Mouse models for mitochondrial disease

American Journal of Medical Genetics - Seminars in Medical Genetics

Volumn 106, Issue 1, 2001, Pages 71-93

  Raha, Sandeep ^b   Robinson, Brian H ^a  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^b NONE

Author keywords

Mitochondrial disease; Mouse models; Reactive oxygen species; Transgenic animals

Indexed keywords

ADENOSINE DIPHOSPHATE; ADENOSINE TRIPHOSPHATE; CELL NUCLEUS DNA; CHLORAMPHENICOL; GLUTATHIONE PEROXIDASE; MITOCHONDRIAL DNA; REACTIVE OXYGEN METABOLITE; RIBOSOME RNA; SUPEROXIDE DISMUTASE; TRANSCRIPTION FACTOR; TRANSFER RNA; UNCOUPLING PROTEIN;

AMINO ACID SUBSTITUTION; ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; ARTICLE; CARDIOMYOPATHY; CATARACT; DIABETES MELLITUS; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GENE DELETION; GENE MUTATION; GROWTH RETARDATION; KIDNEY DISEASE; MOUSE; MYOPATHY; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL;

ANIMALS; DISEASE MODELS, ANIMAL; DNA, MITOCHONDRIAL; GENE DELETION; HUMANS; MICE; MITOCHONDRIAL DISEASES; MODELS, BIOLOGICAL; MUTATION; NEURODEGENERATIVE DISEASES; POTASSIUM CHANNELS; RNA, RIBOSOMAL, 16S; STRESS;

EID: 0034956656     PISSN: 01487299     EISSN: None     Source Type: Journal    
DOI: 10.1002/ajmg.1393     Document Type: Article

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