Abnormalities in mitochondria-associated membranes and phospholipid biosynthetic enzymes in the mnd/mnd mouse model of neuronal ceroid lipofuscinosis

Biochimica et Biophysica Acta - Lipids and Lipid Metabolism

Volumn 1344, Issue 3, 1997, Pages 286-299

  Vance, Jean E ^a   Stone, Scot J ^a   Faust, Jerry R ^b  

^a UNIVERSITY OF ALBERTA   (Canada)

^b TUFTS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Lipid transport; Mitochondrion; mnd mnd mutant; Mouse liver; Neuronal ceroid lipofuscinosis; Phosphatidylethanolamine methyltransferase; Phospholipid

Indexed keywords

CHOLINE PHOSPHATE CYTIDYLYLTRANSFERASE; CYTOCHROME B5; CYTOCHROME B5 REDUCTASE; MESSENGER RNA; PHOSPHATIDYLETHANOLAMINE METHYLTRANSFERASE; PHOSPHATIDYLSERINE SYNTHASE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

AGE; ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL FRACTIONATION; CONTROLLED STUDY; CYTOCHEMISTRY; LIVER; LIVER CELL; LIVER MICROSOME; MOUSE; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PHOSPHOLIPID METABOLISM; PRIORITY JOURNAL;

ANIMALS; CELL FRACTIONATION; DIACYLGLYCEROL CHOLINEPHOSPHOTRANSFERASE; DISEASE MODELS, ANIMAL; ETHANOLAMINEPHOSPHOTRANSFERASE; HUMANS; INTRACELLULAR MEMBRANES; LIPIDS; LIVER; METHYLTRANSFERASES; MICE; MICE, MUTANT STRAINS; MITOCHONDRIA, LIVER; NEURONAL CEROID-LIPOFUSCINOSES; NITROGENOUS GROUP TRANSFERASES; PHOSPHATIDYLETHANOLAMINE N-METHYLTRANSFERASE; PHOSPHOLIPIDS; RNA, MESSENGER; SUBCELLULAR FRACTIONS; TRANSFERASES;

EID: 0031576839     PISSN: 00052760     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0005-2760(96)00153-1     Document Type: Article

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