Frataxin expression rescues mitochondrial dysfunctions in FRDA cells

Human Molecular Genetics

Volumn 10, Issue 19, 2001, Pages 2099-2107

  Tan, Guolin ^a   Chen, Li Sheng ^a   Lonnerdal, Bo ^a   Gellera, Cinzia ^b   Taroni, Franco A ^b   Cortopassi, Gino A ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ACONITATE HYDRATASE; FERROUS GLUCONATE; FRATAXIN; HYDROGEN PEROXIDE; IRON;

ARTICLE; CASE REPORT; CELL DEATH; CELL NUCLEUS; CHEMICAL REACTION; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; EVIDENCE BASED MEDICINE; EXPOSURE; FILTRATION; FRIEDREICH ATAXIA; GENE MUTATION; GENE OVEREXPRESSION; GENETIC CODE; GENETIC TRANSFECTION; HETEROZYGOTE; HOMEOSTASIS; HUMAN; HUMAN CELL; HYPOTHESIS; IRON METABOLISM; LYMPHOBLAST; MEMBRANE POTENTIAL; MITOCHONDRIAL MEMBRANE; MITOCHONDRION; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PHENOTYPE; PHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROVOCATION TEST; TOXICITY;

ATAXIA;

EID: 0034778511     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/10.19.2099     Document Type: Article

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