A Drosophila model of Barth syndrome

Proceedings of the National Academy of Sciences of the United States of America

Volumn 103, Issue 31, 2006, Pages 11584-11588

  Xu, Yang ^a   Condell, Morgan ^a   Plesken, Heide ^a   Edelman Novemsky, Irit ^a   Ma, Jinping ^a   Ren, Mindong ^a   Schlame, Michael ^a  

^a NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Cardiolipin; Mitochondria; Myopathy

Indexed keywords

ACYLTRANSFERASE; CARDIOLIPIN; PHOSPHATIDYLCHOLINE; PHOSPHATIDYLETHANOLAMINE; PHOSPHOLIPID; TAFAZZIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BARTH SYNDROME; BIODIVERSITY; CARDIOMYOPATHY; CONTROLLED STUDY; DISEASE MODEL; DROSOPHILA; GENE IDENTIFICATION; GENE MUTATION; MITOCHONDRIAL MYOPATHY; MITOCHONDRIAL RESPIRATION; MOLECULAR BIOLOGY; MUSCLE WEAKNESS; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; RNA ANALYSIS; SKELETAL MUSCLE; TRANSCRIPTION REGULATION; WESTERN BLOTTING; X CHROMOSOME LINKED DISORDER;

1-ACYLGLYCEROPHOSPHOCHOLINE O-ACYLTRANSFERASE; ANIMALS; ANIMALS, GENETICALLY MODIFIED; CARDIOLIPINS; CARDIOMYOPATHY, DILATED; DISEASE MODELS, ANIMAL; DROSOPHILA MELANOGASTER; DROSOPHILA PROTEINS; GENETIC DISEASES, X-LINKED; HUMANS; MITOCHONDRIAL MYOPATHIES; MOTOR ACTIVITY; MUSCLE, SKELETAL; PHOSPHATIDYLCHOLINES; PHOSPHATIDYLETHANOLAMINES; PROTEIN ISOFORMS; PROTEINS; SYNDROME; TRANSCRIPTION FACTORS;

DROSOPHILA MELANOGASTER;

EID: 33746853114     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0603242103     Document Type: Article

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