Mitochondrial complex I mutations in Caenorhabditis elegans produce cytochrome c oxidase deficiency, oxidative stress and vitamin-responsive lactic acidosis

Human Molecular Genetics

Volumn 13, Issue 3, 2004, Pages 303-314

  Grad, Leslie I ^a   Lemire, Bernard D ^a  

^a UNIVERSITY OF ALBERTA   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; DICHLOROACETIC ACID; PYRUVATE DEHYDROGENASE COMPLEX; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); RIBOFLAVIN; THIAMINE;

ARTICLE; CAENORHABDITIS ELEGANS; CONTROLLED STUDY; CYTOCHROME C OXIDASE DEFICIENCY; DEFENSE MECHANISM; DISEASE SEVERITY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; ENZYME SUBUNIT; GENE MUTATION; GENETIC CODE; INCIDENCE; LACTIC ACIDOSIS; MISSENSE MUTATION; MITOCHONDRIAL RESPIRATION; NEUROLOGIC DISEASE; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; RESPIRATORY CHAIN; STRAIN DIFFERENCE; TRANSGENIC ORGANISM;

ACIDOSIS, LACTIC; AGING; ANIMALS; ANIMALS, GENETICALLY MODIFIED; CAENORHABDITIS ELEGANS; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX IV; ENZYME ACTIVATORS; OXIDATIVE STRESS; PYRUVATE DEHYDROGENASE COMPLEX; VITAMINS;

ANIMALIA; CAENORHABDITIS; CAENORHABDITIS ELEGANS; INVERTEBRATA; NEMATODA;

EID: 1042268861     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh027     Document Type: Article

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