkin. Nature 441: 1157-1161.
-
(2006)
Nature
, vol.441
, pp. 1157-1161
-
-
Park, J.1
Lee, S.B.2
Lee, S.3
-
146
-
-
34247118250
-
Yeast NDI1 improves oxidative phosphorylation capacity and increases protection against oxidative stress and cell death in cells carrying a Leber's hereditary optic neuropathy mutation
-
DOI 10.1016/j.bbadis.2007.01.009, PII S0925443907000294
-
Park JS, Li YF, Bai Y. 2007. Yeast NDI1 improves oxidative phosphorylation capacity and increases protection against oxidative stress and cell death in cells carrying a Leber's hereditary optic neuropathy mutation. Biochim Biophys Acta 1772:533-542. (Pubitemid 46589981)
-
(2007)
Biochimica et Biophysica Acta - Molecular Basis of Disease
, vol.1772
, Issue.5
, pp. 533-542
-
-
Park, J.S.1
Li, Y.-F.2
Bai, Y.3
-
147
-
-
43249118592
-
Primary coenzyme Q deficiency in Pdss2 mutant mice causes isolated renal disease
-
Peng M, Falk MJ, Haase VH, et al. 2008. Primary coenzyme Q deficiency in Pdss2 mutant mice causes isolated renal disease. PLoS Genet 4:e1000061.
-
(2008)
PLoS Genet
, vol.4
-
-
Peng, M.1
Falk, M.J.2
Haase, V.H.3
-
148
-
-
37149037749
-
Systematic screens for human disease genes, from yeast to human and back
-
DOI 10.1039/b709494a
-
Perocchi F, Mancera E, Steinmetz LM. 2008. Systematic screens for human disease genes, from yeast to human and back. Mol Biosyst 4:18-29. (Pubitemid 350261750)
-
(2007)
Molecular BioSystems
, vol.4
, Issue.1
, pp. 18-29
-
-
Perocchi, F.1
Mancera, E.2
Steinmetz, L.M.3
-
149
-
-
0031780877
-
Creating mosaics in Drosophila
-
Perrimon N. 1998. Creating mosaics in Drosophila. Int J Dev Biol 42:243-247.
-
(1998)
Int J Dev Biol
, vol.42
, pp. 243-247
-
-
Perrimon, N.1
-
150
-
-
2542560342
-
Drosophila parkin mutants have decreased mass and cell size and increased sensitivity to oxygen radical stress
-
Pesah Y, Pham T, Burgess H, et al. 2004. Drosophila parkin mutants have decreased mass and cell size and increased sensitivity to oxygen radical stress. Development 131: 2183-2194.
-
(2004)
Development
, vol.131
, pp. 2183-2194
-
-
Pesah, Y.1
Pham, T.2
Burgess, H.3
-
152
-
-
0035918512
-
Identification of two tetranuclear FeS clusters on the ferredoxin-type subunit of NADH:ubiquinone oxidoreductase (complex I)
-
Rasmussen T, Scheide D, Brors B, et al. 2001. Identification of two tetranuclear FeS clusters on the ferredoxin-type subunit of NADH:ubiquinone oxidoreductase (complex I). Biochemistry 40:6124-6131.
-
(2001)
Biochemistry
, vol.40
, pp. 6124-6131
-
-
Rasmussen, T.1
Scheide, D.2
Brors, B.3
-
153
-
-
0041440219
-
A metabolic model for life span determination in Caenorhabditis elegans
-
DOI 10.1016/S1534-5807(03)00242-9, PII S1534580703002429
-
Rea S, Johnson TE. 2003. A metabolic model for life span determination in Caenorhabditis elegans. Dev Cell 5:197-203. (Pubitemid 37006465)
-
(2003)
Developmental Cell
, vol.5
, Issue.2
, pp. 197-203
-
-
Rea, S.1
Johnson, T.E.2
-
154
-
-
35648947912
-
Relationship between mitochondrial electron transport chain dysfunction, development, and life extension in Caenorhabditis elegans
-
Rea SL, Ventura N, Johnson TE. Relationship between mitochondrial electron transport chain dysfunction, development, and life extension in Caenorhabditis elegans. PLoS Biol 5:e259, 2007.
-
(2007)
PLoS Biol
, vol.5
-
-
Rea, S.L.1
Ventura, N.2
Johnson, T.E.3
-
155
-
-
40949091947
-
Proteomics of yeast mitochondria
-
Reinders J, Sickmann A. 2007. Proteomics of yeast mitochondria. Methods Mol Biol 372:543-557.
-
(2007)
Methods Mol Biol
, vol.372
, pp. 543-557
-
-
Reinders, J.1
Sickmann, A.2
-
156
-
-
33745851905
-
Toward the complete yeast mitochondrial proteome: Multidimensional separation techniques for mitochondrial proteomics
-
Reinders J, Zahedi RP, Pfanner N, et al. 2006. Toward the complete yeast mitochondrial proteome: multidimensional separation techniques for mitochondrial proteomics. J Proteome Res 5:1543-1554.
-
(2006)
J Proteome Res
, vol.5
, pp. 1543-1554
-
-
Reinders, J.1
Zahedi, R.P.2
Pfanner, N.3
-
157
-
-
0029803808
-
The role of protein degradation in mitochondrial function and biogenesis
-
DOI 10.1007/s002940050145
-
Rep M, Grivell LA. 1996. The role of protein degradation in mitochondrial function and biogenesis. Curr Genet 30:367-380. (Pubitemid 26402474)
-
(1996)
Current Genetics
, vol.30
, Issue.5
, pp. 367-380
-
-
Rep, M.1
Grivell, L.A.2
-
158
-
-
66349104071
-
Electron transfer and energy transduction in the terminal part of the respiratory chain - Lessons from bacterial model systems
-
Richter OM, Ludwig B. 2009. Electron transfer and energy transduction in the terminal part of the respiratory chain - lessons from bacterial model systems. Biochim Biophys Acta 1787:626-634.
-
(2009)
Biochim Biophys Acta
, vol.1787
, pp. 626-634
-
-
Richter, O.M.1
Ludwig, B.2
-
159
-
-
0347622768
-
A temperature-sensitive allele of Drosophila sesB reveals acute functions for the mitochondrial adenine nucleotide translocase in synaptic transmission and dynamin regulation
-
Rikhy R, Ramaswami M, Krishnan KS. 2003. A temperature-sensitive allele of Drosophila sesB reveals acute functions for the mitochondrial adenine nucleotide translocase in synaptic transmission and dynamin regulation. Genetics 165:1243-1253.
-
(2003)
Genetics
, vol.165
, pp. 1243-1253
-
-
Rikhy, R.1
Ramaswami, M.2
Krishnan, K.S.3
-
160
-
-
0023663056
-
The tko locus, site of a behavioral mutation in D. melanogaster, codes for a protein homologous to prokaryotic ribosomal protein S12
-
Royden CS, Pirrotta V, Jan LY. 1987. The tko locus, site of a behavioral mutation in D. melanogaster, codes for a protein homologous to prokaryotic ribosomal protein S12. Cell 51:165-173.
-
(1987)
Cell
, vol.51
, pp. 165-173
-
-
Royden, C.S.1
Pirrotta, V.2
Jan, L.Y.3
-
161
-
-
3242784956
-
Transposable elements as tools for genomics and genetics in Drosophila
-
Ryder E, Russell S. 2003. Transposable elements as tools for genomics and genetics in Drosophila. Brief Funct Genomic Proteomic 2:57-71.
-
(2003)
Brief Funct Genomic Proteomic
, vol.2
, pp. 57-71
-
-
Ryder, E.1
Russell, S.2
-
162
-
-
0037192846
-
Uptake of exogenous coenzyme Q and transport to mitochondria is required for bc1 complex stability in yeast coq mutants
-
Santos-Ocana C, Do TQ, Padilla S, et al. 2002. Uptake of exogenous coenzyme Q and transport to mitochondria is required for bc1 complex stability in yeast coq mutants. J Biol Chem 277:10973-10981.
-
(2002)
J Biol Chem
, vol.277
, pp. 10973-10981
-
-
Santos-Ocana, C.1
Do, T.Q.2
Padilla, S.3
-
163
-
-
33644872938
-
Structure of the hydrophilic domain of respiratory complex I from Thermus thermophilus
-
DOI 10.1126/science.1123809
-
Sazanov LA, Hinchliffe P. 2006. Structure of the hydrophilic domain of respiratory complex I from Thermus thermophilus. Science 311:1430-1436. (Pubitemid 43376691)
-
(2006)
Science
, vol.311
, Issue.5766
, pp. 1430-1436
-
-
Sazanov, L.A.1
Hinchliffe, P.2
-
164
-
-
0034665878
-
Cryo-electron crystallography of two sub-complexes of bovine complex I reveals the relationship between the membrane and peripheral arms
-
Sazanov LA, Walker JE. 2000. Cryo-electron crystallography of two sub-complexes of bovine complex I reveals the relationship between the membrane and peripheral arms. J Mol Biol 302:455-464.
-
(2000)
J Mol Biol
, vol.302
, pp. 455-464
-
-
Sazanov, L.A.1
Walker, J.E.2
-
165
-
-
0027538471
-
Mitochondrial cardiolipin in diverse eukaryotes. Comparison of biosynthetic reactions and molecular acyl species
-
Schlame M, Brody S, Hostetler KY. 1993. Mitochondrial cardiolipin in diverse eukaryotes. Comparison of biosynthetic reactions and molecular acyl species. Eur J Biochem 212:727-735.
-
(1993)
Eur J Biochem
, vol.212
, pp. 727-735
-
-
Schlame, M.1
Brody, S.2
Hostetler, K.Y.3
-
166
-
-
33749061065
-
Barth syndrome, a human disorder of cardiolipin metabolism
-
Schlame M, Ren M. 2006. Barth syndrome, a human disorder of cardiolipin metabolism. FEBS Lett 580:5450-5455.
-
(2006)
FEBS Lett
, vol.580
, pp. 5450-5455
-
-
Schlame, M.1
Ren, M.2
-
167
-
-
0025650402
-
Lysocardiolipin formation and reacylation in isolated rat liver mitochondria
-
Schlame M, Rustow B. 1990. Lysocardiolipin formation and reacylation in isolated rat liver mitochondria. Biochem J 272:589-595.
-
(1990)
Biochem J
, vol.272
, pp. 589-595
-
-
Schlame, M.1
Rustow, B.2
-
168
-
-
77956203927
-
Is Alzheimer's disease a disorder of mitochondria-associated membranes?
-
Schon EA, Area-Gomez E. 2010. Is Alzheimer's disease a disorder of mitochondria-associated membranes? J Alzheimers Dis 20(Suppl 2):S281-S292.
-
(2010)
J Alzheimers Dis
, vol.20
, Issue.SUPPL. 2
-
-
Schon, E.A.1
Area-Gomez, E.2
-
169
-
-
0042622380
-
SWISS-MODEL: An automated protein homology-modeling server
-
DOI 10.1093/nar/gkg520
-
Schwede T, Kopp J, Guex N, et al. 2003. Swiss-model: an automated protein homology-modeling server. Nucleic Acids Res 31:3381-3385. (Pubitemid 37442164)
-
(2003)
Nucleic Acids Research
, vol.31
, Issue.13
, pp. 3381-3385
-
-
Schwede, T.1
Kopp, J.2
Guex, N.3
Peitsch, M.C.4
-
170
-
-
33749024459
-
Yeast models of human mitochondrial diseases: From molecular mechanisms to drug screening
-
Schwimmer C, Rak M, Lefebvre-Legendre L, et al. 2006. Yeast models of human mitochondrial diseases: from molecular mechanisms to drug screening. Biotechnol J 1:270-281.
-
(2006)
Biotechnol J
, vol.1
, pp. 270-281
-
-
Schwimmer, C.1
Rak, M.2
Lefebvre-Legendre, L.3
-
171
-
-
0037820623
-
A complex II defect affects mitochondrial structure, leading to ced-3- and ced-4-dependent apoptosis and aging
-
Senoo-Matsuda N, Hartman PS, Akatsuka A, et al. 2003. A complex II defect affects mitochondrial structure, leading to ced-3- and ced-4-dependent apoptosis and aging. J Biol Chem 278:22031-22036.
-
(2003)
J Biol Chem
, vol.278
, pp. 22031-22036
-
-
Senoo-Matsuda, N.1
Hartman, P.S.2
Akatsuka, A.3
-
172
-
-
33745739747
-
Energy deficiency in the failing heart: Linking increased reactive oxygen species and disruption of oxidative phosphorylation rate
-
Sheeran FL, Pepe S. 2006. Energy deficiency in the failing heart: linking increased reactive oxygen species and disruption of oxidative phosphorylation rate. Biochim Biophys Acta 1757:543-552.
-
(2006)
Biochim Biophys Acta
, vol.1757
, pp. 543-552
-
-
Sheeran, F.L.1
Pepe, S.2
-
174
-
-
77952886494
-
VDAC, a multi-functional mitochondrial protein regulating cell life and death
-
Shoshan-Barmatz V, De Pinto V, Zweckstetter M, et al. 2010. VDAC, a multi-functional mitochondrial protein regulating cell life and death. Mol Aspects Med 31:227-285.
-
(2010)
Mol Aspects Med
, vol.31
, pp. 227-285
-
-
Shoshan-Barmatz, V.1
De Pinto, V.2
Zweckstetter, M.3
-
175
-
-
77953725586
-
Oxidative protein folding in the endoplasmic reticulum: Tight links to the mitochondria-associated membrane (MAM)
-
Simmen T, Lynes EM, Gesson K, et al. 2010. Oxidative protein folding in the endoplasmic reticulum: tight links to the mitochondria-associated membrane (MAM). Biochim Biophys Acta 1798:1465-1473.
-
(2010)
Biochim Biophys Acta
, vol.1798
, pp. 1465-1473
-
-
Simmen, T.1
Lynes, E.M.2
Gesson, K.3
-
176
-
-
0027349946
-
Biochemical mechanisms underlying MPTP-induced and idiopathic parkinsonism. New vistas
-
Singer TP, Ramsay RR, Sonsalla PK, et al. 1993. Biochemical mechanisms underlying MPTP-induced and idiopathic parkinsonism. New vistas. Adv Neurol 60:300-305.
-
(1993)
Adv Neurol
, vol.60
, pp. 300-305
-
-
Singer, T.P.1
Ramsay, R.R.2
Sonsalla, P.K.3
-
177
-
-
65649153703
-
Critical roles of subunit NuoH (ND1) in the assembly of peripheral subunits with the membrane domain of Escherichia coli NDH-1
-
Sinha PK, Torres-Bacete J, Nakamaru-Ogiso E, et al. 2009. Critical roles of subunit NuoH (ND1) in the assembly of peripheral subunits with the membrane domain of Escherichia coli NDH-1. J Biol Chem 284:9814-9823.
-
(2009)
J Biol Chem
, vol.284
, pp. 9814-9823
-
-
Sinha, P.K.1
Torres-Bacete, J.2
Nakamaru-Ogiso, E.3
-
179
-
-
35549005324
-
Exploring the mitochondrial proteome of the ciliate protozoon Tetrahymena thermophila: Direct analysis by tandem mass spectrometry
-
Smith DG, Gawryluk RM, Spencer DF, et al. 2007. Exploring the mitochondrial proteome of the ciliate protozoon Tetrahymena thermophila: direct analysis by tandem mass spectrometry. J Mol Biol 374:837-863.
-
(2007)
J Mol Biol
, vol.374
, pp. 837-863
-
-
Smith, D.G.1
Gawryluk, R.M.2
Spencer, D.F.3
-
180
-
-
33748424435
-
Cardiac and clinical phenotype in Barth syndrome
-
Spencer CT, Bryant RM, Day J, et al. 2006. Cardiac and clinical phenotype in Barth syndrome. Pediatrics 118:e337-346.
-
(2006)
Pediatrics
, vol.118
-
-
Spencer, C.T.1
Bryant, R.M.2
Day, J.3
-
182
-
-
53049098744
-
Mutation of C20orf7 disrupts complex I assembly and causes lethal neonatal mitochondrial disease
-
Sugiana C, Pagliarini DJ, McKenzie M, et al. 2008. Mutation of C20orf7 disrupts complex I assembly and causes lethal neonatal mitochondrial disease. Am J Hum Genet 83:468-478.
-
(2008)
Am J Hum Genet
, vol.83
, pp. 468-478
-
-
Sugiana, C.1
Pagliarini, D.J.2
McKenzie, M.3
-
183
-
-
65249189438
-
Complex I function is defective in complex IV-deficient Caenorhabditis elegans
-
Suthammarak W, Yang YY, Morgan PG, et al. 2009. Complex I function is defective in complex IV-deficient Caenorhabditis elegans. J Biol Chem 284:6425-6435.
-
(2009)
J Biol Chem
, vol.284
, pp. 6425-6435
-
-
Suthammarak, W.1
Yang, Y.Y.2
Morgan, P.G.3
-
184
-
-
0025100686
-
Biochemical characterization and regulation of cardiolipin synthase in Saccharomyces cerevisiae
-
DOI 10.1016/0005-2760(90)90192-Z
-
Tamai KT, Greenberg ML. 1990. Biochemical characterization and regulation of cardiolipin synthase in Saccharomyces cerevisiae. Biochim Biophys Acta 1046:214-222. (Pubitemid 20287767)
-
(1990)
Biochimica et Biophysica Acta - Lipids and Lipid Metabolism
, vol.1046
, Issue.2
, pp. 214-222
-
-
Tamai, K.T.1
Greenberg, M.L.2
-
185
-
-
77949714959
-
Mislocalization of mitochondria and compromised renal function and
-
Terhzaz S, Cabrero P, Chintapalli VR, et al. 2010. Mislocalization of mitochondria and compromised renal function and oxidative stress resistance in Drosophila SesB mutants. Physiol Genomics 41:33-41.
-
(2010)
Physiol Genomics
, vol.41
, pp. 33-41
-
-
Terhzaz, S.1
Cabrero, P.2
Chintapalli, V.R.3
-
186
-
-
10744231523
-
A complementary transposon tool kit for Drosophila melanogaster using P and piggy-Bac
-
Thibault ST, Singer MA, Miyazaki WY, et al. 2004. A complementary transposon tool kit for Drosophila melanogaster using P and piggy-Bac. Nat Genet 36:283-287.
-
(2004)
Nat Genet
, vol.36
, pp. 283-287
-
-
Thibault, S.T.1
Singer, M.A.2
Miyazaki, W.Y.3
-
187
-
-
0035941485
-
Ingestion of bacterially expressed dsRNAs can produce specific and potent genetic interference in Caenorhabditis elegans
-
Timmons L, Court DL, Fire A. 2001. Ingestion of bacterially expressed dsRNAs can produce specific and potent genetic interference in Caenorhabditis elegans. Gene 263:103-112.
-
(2001)
Gene
, vol.263
, pp. 103-112
-
-
Timmons, L.1
Court, D.L.2
Fire, A.3
-
188
-
-
0034809484
-
Technical knockout, a Drosophila model of mitochondrial deafness
-
Toivonen JM, O'Dell KM, Petit N, et al. 2001. Technical knockout, a Drosophila model of mitochondrial deafness. Genetics 159:241-254.
-
(2001)
Genetics
, vol.159
, pp. 241-254
-
-
Toivonen, J.M.1
O'Dell, K.M.2
Petit, N.3
-
189
-
-
37549049790
-
Characterization of the NuoM (ND4) subunit in Escherichia coli NDH-1: Conserved charged residues essential for energy-coupled activities
-
Torres-Bacete J, Nakamaru-Ogiso E, Matsuno-Yagi A, et al. 2007. Characterization of the NuoM (ND4) subunit in Escherichia coli NDH-1: conserved charged residues essential for energy-coupled activities. J Biol Chem 282:36914-36922.
-
(2007)
J Biol Chem
, vol.282
, pp. 36914-36922
-
-
Torres-Bacete, J.1
Nakamaru-Ogiso, E.2
Matsuno-Yagi, A.3
-
190
-
-
34248195476
-
Endogenous synthesis of coenzyme Q in eukaryotes
-
Tran UC, Clarke CF. 2007. Endogenous synthesis of coenzyme Q in eukaryotes. Mitochondrion 7:S62-S71.
-
(2007)
Mitochondrion
, vol.7
-
-
Tran, U.C.1
Clarke, C.F.2
-
191
-
-
3543111486
-
Cellular bases of activity-dependent paralysis in Drosophila stress-sensitive mutants
-
TrottaN,Rodesch CK, Fergestad T, et al. 2004. Cellular bases of activity-dependent paralysis in Drosophila stress-sensitive mutants. J Neurobiol 60:328-347.
-
(2004)
J Neurobiol
, vol.60
, pp. 328-347
-
-
Trotta, N.1
Rodesch, C.K.2
Fergestad, T.3
-
192
-
-
0036079738
-
Mitochondrial genome content is regulated during nematode development
-
Tsang WY, Lemire BD. 2002. Mitochondrial genome content is regulated during nematode development. Biochem Biophys Res Commun 291:8-16.
-
(2002)
Biochem Biophys Res Commun
, vol.291
, pp. 8-16
-
-
Tsang, W.Y.1
Lemire, B.D.2
-
193
-
-
0038645365
-
The role of mitochondria in the life of the nematode, Caenorhabditis elegans
-
Tsang WY, Lemire BD. 2003. The role of mitochondria in the life of the nematode, Caenorhabditis elegans. Biochim Biophys Acta 1638:91-105.
-
(2003)
Biochim Biophys Acta
, vol.1638
, pp. 91-105
-
-
Tsang, W.Y.1
Lemire, B.D.2
-
194
-
-
0035943727
-
Mitochondrial Respiratory Chain Deficiency in Caenorhabditis elegans Results in Developmental Arrest and Increased Life Span
-
DOI 10.1074/jbc.M103999200
-
Tsang WY, Sayles LC, Grad LI, et al. 2001. Mitochondrial respiratory chain deficiency in Caenorhabditis elegans results in developmental arrest and increased life span. J Biol Chem 276:32240-32246. (Pubitemid 37384888)
-
(2001)
Journal of Biological Chemistry
, vol.276
, Issue.34
, pp. 32240-32246
-
-
Tsang, W.Y.1
Sayles, L.C.2
Grad, L.I.3
Pilgrim, D.B.4
Lemire, B.D.5
-
195
-
-
43449099127
-
The amyotrophic lateral sclerosis 8 protein VAPB is cleaved, secreted, and acts as a ligand for Eph receptors
-
Tsuda H, Han SM, Yang Y, et al. 2008. The amyotrophic lateral sclerosis 8 protein VAPB is cleaved, secreted, and acts as a ligand for Eph receptors. Cell 133:963-977.
-
(2008)
Cell
, vol.133
, pp. 963-977
-
-
Tsuda, H.1
Han, S.M.2
Yang, Y.3
-
196
-
-
0025145542
-
PET genes of Saccharomyces cerevisiae
-
Tzagoloff A, Dieckmann CL. 1990. PET genes of Saccharomyces cerevisiae. Microbiol Rev 54:211-225.
-
(1990)
Microbiol Rev
, vol.54
, pp. 211-225
-
-
Tzagoloff, A.1
Dieckmann, C.L.2
-
197
-
-
0030738589
-
Alternative respiratory pathways of Escherichia coli: Energetics and transcriptional regulation in response to electron acceptors
-
Unden G, Bongaerts J. 1997. Alternative respiratory pathways of Escherichia coli: energetics and transcriptional regulation in response to electron acceptors. Biochim Biophys Acta 1320:217-234.
-
(1997)
Biochim Biophys Acta
, vol.1320
, pp. 217-234
-
-
Unden, G.1
Bongaerts, J.2
-
198
-
-
9144233107
-
The ND1 gene of complex I is a mutational hot spot for Leber's hereditary optic neuropathy
-
Valentino ML, Barboni P, Ghelli A, et al. 2004. The ND1 gene of complex I is a mutational hot spot for Leber's hereditary optic neuropathy. Ann Neurol 56:631-641.
-
(2004)
Ann Neurol
, vol.56
, pp. 631-641
-
-
Valentino, M.L.1
Barboni, P.2
Ghelli, A.3
-
199
-
-
84898708553
-
Reactive oxygen species and aging in Caenorhabditis elegans: Causal or casual relationship?
-
in press
-
Van Raamsdonk JM, Hekimi S. Reactive oxygen species and aging in Caenorhabditis elegans: causal or casual relationship? Antioxid Redox Signal (in press).
-
Antioxid Redox Signal
-
-
Van Raamsdonk, J.M.1
Hekimi, S.2
-
200
-
-
77955503270
-
Decreased energy metabolism extends life span in Caenorhabditis elegans without reducing oxidative damage
-
Van Raamsdonk JM, Meng Y, Camp D, et al. 2010. Decreased energy metabolism extends life span in Caenorhabditis elegans without reducing oxidative damage. Genetics 185:559-571.
-
(2010)
Genetics
, vol.185
, pp. 559-571
-
-
Van Raamsdonk, J.M.1
Meng, Y.2
Camp, D.3
-
201
-
-
0031576839
-
Abnormalities in mitochondria-associated membranes and phospholipid biosynthetic enzymes in the mnd/mnd mouse model of neuronal ceroid lipofuscinosis
-
Vance JE, Stone SJ, et al. 1997. Abnormalities in mitochondria-associated membranes and phospholipid biosynthetic enzymes in the mnd/mnd mouse model of neuronal ceroid lipofuscinosis. Biochim Biophys Acta 1344:286-299.
-
(1997)
Biochim Biophys Acta
, vol.1344
, pp. 286-299
-
-
Vance, J.E.1
Stone, S.J.2
-
202
-
-
0242322008
-
Only One Splice Variant of the Human TAZ Gene Encodes a Functional Protein with a Role in Cardiolipin Metabolism
-
DOI 10.1074/jbc.M305956200
-
Vaz FM, Houtkooper RH, Valianpour F, et al. 2003. Only one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolism. J Biol Chem 278: 43089-43094. (Pubitemid 37345925)
-
(2003)
Journal of Biological Chemistry
, vol.278
, Issue.44
, pp. 43089-43094
-
-
Vaz, F.M.1
Houtkooper, R.H.2
Valianpour, F.3
Barth, P.G.4
Wanders, R.J.A.5
-
203
-
-
30044434872
-
Similar patterns of mitochondrial vulnerability and rescue induced by genetic modification of alpha-synuclein, parkin, and DJ-1 in Caenorhabditis elegans
-
Ved R, Saha S, Westlund B, et al. 2005. Similar patterns of mitochondrial vulnerability and rescue induced by genetic modification of alpha-synuclein, parkin, and DJ-1 in Caenorhabditis elegans. J Biol Chem 280:42655-42668.
-
(2005)
J Biol Chem
, vol.280
, pp. 42655-42668
-
-
Ved, R.1
Saha, S.2
Westlund, B.3
-
204
-
-
20444366238
-
Amino acid residues associated with cluster N3 in the NuoF subunit of the proton-translocating NADH-quinone oxidoreductase from Escherichia coli
-
Velazquez I, Nakamaru-Ogiso E, Yano T, et al. 2005. Amino acid residues associated with cluster N3 in the NuoF subunit of the proton-translocating NADH-quinone oxidoreductase from Escherichia coli. FEBS Lett 579:3164-3168.
-
(2005)
FEBS Lett
, vol.579
, pp. 3164-3168
-
-
Velazquez, I.1
Nakamaru-Ogiso, E.2
Yano, T.3
-
205
-
-
33751437445
-
Long-lived C. elegans mitochondrial mutants as a model for human mitochondrial-associated diseases
-
Ventura N, Rea SL, Testi R. 2006. Long-lived C. elegans mitochondrial mutants as a model for human mitochondrial-associated diseases. Exp Gerontol 41:974-991.
-
(2006)
Exp Gerontol
, vol.41
, pp. 974-991
-
-
Ventura, N.1
Rea, S.L.2
Testi, R.3
-
206
-
-
23044506102
-
Synaptic mitochondria are critical for mobilization of reserve pool vesicles at Drosophila neuromuscular junctions
-
DOI 10.1016/j.neuron.2005.06.018, PII S0896627305005234
-
Verstreken P, Ly CV, Venken KJ, et al. 2005. Synaptic mitochondria are critical for mobilization of reserve pool vesicles at Drosophila neuromuscular junctions. Neuron 47:365-378. (Pubitemid 41073878)
-
(2005)
Neuron
, vol.47
, Issue.3
, pp. 365-378
-
-
Verstreken, P.1
Ly, C.V.2
Venken, K.J.T.3
Koh, T.-W.4
Zhou, Y.5
Bellen, H.J.6
-
207
-
-
0033920064
-
Plasma membrane redox system in the control of stress-induced apoptosis
-
Villalba JM, Navas P. 2000. Plasma membrane redox system in the control of stress-induced apoptosis. Antioxid Redox Signal 2:213-230. (Pubitemid 30445934)
-
(2000)
Antioxidants and Redox Signaling
, vol.2
, Issue.2
, pp. 213-230
-
-
Villalba, J.M.1
Navas, P.2
-
208
-
-
0038620481
-
New perspectives on the regulation of intermembrane glycerophospholipid traffic
-
Voelker DR. 2003. New perspectives on the regulation of intermembrane glycerophospholipid traffic. J Lipid Res 44:441-449.
-
(2003)
J Lipid Res
, vol.44
, pp. 441-449
-
-
Voelker, D.R.1
-
209
-
-
21744445061
-
Bridging gaps in phospholipid transport
-
Voelker DR. 2005. Bridging gaps in phospholipid transport. Trends Biochem Sci 30:396-404.
-
(2005)
Trends Biochem Sci
, vol.30
, pp. 396-404
-
-
Voelker, D.R.1
-
210
-
-
33750840222
-
Hypersensitivity to oxygen and shortened lifespan in a Drosophila mitochondrial complex II mutant
-
Walker DW, Hajek P, Muffat J, et al. 2006. Hypersensitivity to oxygen and shortened lifespan in a Drosophila mitochondrial complex II mutant. Proc Natl Acad Sci USA 103:16382-16387.
-
(2006)
Proc Natl Acad Sci USA
, vol.103
, pp. 16382-16387
-
-
Walker, D.W.1
Hajek, P.2
Muffat, J.3
-
211
-
-
0033672549
-
Mitochondria-targeted green fluorescent proteins: Convenient tools for the study of organelle biogenesis in Saccharomyces cerevisiae
-
Westermann B, Neupert W. 2000. Mitochondria-targeted green fluorescent proteins: convenient tools for the study of organelle biogenesis in Saccharomyces cerevisiae. Yeast 16:1421-1427.
-
(2000)
Yeast
, vol.16
, pp. 1421-1427
-
-
Westermann, B.1
Neupert, W.2
-
213
-
-
0028695434
-
Mosaic analysis using FLP recombinase
-
Xu T, Harrison SD. 1994. Mosaic analysis using FLP recombinase. Methods Cell Biol 44:655-681.
-
(1994)
Methods Cell Biol
, vol.44
, pp. 655-681
-
-
Xu, T.1
Harrison, S.D.2
-
215
-
-
0345803935
-
Remodeling of cardiolipin by phospholipid transacylation
-
Xu Y, Kelley RI, Blanck TJ, et al. 2003. Remodeling of cardiolipin by phospholipid transacylation. J Biol Chem 278:51380-51385.
-
(2003)
J Biol Chem
, vol.278
, pp. 51380-51385
-
-
Xu, Y.1
Kelley, R.I.2
Blanck, T.J.3
-
216
-
-
0032490115
-
Procaryotic complex I (NDH-1), an overview
-
Yagi T, Yano T, Di Bernardo S, et al. 1998. Procaryotic complex I (NDH-1), an overview. Biochim Biophys Acta 1364:125-133.
-
(1998)
Biochim Biophys Acta
, vol.1364
, pp. 125-133
-
-
Yagi, T.1
Yano, T.2
Di Bernardo, S.3
-
217
-
-
77956241785
-
Two modes of mitochondrial dysfunction lead independently to lifespan extension in Caenorhabditis elegans
-
Yang W, Hekimi S. 2010. Two modes of mitochondrial dysfunction lead independently to lifespan extension in Caenorhabditis elegans. Aging Cell 9:433-447.
-
(2010)
Aging Cell
, vol.9
, pp. 433-447
-
-
Yang, W.1
Hekimi, S.2
-
218
-
-
0033215197
-
Characterization of the putative 2x[4Fe-4S]-binding NQO9 subunit of the proton-translocating NADH-quinone oxidoreductase (NDH-1) of Paracoccus denitrificans. Expression, reconstitution, and EPR characterization
-
Yano T, Magnitsky S, Sled VD, et al. 1999. Characterization of the putative 2x[4Fe-4S]-binding NQO9 subunit of the proton-translocating NADH-quinone oxidoreductase (NDH-1) of Paracoccus denitrificans. Expression, reconstitution, and EPR characterization. J Biol Chem 274:28598-28605.
-
(1999)
J Biol Chem
, vol.274
, pp. 28598-28605
-
-
Yano, T.1
Magnitsky, S.2
Sled, V.D.3
-
219
-
-
0037844859
-
Characterization of cluster N5 as a fast-relaxing [4Fe-4S] cluster in the Nqo3 subunit of the proton-translocating NADH-ubiquinone oxidoreductase from Paracoccus denitrificans
-
Yano T, Sklar J, Nakamaru-Ogiso E, et al. 2003. Characterization of cluster N5 as a fast-relaxing [4Fe-4S] cluster in the Nqo3 subunit of the proton-translocating NADH-ubiquinone oxidoreductase from Paracoccus denitrificans. J Biol Chem 278:15514-15522.
-
(2003)
J Biol Chem
, vol.278
, pp. 15514-15522
-
-
Yano, T.1
Sklar, J.2
Nakamaru-Ogiso, E.3
-
220
-
-
0028091327
-
Expression of the 25-kilodalton iron-sulfur subunit of the energy- Transducing NADH-ubiquinone oxidoreductase of Paracoccus denitrificans
-
Yano T, Sled VD, Ohnishi T, et al. 1994. Expression of the 25-kilodalton iron-sulfur subunit of the energy-transducing NADH-ubiquinone oxidoreductase of Paracoccus denitrificans. Biochemistry 33:494-499. (Pubitemid 24048092)
-
(1994)
Biochemistry
, vol.33
, Issue.2
, pp. 494-499
-
-
Yano, T.1
Sled, V.D.2
Ohnishi, T.3
Yagi, T.4
-
221
-
-
0029112808
-
Expression and characterization of the 66-kilodalton (NQO3) iron-sulfur subunit of the proton-translocating NADH-quinone oxidoreductase of Paracoccus denitrificans
-
Yano T, Yagi T, Sled VD, et al. 1995. Expression and characterization of the 66-kilodalton (NQO3) iron-sulfur subunit of the proton-translocating NADH-quinone oxidoreductase of Paracoccus denitrificans. J Biol Chem 270:18264-18270.
-
(1995)
J Biol Chem
, vol.270
, pp. 18264-18270
-
-
Yano, T.1
Yagi, T.2
Sled, V.D.3
-
222
-
-
38949208881
-
The molecular mechanisms of OPA1-mediated optic atrophy in Drosophila model and prospects for antioxidant treatment
-
Yarosh W, Monserrate J, Tong JJ, et al. The molecular mechanisms of OPA1-mediated optic atrophy in Drosophila model and prospects for antioxidant treatment. PLoS Genet 4:e6, 2008.
-
(2008)
PLoS Genet
, vol.4
-
-
Yarosh, W.1
Monserrate, J.2
Tong, J.J.3
-
223
-
-
77950553262
-
Fumarase: A mitochondrial metabolic enzyme and a cytosolic/nuclear component of the DNA damage response
-
Yogev O, Yogev O, Singer E, et al. 2010. Fumarase: a mitochondrial metabolic enzyme and a cytosolic/nuclear component of the DNA damage response. PLoS Biol 8:e1000328.
-
(2010)
PLoS Biol
, vol.8
-
-
Yogev, O.1
Yogev, O.2
Singer, E.3
-
225
-
-
0032566316
-
Analysis of the pathogenic human mitochondrial mutation ND1/3460, and mutations of strictly conserved residues in its vicinity, using the bacterium Paracoccus denitrificans
-
DOI 10.1021/bi9810555
-
Zickermann V, Barquera B, Wikstrom M, et al. 1998. Analysis of the pathogenic human mitochondrial mutation ND1/3460, and mutations of strictly conserved residues in its vicinity, using the bacterium Paracoccus denitrificans. Biochemistry 37:11792-11796. (Pubitemid 28400050)
-
(1998)
Biochemistry
, vol.37
, Issue.34
, pp. 11792-11796
-
-
Zickermann, V.1
Barquera, B.2
Wikstrom, M.3
Finel, M.4
-
226
-
-
0026082909
-
Phospholipid synthesis and lipid composition of subcellular membranes in the unicellular eukaryote Saccharomyces cerevisiae
-
Zinser E, Sperka-Gottlieb CD, Fasch EV, et al. 1991. Phospholipid synthesis and lipid composition of subcellular membranes in the unicellular eukaryote Saccharomyces cerevisiae. J Bacteriol 173:2026-2034.
-
(1991)
J Bacteriol
, vol.173
, pp. 2026-2034
-
-
Zinser, E.1
Sperka-Gottlieb, C.D.2
Fasch, E.V.3
|