SCOPUS 정보 검색 플랫폼

Journal of Neurology

Volumn 256, Issue SUPPL. 1, 2009, Pages 9-17

The pathogenesis of Friedreich ataxia and the structure and function of frataxin

(2) Pandolfo, Massimo a Pastore, Annalisa b

a ERASME HOSPITAL (Belgium)

b NATIONAL INSTITUTE FOR MEDICAL RESEARCH (United Kingdom)

Author keywords

Iron metabolism; Mitochondria; Oxidative stress

Indexed keywords

ASPARTIC ACID; CHAPERONE; FRATAXIN; GLUTAMIC ACID; GLUTATHIONE; GLUTATHIONE TRANSFERASE; IRON; IRON REGULATORY PROTEIN 1; IRON REGULATORY PROTEIN 2; REACTIVE OXYGEN METABOLITE; SULFUR; SULFUR AMINO ACID;

AMINO TERMINAL SEQUENCE; BETA SHEET; CARBOXY TERMINAL SEQUENCE; CELL STRESS; CELLULAR STRESS RESPONSE; ENERGY METABOLISM; EUKARYOTE; FRIEDREICH ATAXIA; HEME SYNTHESIS; HUMAN; IRON BINDING CAPACITY; IRON METABOLISM; METABOLIC DISORDER; MITOCHONDRION; NEUROPATHOLOGY; NONHUMAN; ORTHOLOGY; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN FUNCTION; PROTEIN STABILITY; PROTEIN STRUCTURE; REVIEW; SEQUENCE ALIGNMENT; SEQUENCE HOMOLOGY;

ANIMALS; FRIEDREICH ATAXIA; HUMANS; IRON-BINDING PROTEINS; METABOLIC DISEASES; MODELS, MOLECULAR; PROTEIN BINDING; PROTEIN FOLDING;

EID: 62549093116 PISSN: 03405354 EISSN: 14321459 Source Type: Journal
DOI: 10.1007/s00415-009-1003-2 Document Type: Review

Times cited : (209)

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