Maturation of wild-type and mutated frataxin by the mitochondrial processing peptidase

Human Molecular Genetics

Volumn 7, Issue 9, 1998, Pages 1485-1489

  Koutnikova, Hana ^a   Campuzano, Victoria ^a   Koenig, Michel ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

Author keywords

[No Author keywords available]

Indexed keywords

CELL MEMBRANE PROTEIN; FRATAXIN; PEPTIDASE; UNCLASSIFIED DRUG;

ARTICLE; FRIEDREICH ATAXIA; HUMAN; IRON TRANSPORT; MISSENSE MUTATION; MITOCHONDRIAL MEMBRANE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN PROTEIN INTERACTION;

ANIMALS; BASE SEQUENCE; COS CELLS; DIMERIZATION; DNA PRIMERS; FRIEDREICH ATAXIA; GENE EXPRESSION; HUMANS; IRON-BINDING PROTEINS; METALLOENDOPEPTIDASES; MITOCHONDRIA; MUTATION; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); POLYMERASE CHAIN REACTION; PROTEIN PROCESSING, POST-TRANSLATIONAL; RECOMBINANT PROTEINS; SACCHAROMYCES CEREVISIAE;

ATAXIA;

EID: 0031656903     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/7.9.1485     Document Type: Article

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