-
1
-
-
84929044427
-
IL-17A induces Pendrin expression and chloride-bicarbonate exchange in human bronchial epithelial cells
-
Abraham, V., Spielman, D., Kolls, J.K., Rubenstein, R.C., Conner, G.E., et al. IL-17A induces Pendrin expression and chloride-bicarbonate exchange in human bronchial epithelial cells. PLoS One, 9(8), 2014, e103263.
-
(2014)
PLoS One
, vol.9
, Issue.8
, pp. e103263
-
-
Abraham, V.1
Spielman, D.2
Kolls, J.K.3
Rubenstein, R.C.4
Conner, G.E.5
-
2
-
-
84992571551
-
Short palate, lung, and nasal epithelial clone 1 has antimicrobial and antibiofilm activities against the burkholderia cepacia complex
-
Ahmad, S., Tyrrell, J., Walton, W.G., Tripathy, A., Redinbo, M.R., Tarran, R., Short palate, lung, and nasal epithelial clone 1 has antimicrobial and antibiofilm activities against the burkholderia cepacia complex. Antimicrobial Agents and Chemotherapy 60:10 (2016), 6003–6012.
-
(2016)
Antimicrobial Agents and Chemotherapy
, vol.60
, Issue.10
, pp. 6003-6012
-
-
Ahmad, S.1
Tyrrell, J.2
Walton, W.G.3
Tripathy, A.4
Redinbo, M.R.5
Tarran, R.6
-
3
-
-
84904279683
-
Cystic fibrosis transmembrane conductance regulator dysfunction in VIP knockout mice
-
Alcolado, N.G., Conrad, D.J., Poroca, D., Li, M., Alshafie, W., Chappe, F.G., et al. Cystic fibrosis transmembrane conductance regulator dysfunction in VIP knockout mice. American Journal of Physiology. Cell Physiology 307:2 (2014), C195–C207.
-
(2014)
American Journal of Physiology. Cell Physiology
, vol.307
, Issue.2
, pp. C195-C207
-
-
Alcolado, N.G.1
Conrad, D.J.2
Poroca, D.3
Li, M.4
Alshafie, W.5
Chappe, F.G.6
-
4
-
-
84875206850
-
The SLC26 gene family of anion transporters and channels
-
Alper, S.L., Sharma, A.K., The SLC26 gene family of anion transporters and channels. Molecular Aspects of Medicine 34:2–3 (2013), 494–515.
-
(2013)
Molecular Aspects of Medicine
, vol.34
, Issue.2-3
, pp. 494-515
-
-
Alper, S.L.1
Sharma, A.K.2
-
5
-
-
0025931429
-
Nucleoside triphosphates are required to open the CFTR chloride channel
-
Anderson, M.P., Berger, H.A., Rich, D.P., Gregory, R.J., Smith, A.E., Welsh, M.J., Nucleoside triphosphates are required to open the CFTR chloride channel. Cell 67:4 (1991), 775–784.
-
(1991)
Cell
, vol.67
, Issue.4
, pp. 775-784
-
-
Anderson, M.P.1
Berger, H.A.2
Rich, D.P.3
Gregory, R.J.4
Smith, A.E.5
Welsh, M.J.6
-
6
-
-
84938081322
-
The relationship of mucus concentration (hydration) to mucus osmotic pressure and transport in chronic bronchitis
-
Anderson, W.H., Coakley, R.D., Button, B., Henderson, A.G., Zeman, K.L., Alexis, N.E., et al. The relationship of mucus concentration (hydration) to mucus osmotic pressure and transport in chronic bronchitis. American Journal of Respiratory and Critical Care Medicine 192:2 (2015), 182–190.
-
(2015)
American Journal of Respiratory and Critical Care Medicine
, vol.192
, Issue.2
, pp. 182-190
-
-
Anderson, W.H.1
Coakley, R.D.2
Button, B.3
Henderson, A.G.4
Zeman, K.L.5
Alexis, N.E.6
-
7
-
-
0030768159
-
Lower airway inflammation in infants and young children with cystic fibrosis
-
Armstrong, D.S., Grimwood, K., Carlin, J.B., Carzino, R., Gutierrez, J.P., Hull, J., et al. Lower airway inflammation in infants and young children with cystic fibrosis. American Journal of Respiratory and Critical Care Medicine 156:4 Pt 1 (1997), 1197–1204.
-
(1997)
American Journal of Respiratory and Critical Care Medicine
, vol.156
, Issue.4
, pp. 1197-1204
-
-
Armstrong, D.S.1
Grimwood, K.2
Carlin, J.B.3
Carzino, R.4
Gutierrez, J.P.5
Hull, J.6
-
8
-
-
84920273225
-
Linking increased airway hydration, ciliary beating, and mucociliary clearance through ENaC inhibition
-
Astrand, A.B., Hemmerling, M., Root, J., Wingren, C., Pesic, J., Johansson, E., et al. Linking increased airway hydration, ciliary beating, and mucociliary clearance through ENaC inhibition. American Journal of physiology. Lung Cellular and Molecular Physiology 308:1 (2015), L22–L32.
-
(2015)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.308
, Issue.1
, pp. L22-L32
-
-
Astrand, A.B.1
Hemmerling, M.2
Root, J.3
Wingren, C.4
Pesic, J.5
Johansson, E.6
-
9
-
-
78049250871
-
SLC26A9 stimulates CFTR expression and function in human bronchial cell lines
-
Avella, M., Loriol, C., Boulukos, K., Borgese, F., Ehrenfeld, J., SLC26A9 stimulates CFTR expression and function in human bronchial cell lines. Journal of Cellular Physiology 226:1 (2011), 212–223.
-
(2011)
Journal of Cellular Physiology
, vol.226
, Issue.1
, pp. 212-223
-
-
Avella, M.1
Loriol, C.2
Boulukos, K.3
Borgese, F.4
Ehrenfeld, J.5
-
10
-
-
84888632051
-
Antimicrobial peptides
-
Bahar, A.A., Ren, D., Antimicrobial peptides. Pharmaceuticals 6:12 (2013), 1543–1575.
-
(2013)
Pharmaceuticals
, vol.6
, Issue.12
, pp. 1543-1575
-
-
Bahar, A.A.1
Ren, D.2
-
11
-
-
0032906408
-
The innate immune system in cystic fibrosis lung disease
-
Bals, R., Weiner, D.J., Wilson, J.M., The innate immune system in cystic fibrosis lung disease. Journal of Clinical Investigation 103:3 (1999), 303–307.
-
(1999)
Journal of Clinical Investigation
, vol.103
, Issue.3
, pp. 303-307
-
-
Bals, R.1
Weiner, D.J.2
Wilson, J.M.3
-
12
-
-
59449095025
-
Molecular diversity and function of K+ channels in airway and alveolar epithelial cells
-
Bardou, O., Trinh, N.T., Brochiero, E., Molecular diversity and function of K+ channels in airway and alveolar epithelial cells. American Journal of physiology. Lung Cellular and Molecular Physiology 296:2 (2009), L145–L155.
-
(2009)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.296
, Issue.2
, pp. L145-L155
-
-
Bardou, O.1
Trinh, N.T.2
Brochiero, E.3
-
13
-
-
84879640376
-
Type 2 alveolar cells are stem cells in adult lung
-
Barkauskas, C.E., Cronce, M.J., Rackley, C.R., Bowie, E.J., Keene, D.R., Stripp, B.R., et al. Type 2 alveolar cells are stem cells in adult lung. The Journal of Clinical Investigation 123:7 (2013), 3025–3036.
-
(2013)
The Journal of Clinical Investigation
, vol.123
, Issue.7
, pp. 3025-3036
-
-
Barkauskas, C.E.1
Cronce, M.J.2
Rackley, C.R.3
Bowie, E.J.4
Keene, D.R.5
Stripp, B.R.6
-
14
-
-
79960866459
-
PLUNC: A multifunctional surfactant of the airways
-
Bartlett, J., Gakhar, L., Penterman, J., Singh, P., Mallampalli, R.K., Porter, E., et al. PLUNC: A multifunctional surfactant of the airways. Biochemical Society Transactions 39:4 (2011), 1012–1016.
-
(2011)
Biochemical Society Transactions
, vol.39
, Issue.4
, pp. 1012-1016
-
-
Bartlett, J.1
Gakhar, L.2
Penterman, J.3
Singh, P.4
Mallampalli, R.K.5
Porter, E.6
-
15
-
-
84992436652
-
Newborn cystic fibrosis pigs have a blunted early response to an inflammatory stimulus
-
Bartlett, J.A., Ramachandran, S., Wohlford-Lenane, C.L., Barker, C.K., Pezzulo, A.A., Zabner, J., et al. Newborn cystic fibrosis pigs have a blunted early response to an inflammatory stimulus. American Journal of Respiratory and Critical Care Medicine 194:7 (2016), 845–854.
-
(2016)
American Journal of Respiratory and Critical Care Medicine
, vol.194
, Issue.7
, pp. 845-854
-
-
Bartlett, J.A.1
Ramachandran, S.2
Wohlford-Lenane, C.L.3
Barker, C.K.4
Pezzulo, A.A.5
Zabner, J.6
-
16
-
-
0030589158
-
Towards membrane protein design: pH-sensitive topology of histidine-containing polypeptides
-
Bechinger, B., Towards membrane protein design: pH-sensitive topology of histidine-containing polypeptides. Journal of Molecular Biology 263:5 (1996), 768–775.
-
(1996)
Journal of Molecular Biology
, vol.263
, Issue.5
, pp. 768-775
-
-
Bechinger, B.1
-
17
-
-
1442325340
-
Cytokine secretion by cystic fibrosis airway epithelial cells
-
Becker, M.N., Sauer, M.S., Muhlebach, M.S., Hirsh, A.J., Wu, Q., Verghese, M.W., et al. Cytokine secretion by cystic fibrosis airway epithelial cells. American Journal of Respiratory and Critical Care Medicine 169:5 (2004), 645–653.
-
(2004)
American Journal of Respiratory and Critical Care Medicine
, vol.169
, Issue.5
, pp. 645-653
-
-
Becker, M.N.1
Sauer, M.S.2
Muhlebach, M.S.3
Hirsh, A.J.4
Wu, Q.5
Verghese, M.W.6
-
18
-
-
0026077676
-
Identification and regulation of the cystic fibrosis transmembrane conductance regulator-generated chloride channel
-
Berger, H.A., Anderson, M.P., Gregory, R.J., Thompson, S., Howard, P.W., Maurer, R.A., et al. Identification and regulation of the cystic fibrosis transmembrane conductance regulator-generated chloride channel. Journal of Clinical Investigation 88:4 (1991), 1422–1431.
-
(1991)
Journal of Clinical Investigation
, vol.88
, Issue.4
, pp. 1422-1431
-
-
Berger, H.A.1
Anderson, M.P.2
Gregory, R.J.3
Thompson, S.4
Howard, P.W.5
Maurer, R.A.6
-
19
-
-
84901604661
-
Effects of airway surface liquid pH on host defense in cystic fibrosis
-
Berkebile, A.R., McCray, P.B. Jr., Effects of airway surface liquid pH on host defense in cystic fibrosis. Int J Biochem Cell Biol 52 (2014), 124–129.
-
(2014)
Int J Biochem Cell Biol
, vol.52
, pp. 124-129
-
-
Berkebile, A.R.1
McCray, P.B.2
-
20
-
-
64549085967
-
SLC26A9 is a constitutively active, CFTR-regulated anion conductance in human bronchial epithelia
-
Bertrand, C.A., Zhang, R., Pilewski, J.M., Frizzell, R.A., SLC26A9 is a constitutively active, CFTR-regulated anion conductance in human bronchial epithelia. The Journal of General Physiology 133:4 (2009), 421–438.
-
(2009)
The Journal of General Physiology
, vol.133
, Issue.4
, pp. 421-438
-
-
Bertrand, C.A.1
Zhang, R.2
Pilewski, J.M.3
Frizzell, R.A.4
-
21
-
-
0028240276
-
Protease-antiprotease imbalance in the lungs of children with cystic fibrosis
-
Birrer, P., McElvaney, N.G., Rudeberg, A., Sommer, C.W., Liechti-Gallati, S., Kraemer, R., et al. Protease-antiprotease imbalance in the lungs of children with cystic fibrosis. American Journal of Respiratory and Critical Care Medicine 150:1 (1994), 207–213.
-
(1994)
American Journal of Respiratory and Critical Care Medicine
, vol.150
, Issue.1
, pp. 207-213
-
-
Birrer, P.1
McElvaney, N.G.2
Rudeberg, A.3
Sommer, C.W.4
Liechti-Gallati, S.5
Kraemer, R.6
-
22
-
-
85057510049
-
An approach to testing undiluted e-cigarette aerosol in vitro using 3D reconstituted human airway epithelium
-
S0887-2333(18)30011-0
-
Bishop, E., Haswell, L., Adamson, J., Costigan, S., Thorne, D., Gaca, M., An approach to testing undiluted e-cigarette aerosol in vitro using 3D reconstituted human airway epithelium. Toxicology in Vitro, 2018 S0887-2333(18)30011-0.
-
(2018)
Toxicology in Vitro
-
-
Bishop, E.1
Haswell, L.2
Adamson, J.3
Costigan, S.4
Thorne, D.5
Gaca, M.6
-
23
-
-
0036258208
-
Cystic fibrosis: A worldwide analysis of CFTR mutations–correlation with incidence data and application to screening
-
Bobadilla, J.L., Macek, M. Jr., Fine, J.P., Farrell, P.M., Cystic fibrosis: A worldwide analysis of CFTR mutations–correlation with incidence data and application to screening. Human Mutation 19:6 (2002), 575–606.
-
(2002)
Human Mutation
, vol.19
, Issue.6
, pp. 575-606
-
-
Bobadilla, J.L.1
Macek, M.2
Fine, J.P.3
Farrell, P.M.4
-
24
-
-
84941049266
-
CFTR, bicarbonate, and the pathophysiology of cystic fibrosis
-
Borowitz, D., CFTR, bicarbonate, and the pathophysiology of cystic fibrosis. Pediatric Pulmonology 50:Suppl 40 (2015), s24–s30.
-
(2015)
Pediatric Pulmonology
, vol.50
, pp. s24-s30
-
-
Borowitz, D.1
-
26
-
-
34047166052
-
Airway surface dehydration in cystic fibrosis: Pathogenesis and therapy
-
Boucher, R.C., Airway surface dehydration in cystic fibrosis: Pathogenesis and therapy. Annual Review of Medicine 58 (2007), 157–170.
-
(2007)
Annual Review of Medicine
, vol.58
, pp. 157-170
-
-
Boucher, R.C.1
-
27
-
-
33845992179
-
Evidence for airway surface dehydration as the initiating event in CF airway disease
-
Boucher, R.C., Evidence for airway surface dehydration as the initiating event in CF airway disease. Journal of Internal Medicine 261:1 (2007), 5–16.
-
(2007)
Journal of Internal Medicine
, vol.261
, Issue.1
, pp. 5-16
-
-
Boucher, R.C.1
-
28
-
-
0022973473
-
Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation
-
Boucher, R.C., Stutts, M.J., Knowles, M.R., Cantley, L., Gatzy, J.T., Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation. Journal of Clinical Investigation 78:5 (1986), 1245–1252.
-
(1986)
Journal of Clinical Investigation
, vol.78
, Issue.5
, pp. 1245-1252
-
-
Boucher, R.C.1
Stutts, M.J.2
Knowles, M.R.3
Cantley, L.4
Gatzy, J.T.5
-
29
-
-
84927740385
-
Pulmonary epithelial barrier function: Some new players and mechanisms
-
Brune, K., Frank, J., Schwingshackl, A., Finigan, J., Sidhaye, V.K., Pulmonary epithelial barrier function: Some new players and mechanisms. American Journal of physiology. Lung Cellular and Molecular Physiology 308:8 (2015), L731–L745.
-
(2015)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.308
, Issue.8
, pp. L731-L745
-
-
Brune, K.1
Frank, J.2
Schwingshackl, A.3
Finigan, J.4
Sidhaye, V.K.5
-
30
-
-
34250207969
-
Epithelial Na+ channels are fully activated by furin- and prostasin-dependent release of an inhibitory peptide from the gamma-subunit
-
Bruns, J.B., Carattino, M.D., Sheng, S., Maarouf, A.B., Weisz, O.A., Pilewski, J.M., et al. Epithelial Na+ channels are fully activated by furin- and prostasin-dependent release of an inhibitory peptide from the gamma-subunit. Journal of Biological Chemistry 282:9 (2007), 6153–6160.
-
(2007)
Journal of Biological Chemistry
, vol.282
, Issue.9
, pp. 6153-6160
-
-
Bruns, J.B.1
Carattino, M.D.2
Sheng, S.3
Maarouf, A.B.4
Weisz, O.A.5
Pilewski, J.M.6
-
31
-
-
84989261241
-
Mucus hyperconcentration as a unifying aspect of the chronic bronchitic phenotype
-
Button, B., Anderson, W.H., Boucher, R.C., Mucus hyperconcentration as a unifying aspect of the chronic bronchitic phenotype. Ann Am Thorac Soc 13:Suppl 2 (2016), S156–S162.
-
(2016)
Ann Am Thorac Soc
, vol.13
, pp. S156-S162
-
-
Button, B.1
Anderson, W.H.2
Boucher, R.C.3
-
32
-
-
84865305392
-
A periciliary brush promotes the lung health by separating the mucus layer from airway epithelia
-
Button, B., Cai, L.H., Ehre, C., Kesimer, M., Hill, D.B., Sheehan, J.K., et al. A periciliary brush promotes the lung health by separating the mucus layer from airway epithelia. Science 337:6097 (2012), 937–941.
-
(2012)
Science
, vol.337
, Issue.6097
, pp. 937-941
-
-
Button, B.1
Cai, L.H.2
Ehre, C.3
Kesimer, M.4
Hill, D.B.5
Sheehan, J.K.6
-
33
-
-
0347988218
-
Serine protease activation of near-silent epithelial Na+ channels
-
Caldwell, R.A., Boucher, R.C., Stutts, M.J., Serine protease activation of near-silent epithelial Na+ channels. American Journal of Physiology. Cell Physiology 286:1 (2004), C190–C194.
-
(2004)
American Journal of Physiology. Cell Physiology
, vol.286
, Issue.1
, pp. C190-C194
-
-
Caldwell, R.A.1
Boucher, R.C.2
Stutts, M.J.3
-
34
-
-
17444418987
-
Neutrophil elastase activates near-silent epithelial Na+ channels and increases airway epithelial Na+ transport
-
Caldwell, R.A., Boucher, R.C., Stutts, M.J., Neutrophil elastase activates near-silent epithelial Na+ channels and increases airway epithelial Na+ transport. American Journal of Physiology - Lung Cellular and Molecular Physiology 288:5 (2005), L813–L819.
-
(2005)
American Journal of Physiology - Lung Cellular and Molecular Physiology
, vol.288
, Issue.5
, pp. L813-L819
-
-
Caldwell, R.A.1
Boucher, R.C.2
Stutts, M.J.3
-
35
-
-
0027483065
-
Epithelial sodium channel related to proteins involved in neurodegeneration
-
Canessa, C.M., Horisberger, J.D., Rossier, B.C., Epithelial sodium channel related to proteins involved in neurodegeneration. Nature 361:6411 (1993), 467–470.
-
(1993)
Nature
, vol.361
, Issue.6411
, pp. 467-470
-
-
Canessa, C.M.1
Horisberger, J.D.2
Rossier, B.C.3
-
36
-
-
54949112835
-
TMEM16A, a membrane protein associated with calcium-dependent chloride channel activity
-
Caputo, A., Caci, E., Ferrera, L., Pedemonte, N., Barsanti, C., Sondo, E., et al. TMEM16A, a membrane protein associated with calcium-dependent chloride channel activity. Science 322:5901 (2008), 590–594.
-
(2008)
Science
, vol.322
, Issue.5901
, pp. 590-594
-
-
Caputo, A.1
Caci, E.2
Ferrera, L.3
Pedemonte, N.4
Barsanti, C.5
Sondo, E.6
-
37
-
-
57749120649
-
Interleukin-1, neutrophil elastase, and lipopolysaccharide: Key proinflammatory stimuli regulating inflammation in cystic fibrosis
-
Carroll, T.P., Greene, C.M., Taggart, C.C., McElvaney, N.G., O'Neill, S.J., Interleukin-1, neutrophil elastase, and lipopolysaccharide: Key proinflammatory stimuli regulating inflammation in cystic fibrosis. Current Respiratory Medicine Review, 1, 2005.
-
(2005)
Current Respiratory Medicine Review
, vol.1
-
-
Carroll, T.P.1
Greene, C.M.2
Taggart, C.C.3
McElvaney, N.G.4
O'Neill, S.J.5
-
38
-
-
70350516261
-
Slc26a9 is inhibited by the R-region of the cystic fibrosis transmembrane conductance regulator via the STAS domain
-
Chang, M.H., Plata, C., Sindic, A., Ranatunga, W.K., Chen, A.P., Zandi-Nejad, K., et al. Slc26a9 is inhibited by the R-region of the cystic fibrosis transmembrane conductance regulator via the STAS domain. Journal of Biological Chemistry 284:41 (2009), 28306–28318.
-
(2009)
Journal of Biological Chemistry
, vol.284
, Issue.41
, pp. 28306-28318
-
-
Chang, M.H.1
Plata, C.2
Sindic, A.3
Ranatunga, W.K.4
Chen, A.P.5
Zandi-Nejad, K.6
-
39
-
-
0025987020
-
Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel
-
Cheng, S.H., Rich, D.P., Marshall, J., Gregory, R.J., Welsh, M.J., Smith, A.E., Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel. Cell 66:5 (1991), 1027–1036.
-
(1991)
Cell
, vol.66
, Issue.5
, pp. 1027-1036
-
-
Cheng, S.H.1
Rich, D.P.2
Marshall, J.3
Gregory, R.J.4
Welsh, M.J.5
Smith, A.E.6
-
40
-
-
0035282581
-
Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis
-
Choi, J.Y., Muallem, D., Kiselyov, K., Lee, M.G., Thomas, P.J., Muallem, S., Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis. Nature 410:6824 (2001), 94–97.
-
(2001)
Nature
, vol.410
, Issue.6824
, pp. 94-97
-
-
Choi, J.Y.1
Muallem, D.2
Kiselyov, K.3
Lee, M.G.4
Thomas, P.J.5
Muallem, S.6
-
41
-
-
0036023395
-
Na self inhibition of human epithelial Na channel: Temperature dependence and effect of extracellular proteases
-
Chraibi, A., Horisberger, J.D., Na self inhibition of human epithelial Na channel: Temperature dependence and effect of extracellular proteases. The Journal of General Physiology 120:2 (2002), 133–145.
-
(2002)
The Journal of General Physiology
, vol.120
, Issue.2
, pp. 133-145
-
-
Chraibi, A.1
Horisberger, J.D.2
-
42
-
-
0030741092
-
Extracellular ATP stimulates K+ secretion across cultured human airway epithelium
-
Clarke, L.L., Chinet, T., Boucher, R.C., Extracellular ATP stimulates K+ secretion across cultured human airway epithelium. American Journal of Physiology 272:6 Pt 1 (1997), L1084–L1091.
-
(1997)
American Journal of Physiology
, vol.272
, Issue.6
, pp. L1084-L1091
-
-
Clarke, L.L.1
Chinet, T.2
Boucher, R.C.3
-
43
-
-
0027052928
-
Histamine-induced Cl- secretion in human nasal epithelium: Responses of apical and basolateral membranes
-
Clarke, L.L., Paradiso, A.M., Boucher, R.C., Histamine-induced Cl- secretion in human nasal epithelium: Responses of apical and basolateral membranes. American Journal of Physiology - cell Physiology 263:6 (1992), C1190–C1199.
-
(1992)
American Journal of Physiology - cell Physiology
, vol.263
, Issue.6
, pp. C1190-C1199
-
-
Clarke, L.L.1
Paradiso, A.M.2
Boucher, R.C.3
-
44
-
-
0346103648
-
Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium
-
Coakley, R.D., Grubb, B.R., Paradiso, A.M., Gatzy, J.T., Johnson, L.G., Kreda, S.M., et al. Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium. Proc Natl Acad Sci U S A 100:26 (2003), 16083–16088.
-
(2003)
Proc Natl Acad Sci U S A
, vol.100
, Issue.26
, pp. 16083-16088
-
-
Coakley, R.D.1
Grubb, B.R.2
Paradiso, A.M.3
Gatzy, J.T.4
Johnson, L.G.5
Kreda, S.M.6
-
45
-
-
59449106459
-
Extracellular protons regulate human ENaC by modulating Na+ self-inhibition
-
Collier, D.M., Snyder, P.M., Extracellular protons regulate human ENaC by modulating Na+ self-inhibition. Journal of Biological Chemistry 284:2 (2009), 792–798.
-
(2009)
Journal of Biological Chemistry
, vol.284
, Issue.2
, pp. 792-798
-
-
Collier, D.M.1
Snyder, P.M.2
-
46
-
-
79953169501
-
Identification of epithelial Na(+) channel (ENaC) intersubunit Cl(−) inhibitory residues suggests a trimeric αγβ channel architecture
-
Collier, D.M., Snyder, P.M., Identification of epithelial Na(+) channel (ENaC) intersubunit Cl(−) inhibitory residues suggests a trimeric αγβ channel architecture. The Journal of Biological Chemistry 286:8 (2011), 6027–6032.
-
(2011)
The Journal of Biological Chemistry
, vol.286
, Issue.8
, pp. 6027-6032
-
-
Collier, D.M.1
Snyder, P.M.2
-
47
-
-
65649148597
-
Camostat attenuates airway epithelial sodium channel function in vivo through the inhibition of a channel-activating protease
-
Coote, K., Atherton-Watson, H.C., Sugar, R., Young, A., MacKenzie-Beevor, A., Gosling, M., et al. Camostat attenuates airway epithelial sodium channel function in vivo through the inhibition of a channel-activating protease. The Journal of Pharmacology and Experimental Therapeutics 329:2 (2009), 764–774.
-
(2009)
The Journal of Pharmacology and Experimental Therapeutics
, vol.329
, Issue.2
, pp. 764-774
-
-
Coote, K.1
Atherton-Watson, H.C.2
Sugar, R.3
Young, A.4
MacKenzie-Beevor, A.5
Gosling, M.6
-
49
-
-
0025887254
-
Immunocytochemical investigation of the tissue of origin of two lung cancer cell lines
-
Daniel, M.R., Burnett, H.E., Immunocytochemical investigation of the tissue of origin of two lung cancer cell lines. International Journal of Experimental Pathology 72:4 (1991), 397–405.
-
(1991)
International Journal of Experimental Pathology
, vol.72
, Issue.4
, pp. 397-405
-
-
Daniel, M.R.1
Burnett, H.E.2
-
50
-
-
43549083496
-
Regulated airway goblet cell mucin secretion
-
Davis, C.W., Dickey, B.F., Regulated airway goblet cell mucin secretion. Annual Review of Physiology 70 (2008), 487–512.
-
(2008)
Annual Review of Physiology
, vol.70
, pp. 487-512
-
-
Davis, C.W.1
Dickey, B.F.2
-
51
-
-
54049094727
-
Coupling of airway ciliary activity and mucin secretion to mechanical stresses by purinergic signaling
-
Davis, C.W., Lazarowski, E., Coupling of airway ciliary activity and mucin secretion to mechanical stresses by purinergic signaling. Respiratory Physiology & Neurobiology 163:1–3 (2008), 208–213.
-
(2008)
Respiratory Physiology & Neurobiology
, vol.163
, Issue.1-3
, pp. 208-213
-
-
Davis, C.W.1
Lazarowski, E.2
-
52
-
-
85053185850
-
Airway epithelium dysfunction in cystic fibrosis and COPD
-
De Rose, V., Molloy, K., Gohy, S., Pilette, C., Greene, C.M., Airway epithelium dysfunction in cystic fibrosis and COPD. Mediators of Inflammation, 2018, 2018, 1309746.
-
(2018)
Mediators of Inflammation
, vol.2018
, pp. 1309746
-
-
De Rose, V.1
Molloy, K.2
Gohy, S.3
Pilette, C.4
Greene, C.M.5
-
53
-
-
0032899770
-
UTP inhibits Na+ absorption in wild-type and DeltaF508 CFTR-expressing human bronchial epithelia
-
Devor, D.C., Pilewski, J.M., UTP inhibits Na+ absorption in wild-type and DeltaF508 CFTR-expressing human bronchial epithelia. American Journal of Physiology 276:4 Pt 1 (1999), C827–C837.
-
(1999)
American Journal of Physiology
, vol.276
, Issue.4
, pp. C827-C837
-
-
Devor, D.C.1
Pilewski, J.M.2
-
54
-
-
84932181891
-
A millennial view of cystic fibrosis
-
Dodge, J.A., A millennial view of cystic fibrosis. Dev Period Med 19:1 (2015), 9–13.
-
(2015)
Dev Period Med
, vol.19
, Issue.1
, pp. 9-13
-
-
Dodge, J.A.1
-
55
-
-
0037040995
-
Regulation of the epithelial sodium channel by serine proteases in human airways
-
Donaldson, S.H., Hirsh, A., Li, D.C., Holloway, G., Chao, J., Boucher, R.C., et al. Regulation of the epithelial sodium channel by serine proteases in human airways. Journal of Biological Chemistry 277:10 (2002), 8338–8345.
-
(2002)
Journal of Biological Chemistry
, vol.277
, Issue.10
, pp. 8338-8345
-
-
Donaldson, S.H.1
Hirsh, A.2
Li, D.C.3
Holloway, G.4
Chao, J.5
Boucher, R.C.6
-
56
-
-
30744475282
-
The mammalian ionic environment dictates microbial susceptibility to antimicrobial defense peptides
-
Dorschner, R.A., Lopez-Garcia, B., Peschel, A., Kraus, D., Morikawa, K., Nizet, V., et al. The mammalian ionic environment dictates microbial susceptibility to antimicrobial defense peptides. FASEB Journal: Official Publication of the Federation of American Societies for Experimental Biology 20:1 (2006), 35–42.
-
(2006)
FASEB Journal: Official Publication of the Federation of American Societies for Experimental Biology
, vol.20
, Issue.1
, pp. 35-42
-
-
Dorschner, R.A.1
Lopez-Garcia, B.2
Peschel, A.3
Kraus, D.4
Morikawa, K.5
Nizet, V.6
-
57
-
-
34848832938
-
SLC26A9 is a Cl(-) channel regulated by the WNK kinases
-
Dorwart, M.R., Shcheynikov, N., Wang, Y., Stippec, S., Muallem, S., SLC26A9 is a Cl(-) channel regulated by the WNK kinases. J Physiol 584:Pt 1 (2007), 333–345.
-
(2007)
J Physiol
, vol.584
, pp. 333-345
-
-
Dorwart, M.R.1
Shcheynikov, N.2
Wang, Y.3
Stippec, S.4
Muallem, S.5
-
58
-
-
0024824522
-
The pathophysiology of the pancreatic defect in cystic fibrosis
-
Durie, P.R., The pathophysiology of the pancreatic defect in cystic fibrosis. Acta Psychiatrica Scandinavica Supplementum 363 (1989), 41–44.
-
(1989)
Acta Psychiatrica Scandinavica Supplementum
, vol.363
, pp. 41-44
-
-
Durie, P.R.1
-
59
-
-
85037631931
-
Versatility of NaCl transport mechanisms in the cortical collecting duct
-
Edwards, A., Crambert, G., Versatility of NaCl transport mechanisms in the cortical collecting duct. American Journal of Physiology - Renal Physiology 313:6 (2017), F1254–F1263.
-
(2017)
American Journal of Physiology - Renal Physiology
, vol.313
, Issue.6
, pp. F1254-F1263
-
-
Edwards, A.1
Crambert, G.2
-
60
-
-
84975744535
-
Cystic fibrosis
-
Elborn, J.S., Cystic fibrosis. The Lancet 388:10059 (2016), 2519–2531.
-
(2016)
The Lancet
, vol.388
, Issue.10059
, pp. 2519-2531
-
-
Elborn, J.S.1
-
61
-
-
0026951303
-
Submucosal glands are the predominant site of CFTR expression in the human bronchus
-
Engelhardt, J.F., Yankaskas, J.R., Ernst, S.A., Yang, Y., Marino, C.R., Boucher, R.C., et al. Submucosal glands are the predominant site of CFTR expression in the human bronchus. Nature Genetics 2:3 (1992), 240–248.
-
(1992)
Nature Genetics
, vol.2
, Issue.3
, pp. 240-248
-
-
Engelhardt, J.F.1
Yankaskas, J.R.2
Ernst, S.A.3
Yang, Y.4
Marino, C.R.5
Boucher, R.C.6
-
62
-
-
0030754623
-
Geographic distribution and regional origin of 272 cystic fibrosis mutations in European populations. The Biomed CF Mutation Analysis Consortium
-
Estivill, X., Bancells, C., Ramos, C., Geographic distribution and regional origin of 272 cystic fibrosis mutations in European populations. The Biomed CF Mutation Analysis Consortium. Human Mutation 10:2 (1997), 135–154.
-
(1997)
Human Mutation
, vol.10
, Issue.2
, pp. 135-154
-
-
Estivill, X.1
Bancells, C.2
Ramos, C.3
-
63
-
-
51349100398
-
The prevalence of cystic fibrosis in the European Union
-
Farrell, P.M., The prevalence of cystic fibrosis in the European Union. Journal of Cystic Fibrosis 7:5 (2008), 450–453.
-
(2008)
Journal of Cystic Fibrosis
, vol.7
, Issue.5
, pp. 450-453
-
-
Farrell, P.M.1
-
64
-
-
84862211880
-
Ca2+-activated Cl- channels
-
Ferrera, L., Zegarra-Moran, O., Galietta, L.J., Ca2+-activated Cl- channels. Comparative Physiology 1:4 (2011), 2155–2174.
-
(2011)
Comparative Physiology
, vol.1
, Issue.4
, pp. 2155-2174
-
-
Ferrera, L.1
Zegarra-Moran, O.2
Galietta, L.J.3
-
65
-
-
85050583048
-
Mucosal acidification drives early progressive lung disease in cystic fibrosis
-
Figuiera, M.F., Webster, M.J., Tarran, R., Mucosal acidification drives early progressive lung disease in cystic fibrosis. Journal of Physiology, Paris 596:16 (2018), 3433–3437.
-
(2018)
Journal of Physiology, Paris
, vol.596
, Issue.16
, pp. 3433-3437
-
-
Figuiera, M.F.1
Webster, M.J.2
Tarran, R.3
-
66
-
-
70349354334
-
Mechanisms and function of DUOX in epithelia of the lung
-
Fischer, H., Mechanisms and function of DUOX in epithelia of the lung. Antioxidants and Redox Signaling 11:10 (2009), 2453–2465.
-
(2009)
Antioxidants and Redox Signaling
, vol.11
, Issue.10
, pp. 2453-2465
-
-
Fischer, H.1
-
67
-
-
84963811907
-
Site of fluid secretion in small airways
-
Flores-Delgado, G., Lytle, C., Quinton, P.M., Site of fluid secretion in small airways. American Journal of Respiratory Cell and Molecular Biology 54:3 (2016), 312–318.
-
(2016)
American Journal of Respiratory Cell and Molecular Biology
, vol.54
, Issue.3
, pp. 312-318
-
-
Flores-Delgado, G.1
Lytle, C.2
Quinton, P.M.3
-
68
-
-
0029009408
-
Immunolocalization of the mercurial-insensitive water channel and glycerol intrinsic protein in epithelial cell plasma membranes
-
Frigeri, A., Gropper, M.A., Turck, C.W., Verkman, A.S., Immunolocalization of the mercurial-insensitive water channel and glycerol intrinsic protein in epithelial cell plasma membranes. Proc Natl Acad Sci U S A 92:10 (1995), 4328–4331.
-
(1995)
Proc Natl Acad Sci U S A
, vol.92
, Issue.10
, pp. 4328-4331
-
-
Frigeri, A.1
Gropper, M.A.2
Turck, C.W.3
Verkman, A.S.4
-
69
-
-
0033951227
-
Early expression of beta- and gamma-subunits of epithelial sodium channel during human airway development
-
Gaillard, D., Hinnrasky, J., Coscoy, S., Hofman, P., Matthay, M.A., Puchelle, E., et al. Early expression of beta- and gamma-subunits of epithelial sodium channel during human airway development. American Journal of physiology. Lung Cellular and Molecular Physiology 278:1 (2000), L177–L184.
-
(2000)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.278
, Issue.1
, pp. L177-L184
-
-
Gaillard, D.1
Hinnrasky, J.2
Coscoy, S.3
Hofman, P.4
Matthay, M.A.5
Puchelle, E.6
-
70
-
-
67650488822
-
SPLUNC1 regulates airway surface liquid volume by protecting ENaC from proteolytic cleavage
-
Garcia-Caballero, A., Rasmussen, J.E., Gaillard, E., Watson, M.J., Olsen, J.C., Donaldson, S.H., et al. SPLUNC1 regulates airway surface liquid volume by protecting ENaC from proteolytic cleavage. Proceedings of the National Academy of Sciences 106:27 (2009), 11412–11417.
-
(2009)
Proceedings of the National Academy of Sciences
, vol.106
, Issue.27
, pp. 11412-11417
-
-
Garcia-Caballero, A.1
Rasmussen, J.E.2
Gaillard, E.3
Watson, M.J.4
Olsen, J.C.5
Donaldson, S.H.6
-
71
-
-
84885084821
-
Molecular basis for pH-dependent mucosal dehydration in cystic fibrosis airways
-
Garland, A.L., Walton, W.G., Coakley, R.D., Tan, C.D., Gilmore, R.C., Hobbs, C.A., et al. Molecular basis for pH-dependent mucosal dehydration in cystic fibrosis airways. Proceedings of the National Academy of Sciences 110:40 (2013), 15973–15978.
-
(2013)
Proceedings of the National Academy of Sciences
, vol.110
, Issue.40
, pp. 15973-15978
-
-
Garland, A.L.1
Walton, W.G.2
Coakley, R.D.3
Tan, C.D.4
Gilmore, R.C.5
Hobbs, C.A.6
-
72
-
-
84868513768
-
Sweet talk: Insights into the nature and importance of glucose transport in lung epithelium
-
Garnett, J.P., Baker, E.H., Baines, D.L., Sweet talk: Insights into the nature and importance of glucose transport in lung epithelium. The European Respiratory Journal 40:5 (2012), 1269–1276.
-
(2012)
The European Respiratory Journal
, vol.40
, Issue.5
, pp. 1269-1276
-
-
Garnett, J.P.1
Baker, E.H.2
Baines, D.L.3
-
73
-
-
81755189072
-
Novel role for pendrin in orchestrating bicarbonate secretion in cystic fibrosis transmembrane conductance regulator (CFTR)-expressing airway serous cells
-
Garnett, J.P., Hickman, E., Burrows, R., Hegyi, P., Tiszlavicz, L., Cuthbert, A.W., et al. Novel role for pendrin in orchestrating bicarbonate secretion in cystic fibrosis transmembrane conductance regulator (CFTR)-expressing airway serous cells. Journal of Biological Chemistry 286:47 (2011), 41069–41082.
-
(2011)
Journal of Biological Chemistry
, vol.286
, Issue.47
, pp. 41069-41082
-
-
Garnett, J.P.1
Hickman, E.2
Burrows, R.3
Hegyi, P.4
Tiszlavicz, L.5
Cuthbert, A.W.6
-
74
-
-
84941423127
-
Airway hydration and COPD
-
Ghosh, A., Boucher, R.C., Tarran, R., Airway hydration and COPD. Cellular and Molecular Life Sciences: CMLS 72:19 (2015), 3637–3652.
-
(2015)
Cellular and Molecular Life Sciences: CMLS
, vol.72
, Issue.19
, pp. 3637-3652
-
-
Ghosh, A.1
Boucher, R.C.2
Tarran, R.3
-
75
-
-
0142043977
-
Pathophysiology and management of pulmonary infections in cystic fibrosis
-
Gibson, R.L., Burns, J.L., Ramsey, B.W., Pathophysiology and management of pulmonary infections in cystic fibrosis. American Journal of Respiratory and Critical Care Medicine 168:8 (2003), 918–951.
-
(2003)
American Journal of Respiratory and Critical Care Medicine
, vol.168
, Issue.8
, pp. 918-951
-
-
Gibson, R.L.1
Burns, J.L.2
Ramsey, B.W.3
-
76
-
-
2342656361
-
Bicarbonate secretion: It takes two to tango
-
Gray, M.A., Bicarbonate secretion: It takes two to tango. Nature Cell Biology 6:4 (2004), 292–294.
-
(2004)
Nature Cell Biology
, vol.6
, Issue.4
, pp. 292-294
-
-
Gray, M.A.1
-
77
-
-
1642581818
-
Regulation of MUC5AC mucin secretion and airway surface liquid metabolism by IL-1beta in human bronchial epithelia
-
Gray, T., Coakley, R., Hirsh, A., Thornton, D., Kirkham, S., Koo, J.S., et al. Regulation of MUC5AC mucin secretion and airway surface liquid metabolism by IL-1beta in human bronchial epithelia. American Journal of physiology. Lung Cellular and Molecular Physiology 286:2 (2004), L320–L330.
-
(2004)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.286
, Issue.2
, pp. L320-L330
-
-
Gray, T.1
Coakley, R.2
Hirsh, A.3
Thornton, D.4
Kirkham, S.5
Koo, J.S.6
-
78
-
-
0023782863
-
Secretin-regulated chloride channel on the apical plasma membrane of pancreatic duct cells
-
Gray, M.A., Greenwell, J.R., Argent, B.E., Secretin-regulated chloride channel on the apical plasma membrane of pancreatic duct cells. The Journal of Membrane Biology 105:2 (1988), 131–142.
-
(1988)
The Journal of Membrane Biology
, vol.105
, Issue.2
, pp. 131-142
-
-
Gray, M.A.1
Greenwell, J.R.2
Argent, B.E.3
-
79
-
-
0025092468
-
Anion selectivity and block of the small-conductance chloride channel on pancreatic duct cells
-
Gray, M.A., Pollard, C.E., Harris, A., Coleman, L., Greenwell, J.R., Argent, B.E., Anion selectivity and block of the small-conductance chloride channel on pancreatic duct cells. American Journal of Physiology 259:5 Pt 1 (1990), C752–C761.
-
(1990)
American Journal of Physiology
, vol.259
, Issue.5
, pp. C752-C761
-
-
Gray, M.A.1
Pollard, C.E.2
Harris, A.3
Coleman, L.4
Greenwell, J.R.5
Argent, B.E.6
-
80
-
-
0028333866
-
Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice
-
Grubb, B.R., Vick, R.N., Boucher, R.C., Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice. American Journal of Physiology 266:5 Pt 1 (1994), C1478–C1483.
-
(1994)
American Journal of Physiology
, vol.266
, Issue.5
, pp. C1478-C1483
-
-
Grubb, B.R.1
Vick, R.N.2
Boucher, R.C.3
-
81
-
-
84878506887
-
Claudins and the modulation of tight junction permeability
-
Gunzel, D., Yu, A.S., Claudins and the modulation of tight junction permeability. Physiological Reviews 93:2 (2013), 525–569.
-
(2013)
Physiological Reviews
, vol.93
, Issue.2
, pp. 525-569
-
-
Gunzel, D.1
Yu, A.S.2
-
82
-
-
84973137939
-
Inhibitors of pendrin anion exchange identified in a small molecule screen increase airway surface liquid volume in cystic fibrosis
-
Haggie, P.M., Phuan, P.W., Tan, J.A., Zlock, L., Finkbeiner, W.E., Verkman, A.S., Inhibitors of pendrin anion exchange identified in a small molecule screen increase airway surface liquid volume in cystic fibrosis. FASEB Journal: Official Publication of the Federation of American Societies for Experimental Biology 30:6 (2016), 2187–2197.
-
(2016)
FASEB Journal: Official Publication of the Federation of American Societies for Experimental Biology
, vol.30
, Issue.6
, pp. 2187-2197
-
-
Haggie, P.M.1
Phuan, P.W.2
Tan, J.A.3
Zlock, L.4
Finkbeiner, W.E.5
Verkman, A.S.6
-
83
-
-
84954285138
-
Airway surface liquid homeostasis in cystic fibrosis: Pathophysiology and therapeutic targets
-
Haq, I.J., Gray, M.A., Garnett, J.P., Ward, C., Brodlie, M., Airway surface liquid homeostasis in cystic fibrosis: Pathophysiology and therapeutic targets. Thorax 71:3 (2016), 284–287.
-
(2016)
Thorax
, vol.71
, Issue.3
, pp. 284-287
-
-
Haq, I.J.1
Gray, M.A.2
Garnett, J.P.3
Ward, C.4
Brodlie, M.5
-
84
-
-
85013815260
-
Haschek and Rousseaux's handbook of toxicologic pathology
-
3rd ed. Academic Press Boston
-
Harkema, J.R., Nikula, K.J., Haschek, W.M., Haschek and Rousseaux's handbook of toxicologic pathology. 3rd ed., 2013, Academic Press, Boston.
-
(2013)
-
-
Harkema, J.R.1
Nikula, K.J.2
Haschek, W.M.3
-
85
-
-
85053213456
-
What's new in cystic fibrosis, bpd and other congenital pediatric lung diseases?
-
American Thoracic Society San Diego, USA
-
Hill, D.B., Long, M.R., Markovetz, M.R., Kissner, W.J., Garabine, I.C., Button, B., What's new in cystic fibrosis, bpd and other congenital pediatric lung diseases?. 2018, American Thoracic Society, San Diego, USA, A2316.
-
(2018)
, pp. A2316
-
-
Hill, D.B.1
Long, M.R.2
Markovetz, M.R.3
Kissner, W.J.4
Garabine, I.C.5
Button, B.6
-
86
-
-
84890393972
-
Identification of the SPLUNC1 ENaC-inhibitory domain yields novel strategies to treat sodium hyperabsorption in cystic fibrosis airway epithelial cultures
-
Hobbs, C.A., Blanchard, M.G., Alijevic, O., Tan, C.D., Kellenberger, S., Bencharit, S., et al. Identification of the SPLUNC1 ENaC-inhibitory domain yields novel strategies to treat sodium hyperabsorption in cystic fibrosis airway epithelial cultures. American Journal of physiology. Lung Cellular and Molecular Physiology 305:12 (2013), L990–L1001.
-
(2013)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.305
, Issue.12
, pp. L990-L1001
-
-
Hobbs, C.A.1
Blanchard, M.G.2
Alijevic, O.3
Tan, C.D.4
Kellenberger, S.5
Bencharit, S.6
-
87
-
-
84855172432
-
Ion transport by pulmonary epithelia
-
Hollenhorst, M.I., Richter, K., Fronius, M., Ion transport by pulmonary epithelia. Journal of Biomedicine and Biotechnology, 2011, 2011, 174306.
-
(2011)
Journal of Biomedicine and Biotechnology
, vol.2011
, pp. 174306
-
-
Hollenhorst, M.I.1
Richter, K.2
Fronius, M.3
-
88
-
-
2442427527
-
Epithelial sodium channels are activated by furin-dependent proteolysis
-
Hughey, R.P., Bruns, J.B., Kinlough, C.L., Harkleroad, K.L., Tong, Q., Carattino, M.D., et al. Epithelial sodium channels are activated by furin-dependent proteolysis. Journal of Biological Chemistry 279:18 (2004), 18111–18114.
-
(2004)
Journal of Biological Chemistry
, vol.279
, Issue.18
, pp. 18111-18114
-
-
Hughey, R.P.1
Bruns, J.B.2
Kinlough, C.L.3
Harkleroad, K.L.4
Tong, Q.5
Carattino, M.D.6
-
89
-
-
65749102092
-
Gating of the CFTR Cl(−) channel by ATP-driven nucleotide-binding domain dimerisation
-
Hwang, T.-C., Sheppard, D.N., Gating of the CFTR Cl(−) channel by ATP-driven nucleotide-binding domain dimerisation. The Journal of Physiology 587:Pt 10 (2009), 2151–2161.
-
(2009)
The Journal of Physiology
, vol.587
, pp. 2151-2161
-
-
Hwang, T.-C.1
Sheppard, D.N.2
-
90
-
-
75349114365
-
Anatomy, pathology, and physiology of the tracheobronchial tree: Emphasis on the distal airways
-
Hyde, D.M., Hamid, Q., Irvin, C.G., Anatomy, pathology, and physiology of the tracheobronchial tree: Emphasis on the distal airways. The Journal of Allergy and Clinical Immunology 124:6 (2009), S72–S77.
-
(2009)
The Journal of Allergy and Clinical Immunology
, vol.124
, Issue.6
, pp. S72-S77
-
-
Hyde, D.M.1
Hamid, Q.2
Irvin, C.G.3
-
91
-
-
0035132659
-
Noninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH
-
Jayaraman, S., Song, Y., Vetrivel, L., Shankar, L., Verkman, A.S., Noninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH. Journal of Clinical Investigation 107:3 (2001), 317–324.
-
(2001)
Journal of Clinical Investigation
, vol.107
, Issue.3
, pp. 317-324
-
-
Jayaraman, S.1
Song, Y.2
Vetrivel, L.3
Shankar, L.4
Verkman, A.S.5
-
92
-
-
84881451201
-
Cellular pressure and volume regulation and implications for cell mechanics
-
Jiang, H., Sun, S.X., Cellular pressure and volume regulation and implications for cell mechanics. Biophysical Journal 105:3 (2013), 609–619.
-
(2013)
Biophysical Journal
, vol.105
, Issue.3
, pp. 609-619
-
-
Jiang, H.1
Sun, S.X.2
-
93
-
-
84878540443
-
Human neutrophil elastase degrades SPLUNC1 and impairs airway epithelial defense against bacteria
-
Jiang, D., Wenzel, S.E., Wu, Q., Bowler, R.P., Schnell, C., Chu, H.W., Human neutrophil elastase degrades SPLUNC1 and impairs airway epithelial defense against bacteria. PLoS One, 8(5), 2013, e64689.
-
(2013)
PLoS One
, vol.8
, Issue.5
-
-
Jiang, D.1
Wenzel, S.E.2
Wu, Q.3
Bowler, R.P.4
Schnell, C.5
Chu, H.W.6
-
94
-
-
0034623128
-
The cytosolic termini of the beta- and gamma-ENaC subunits are involved in the functional interactions between cystic fibrosis transmembrane conductance regulator and epithelial sodium channel
-
Ji, H.L., Chalfant, M.L., Jovov, B., Lockhart, J.P., Parker, S.B., Fuller, C.M., et al. The cytosolic termini of the beta- and gamma-ENaC subunits are involved in the functional interactions between cystic fibrosis transmembrane conductance regulator and epithelial sodium channel. Journal of Biological Chemistry 275:36 (2000), 27947–27956.
-
(2000)
Journal of Biological Chemistry
, vol.275
, Issue.36
, pp. 27947-27956
-
-
Ji, H.L.1
Chalfant, M.L.2
Jovov, B.3
Lockhart, J.P.4
Parker, S.B.5
Fuller, C.M.6
-
95
-
-
84871959313
-
Dynamic modulation of ANO1/TMEM16A HCO3(-) permeability by Ca2+/calmodulin
-
Jung, J., Nam, J.H., Park, H.W., Oh, U., Yoon, J.H., Lee, M.G., Dynamic modulation of ANO1/TMEM16A HCO3(-) permeability by Ca2+/calmodulin. Proc Natl Acad Sci U S A 110:1 (2013), 360–365.
-
(2013)
Proc Natl Acad Sci U S A
, vol.110
, Issue.1
, pp. 360-365
-
-
Jung, J.1
Nam, J.H.2
Park, H.W.3
Oh, U.4
Yoon, J.H.5
Lee, M.G.6
-
96
-
-
84874102944
-
Molecular organization of the mucins and glycocalyx underlying mucus transport over mucosal surfaces of the airways
-
Kesimer, M., Ehre, C., Burns, K.A., Davis, C.W., Sheehan, J.K., Pickles, R.J., Molecular organization of the mucins and glycocalyx underlying mucus transport over mucosal surfaces of the airways. Mucosal Immunology 6:2 (2013), 379–392.
-
(2013)
Mucosal Immunology
, vol.6
, Issue.2
, pp. 379-392
-
-
Kesimer, M.1
Ehre, C.2
Burns, K.A.3
Davis, C.W.4
Sheehan, J.K.5
Pickles, R.J.6
-
97
-
-
85048472619
-
SPLUNC1 is an allosteric modulator of the epithelial sodium channel
-
Kim, C.S., Ahmad, S., Wu, T., Walton, W.G., Redinbo, M.R., Tarran, R., SPLUNC1 is an allosteric modulator of the epithelial sodium channel. FASEB Journal: Official Publication of the Federation of American Societies for Experimental Biology 32:5 (2018), 2478–2491.
-
(2018)
FASEB Journal: Official Publication of the Federation of American Societies for Experimental Biology
, vol.32
, Issue.5
, pp. 2478-2491
-
-
Kim, C.S.1
Ahmad, S.2
Wu, T.3
Walton, W.G.4
Redinbo, M.R.5
Tarran, R.6
-
98
-
-
84989231095
-
Airway hydration, apical K(+) secretion, and the large-conductance, Ca(2+)-activated and voltage-dependent potassium (BK) channel
-
Kis, A., Krick, S., Baumlin, N., Salathe, M., Airway hydration, apical K(+) secretion, and the large-conductance, Ca(2+)-activated and voltage-dependent potassium (BK) channel. Annals of the American Thoracic Society 13:Suppl 2 (2016), S163–S168.
-
(2016)
Annals of the American Thoracic Society
, vol.13
, pp. S163-S168
-
-
Kis, A.1
Krick, S.2
Baumlin, N.3
Salathe, M.4
-
99
-
-
0019809960
-
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis
-
Knowles, M., Gatzy, J., Boucher, R., Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis. The New England Journal of Medicine 305:25 (1981), 1489–1495.
-
(1981)
The New England Journal of Medicine
, vol.305
, Issue.25
, pp. 1489-1495
-
-
Knowles, M.1
Gatzy, J.2
Boucher, R.3
-
100
-
-
0020596438
-
Relative ion permeability of normal and cystic fibrosis nasal epithelium
-
Knowles, M., Gatzy, J., Boucher, R., Relative ion permeability of normal and cystic fibrosis nasal epithelium. Journal of Clinical Investigation 71:5 (1983), 1410–1417.
-
(1983)
Journal of Clinical Investigation
, vol.71
, Issue.5
, pp. 1410-1417
-
-
Knowles, M.1
Gatzy, J.2
Boucher, R.3
-
101
-
-
0030814886
-
Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects
-
Knowles, M.R., Robinson, J.M., Wood, R.E., Pue, C.A., Mentz, W.M., Wager, G.C., et al. Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects. Journal of Clinical Investigation 100:10 (1997), 2588–2595.
-
(1997)
Journal of Clinical Investigation
, vol.100
, Issue.10
, pp. 2588-2595
-
-
Knowles, M.R.1
Robinson, J.M.2
Wood, R.E.3
Pue, C.A.4
Mentz, W.M.5
Wager, G.C.6
-
102
-
-
0020610435
-
Abnormal ion permeation through cystic fibrosis respiratory epithelium
-
Knowles, M.R., Stutts, M.J., Spock, A., Fischer, N., Gatzy, J.T., Boucher, R.C., Abnormal ion permeation through cystic fibrosis respiratory epithelium. Science 221:4615 (1983), 1067–1070.
-
(1983)
Science
, vol.221
, Issue.4615
, pp. 1067-1070
-
-
Knowles, M.R.1
Stutts, M.J.2
Spock, A.3
Fischer, N.4
Gatzy, J.T.5
Boucher, R.C.6
-
103
-
-
84873697794
-
Claudin heterogeneity and control of lung tight junctions
-
Koval, M., Claudin heterogeneity and control of lung tight junctions. Annual Review of Physiology 75:1 (2013), 551–567.
-
(2013)
Annual Review of Physiology
, vol.75
, Issue.1
, pp. 551-567
-
-
Koval, M.1
-
104
-
-
2342449944
-
Gating of CFTR by the STAS domain of SLC26 transporters
-
Ko, S.B., Zeng, W., Dorwart, M.R., Luo, X., Kim, K.H., Millen, L., et al. Gating of CFTR by the STAS domain of SLC26 transporters. Nature Cell Biology 6:4 (2004), 343–350.
-
(2004)
Nature Cell Biology
, vol.6
, Issue.4
, pp. 343-350
-
-
Ko, S.B.1
Zeng, W.2
Dorwart, M.R.3
Luo, X.4
Kim, K.H.5
Millen, L.6
-
105
-
-
18244377969
-
Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia
-
Kreda, S.M., Mall, M., Mengos, A., Rochelle, L., Yankaskas, J., Riordan, J.R., et al. Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia. Molecular Biology of the Cell 16:5 (2005), 2154–2167.
-
(2005)
Molecular Biology of the Cell
, vol.16
, Issue.5
, pp. 2154-2167
-
-
Kreda, S.M.1
Mall, M.2
Mengos, A.3
Rochelle, L.4
Yankaskas, J.5
Riordan, J.R.6
-
106
-
-
34848851105
-
Coordinated release of nucleotides and mucin from human airway epithelial Calu-3 cells
-
Kreda, S.M., Okada, S.F., van Heusden, C.A., O'Neal, W., Gabriel, S., Abdullah, L., et al. Coordinated release of nucleotides and mucin from human airway epithelial Calu-3 cells. J Physiol 584:Pt 1 (2007), 245–259.
-
(2007)
J Physiol
, vol.584
, pp. 245-259
-
-
Kreda, S.M.1
Okada, S.F.2
van Heusden, C.A.3
O'Neal, W.4
Gabriel, S.5
Abdullah, L.6
-
107
-
-
0035071662
-
The effects of extracellular pH on immune function
-
Lardner, A., The effects of extracellular pH on immune function. Journal of Leukocyte Biology 69:4 (2001), 522–530.
-
(2001)
Journal of Leukocyte Biology
, vol.69
, Issue.4
, pp. 522-530
-
-
Lardner, A.1
-
108
-
-
33751108498
-
Large conductance Ca2+-activated K+ (BK) channel: Activation by Ca2+ and voltage
-
Latorre, R., Brauchi, S., Large conductance Ca2+-activated K+ (BK) channel: Activation by Ca2+ and voltage. Biological Research 39:3 (2006), 385–401.
-
(2006)
Biological Research
, vol.39
, Issue.3
, pp. 385-401
-
-
Latorre, R.1
Brauchi, S.2
-
109
-
-
65749098350
-
Purinergic receptors in airway epithelia
-
Lazarowski, E.R., Boucher, R.C., Purinergic receptors in airway epithelia. Current Opinion in Pharmacology 9:3 (2009), 262–267.
-
(2009)
Current Opinion in Pharmacology
, vol.9
, Issue.3
, pp. 262-267
-
-
Lazarowski, E.R.1
Boucher, R.C.2
-
110
-
-
4344619319
-
Nucleotide release provides a mechanism for airway surface liquid homeostasis
-
Lazarowski, E.R., Tarran, R., Grubb, B.R., van Heusden, C.A., Okada, S., Boucher, R.C., Nucleotide release provides a mechanism for airway surface liquid homeostasis. The Journal of Biological Chemistry 279:35 (2004), 36855–36864.
-
(2004)
The Journal of Biological Chemistry
, vol.279
, Issue.35
, pp. 36855-36864
-
-
Lazarowski, E.R.1
Tarran, R.2
Grubb, B.R.3
van Heusden, C.A.4
Okada, S.5
Boucher, R.C.6
-
111
-
-
84890535104
-
Vasoactive intestinal peptide regulates sinonasal mucociliary clearance and synergizes with histamine in stimulating sinonasal fluid secretion
-
Lee, R.J., Chen, B., Doghramji, L., Adappa, N.D., Palmer, J.N., Kennedy, D.W., et al. Vasoactive intestinal peptide regulates sinonasal mucociliary clearance and synergizes with histamine in stimulating sinonasal fluid secretion. The FASEB Journal 27:12 (2013), 5094–5103.
-
(2013)
The FASEB Journal
, vol.27
, Issue.12
, pp. 5094-5103
-
-
Lee, R.J.1
Chen, B.2
Doghramji, L.3
Adappa, N.D.4
Palmer, J.N.5
Kennedy, D.W.6
-
112
-
-
0029904733
-
ATPase activity of the cystic fibrosis transmembrane conductance regulator
-
Li, C., Ramjeesingh, M., Wang, W., Garami, E., Hewryk, M., Lee, D., et al. ATPase activity of the cystic fibrosis transmembrane conductance regulator. Journal of Biological Chemistry 271:45 (1996), 28463–28468.
-
(1996)
Journal of Biological Chemistry
, vol.271
, Issue.45
, pp. 28463-28468
-
-
Li, C.1
Ramjeesingh, M.2
Wang, W.3
Garami, E.4
Hewryk, M.5
Lee, D.6
-
113
-
-
85030778856
-
Cystic fibrosis swine fail to secrete airway surface liquid in response to inhalation of pathogens
-
Luan, X., Belev, G., Tam, J.S., Jagadeeshan, S., Hassan, N., Gioino, P., et al. Cystic fibrosis swine fail to secrete airway surface liquid in response to inhalation of pathogens. Nature Communications, 8(1), 2017, 786.
-
(2017)
Nature Communications
, vol.8
, Issue.1
, pp. 786
-
-
Luan, X.1
Belev, G.2
Tam, J.S.3
Jagadeeshan, S.4
Hassan, N.5
Gioino, P.6
-
114
-
-
0021200147
-
Goblet and Clara cells of human distal airways: Evidence for smoking induced changes in their numbers
-
Lumsden, A.B., McLean, A., Lamb, D., Goblet and Clara cells of human distal airways: Evidence for smoking induced changes in their numbers. Thorax 39:11 (1984), 844–849.
-
(1984)
Thorax
, vol.39
, Issue.11
, pp. 844-849
-
-
Lumsden, A.B.1
McLean, A.2
Lamb, D.3
-
115
-
-
0037383908
-
Modulation of Ca2+-activated Cl- secretion by basolateral K+ channels in human normal and cystic fibrosis airway epithelia
-
Mall, M., Gonska, T., Thomas, J., Schreiber, R., Seydewitz, H.H., Kuehr, J., et al. Modulation of Ca2+-activated Cl- secretion by basolateral K+ channels in human normal and cystic fibrosis airway epithelia. Pediatric Research 53:4 (2003), 608–618.
-
(2003)
Pediatric Research
, vol.53
, Issue.4
, pp. 608-618
-
-
Mall, M.1
Gonska, T.2
Thomas, J.3
Schreiber, R.4
Seydewitz, H.H.5
Kuehr, J.6
-
116
-
-
79957592464
-
Functional apical large conductance, Ca(2+)-activated, and voltage-dependent K(+) channels are required for maintenance of airway surface liquid volume
-
Manzanares, D., Gonzalez, C., Ivonnet, P., Chen, R.-S., Valencia-Gattas, M., Conner, G.E., et al. Functional apical large conductance, Ca(2+)-activated, and voltage-dependent K(+) channels are required for maintenance of airway surface liquid volume. The Journal of Biological Chemistry 286:22 (2011), 19830–19839.
-
(2011)
The Journal of Biological Chemistry
, vol.286
, Issue.22
, pp. 19830-19839
-
-
Manzanares, D.1
Gonzalez, C.2
Ivonnet, P.3
Chen, R.-S.4
Valencia-Gattas, M.5
Conner, G.E.6
-
117
-
-
84944400951
-
Airway surface dehydration by transforming growth factor beta (TGF-beta) in cystic fibrosis is due to decreased function of a voltage-dependent potassium channel and can Be rescued by the drug pirfenidone
-
Manzanares, D., Krick, S., Baumlin, N., Dennis, J.S., Tyrrell, J., Tarran, R., et al. Airway surface dehydration by transforming growth factor beta (TGF-beta) in cystic fibrosis is due to decreased function of a voltage-dependent potassium channel and can Be rescued by the drug pirfenidone. Journal of Biological Chemistry 290:42 (2015), 25710–25716.
-
(2015)
Journal of Biological Chemistry
, vol.290
, Issue.42
, pp. 25710-25716
-
-
Manzanares, D.1
Krick, S.2
Baumlin, N.3
Dennis, J.S.4
Tyrrell, J.5
Tarran, R.6
-
118
-
-
0034636160
-
Nephrogenic diabetes insipidus in mice lacking aquaporin-3 water channels
-
Ma, T., Song, Y., Yang, B., Gillespie, A., Carlson, E.J., Epstein, C.J., et al. Nephrogenic diabetes insipidus in mice lacking aquaporin-3 water channels. Proc Natl Acad Sci U S A 97:8 (2000), 4386–4391.
-
(2000)
Proc Natl Acad Sci U S A
, vol.97
, Issue.8
, pp. 4386-4391
-
-
Ma, T.1
Song, Y.2
Yang, B.3
Gillespie, A.4
Carlson, E.J.5
Epstein, C.J.6
-
119
-
-
84949524093
-
Role of epithelial sodium channels in the regulation of lung fluid homeostasis
-
Matalon, S., Bartoszewski, R., Collawn, J.F., Role of epithelial sodium channels in the regulation of lung fluid homeostasis. American Journal of physiology. Lung Cellular and Molecular Physiology 309:11 (2015), L1229–L1238.
-
(2015)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.309
, Issue.11
, pp. L1229-L1238
-
-
Matalon, S.1
Bartoszewski, R.2
Collawn, J.F.3
-
120
-
-
0034125685
-
Osmotic water permeabilities of cultured, well-differentiated normal and cystic fibrosis airway epithelia
-
Matsui, H., Davis, C.W., Tarran, R., Boucher, R.C., Osmotic water permeabilities of cultured, well-differentiated normal and cystic fibrosis airway epithelia. Journal of Clinical Investigation 105:10 (2000), 1419–1427.
-
(2000)
Journal of Clinical Investigation
, vol.105
, Issue.10
, pp. 1419-1427
-
-
Matsui, H.1
Davis, C.W.2
Tarran, R.3
Boucher, R.C.4
-
121
-
-
0032433707
-
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
-
Matsui, H., Grubb, B.R., Tarran, R., Randell, S.H., Gatzy, J.T., Davis, C.W., et al. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 95:7 (1998), 1005–1015.
-
(1998)
Cell
, vol.95
, Issue.7
, pp. 1005-1015
-
-
Matsui, H.1
Grubb, B.R.2
Tarran, R.3
Randell, S.H.4
Gatzy, J.T.5
Davis, C.W.6
-
122
-
-
0014599770
-
A reconstruction of the duct system and secretory tubules of the human bronchial submucosal gland
-
Meyrick, B., Sturgess, J.M., Reid, L., A reconstruction of the duct system and secretory tubules of the human bronchial submucosal gland. Thorax 24:6 (1969), 729–736.
-
(1969)
Thorax
, vol.24
, Issue.6
, pp. 729-736
-
-
Meyrick, B.1
Sturgess, J.M.2
Reid, L.3
-
123
-
-
85053199398
-
Cigarette smoke modifies and inactivates SPLUNC1, leading to airway dehydration
-
fj201800345R
-
Moore, P.J., Reidel, B., Ghosh, A., Sesma, J., Kesimer, M., Tarran, R., Cigarette smoke modifies and inactivates SPLUNC1, leading to airway dehydration. The FASEB Journal, 2018 fj201800345R.
-
(2018)
The FASEB Journal
-
-
Moore, P.J.1
Reidel, B.2
Ghosh, A.3
Sesma, J.4
Kesimer, M.5
Tarran, R.6
-
124
-
-
0019163995
-
Parasympathetic and sympathetic regulation of secretion from submucosal glands in airways
-
Nadel, J.A., Davis, B., Parasympathetic and sympathetic regulation of secretion from submucosal glands in airways. Federation Proceedings 39:13 (1980), 3075–3079.
-
(1980)
Federation Proceedings
, vol.39
, Issue.13
, pp. 3075-3079
-
-
Nadel, J.A.1
Davis, B.2
-
125
-
-
44449127236
-
Identification of pendrin as a common mediator for mucus production in bronchial asthma and chronic obstructive pulmonary disease
-
Nakao, I., Kanaji, S., Ohta, S., Matsushita, H., Arima, K., Yuyama, N., et al. Identification of pendrin as a common mediator for mucus production in bronchial asthma and chronic obstructive pulmonary disease. The Journal of Immunology: Official Journal of the American Association of Immunologists 180:9 (2008), 6262–6269.
-
(2008)
The Journal of Immunology: Official Journal of the American Association of Immunologists
, vol.180
, Issue.9
, pp. 6262-6269
-
-
Nakao, I.1
Kanaji, S.2
Ohta, S.3
Matsushita, H.4
Arima, K.5
Yuyama, N.6
-
126
-
-
78751478642
-
TMEM16A inhibitors reveal TMEM16A as a minor component of calcium-activated chloride channel conductance in airway and intestinal epithelial cells
-
Namkung, W., Phuan, P.W., Verkman, A.S., TMEM16A inhibitors reveal TMEM16A as a minor component of calcium-activated chloride channel conductance in airway and intestinal epithelial cells. Journal of Biological Chemistry 286:3 (2011), 2365–2374.
-
(2011)
Journal of Biological Chemistry
, vol.286
, Issue.3
, pp. 2365-2374
-
-
Namkung, W.1
Phuan, P.W.2
Verkman, A.S.3
-
127
-
-
0032578636
-
Role of Ca2+/K+ ion exchange in intracellular storage and release of Ca2+
-
Nguyen, T., Chin, W.C., Verdugo, P., Role of Ca2+/K+ ion exchange in intracellular storage and release of Ca2+. Nature 395:6705 (1998), 908–912.
-
(1998)
Nature
, vol.395
, Issue.6705
, pp. 908-912
-
-
Nguyen, T.1
Chin, W.C.2
Verdugo, P.3
-
128
-
-
84941102510
-
Inflammation and its genesis in cystic fibrosis
-
Nichols, D.P., Chmiel, J.F., Inflammation and its genesis in cystic fibrosis. Pediatric Pulmonology 50:Suppl 40 (2015), S39–S56.
-
(2015)
Pediatric Pulmonology
, vol.50
, pp. S39-S56
-
-
Nichols, D.P.1
Chmiel, J.F.2
-
129
-
-
0030657804
-
Aquaporins in complex tissues. II. Subcellular distribution in respiratory and glandular tissues of rat
-
Nielsen, S., King, L.S., Christensen, B.M., Agre, P., Aquaporins in complex tissues. II. Subcellular distribution in respiratory and glandular tissues of rat. American Journal of Physiology 273:5 Pt 1 (1997), C1549–C1561.
-
(1997)
American Journal of Physiology
, vol.273
, Issue.5
, pp. C1549-C1561
-
-
Nielsen, S.1
King, L.S.2
Christensen, B.M.3
Agre, P.4
-
130
-
-
0027306170
-
Distribution of the aquaporin CHIP in secretory and resorptive epithelia and capillary endothelia
-
Nielsen, S., Smith, B.L., Christensen, E.I., Agre, P., Distribution of the aquaporin CHIP in secretory and resorptive epithelia and capillary endothelia. Proceedings of the National Academy of Sciences of the United States of America 90:15 (1993), 7275–7279.
-
(1993)
Proceedings of the National Academy of Sciences of the United States of America
, vol.90
, Issue.15
, pp. 7275-7279
-
-
Nielsen, S.1
Smith, B.L.2
Christensen, E.I.3
Agre, P.4
-
131
-
-
82255167090
-
Pendrin function in airway epithelia
-
Nofziger, C., Dossena, S., Suzuki, S., Izuhara, K., Paulmichl, M., Pendrin function in airway epithelia. Cellular Physiology and Biochemistry: International Journal of Experimental Cellular Physiology, Biochemistry, and Pharmacology 28:3 (2011), 571–578.
-
(2011)
Cellular Physiology and Biochemistry: International Journal of Experimental Cellular Physiology, Biochemistry, and Pharmacology
, vol.28
, Issue.3
, pp. 571-578
-
-
Nofziger, C.1
Dossena, S.2
Suzuki, S.3
Izuhara, K.4
Paulmichl, M.5
-
132
-
-
83755183440
-
CFTR and TMEM16A are separate but functionally related Cl- channels
-
Ousingsawat, J., Kongsuphol, P., Schreiber, R., Kunzelmann, K., CFTR and TMEM16A are separate but functionally related Cl- channels. Cellular Physiology and Biochemistry 28:4 (2011), 715–724.
-
(2011)
Cellular Physiology and Biochemistry
, vol.28
, Issue.4
, pp. 715-724
-
-
Ousingsawat, J.1
Kongsuphol, P.2
Schreiber, R.3
Kunzelmann, K.4
-
133
-
-
0031182749
-
ATP-activated basolateral Na+/H+ exchange in human normal and cystic fibrosis airway epithelium
-
Paradiso, A.M., ATP-activated basolateral Na+/H+ exchange in human normal and cystic fibrosis airway epithelium. American Journal of Physiology 273:1 Pt 1 (1997), L148–L158.
-
(1997)
American Journal of Physiology
, vol.273
, Issue.1
, pp. L148-L158
-
-
Paradiso, A.M.1
-
134
-
-
80051626877
-
Innate immunity in the respiratory epithelium
-
Parker, D., Prince, A., Innate immunity in the respiratory epithelium. American Journal of Respiratory Cell and Molecular Biology 45:2 (2011), 189–201.
-
(2011)
American Journal of Respiratory Cell and Molecular Biology
, vol.45
, Issue.2
, pp. 189-201
-
-
Parker, D.1
Prince, A.2
-
135
-
-
84942091798
-
Anatomy and physiology of respiratory system relevant to anaesthesia
-
Patwa, A., Shah, A., Anatomy and physiology of respiratory system relevant to anaesthesia. Indian Journal of Anaesthesia 59:9 (2015), 533–541.
-
(2015)
Indian Journal of Anaesthesia
, vol.59
, Issue.9
, pp. 533-541
-
-
Patwa, A.1
Shah, A.2
-
136
-
-
85014016879
-
Localization and pneumococcal alteration of junction proteins in the human alveolar-capillary compartment
-
Peter, A., Fatykhova, D., Kershaw, O., Gruber, A.D., Rueckert, J., Neudecker, J., et al. Localization and pneumococcal alteration of junction proteins in the human alveolar-capillary compartment. Histochemistry and Cell Biology 147:6 (2017), 707–719.
-
(2017)
Histochemistry and Cell Biology
, vol.147
, Issue.6
, pp. 707-719
-
-
Peter, A.1
Fatykhova, D.2
Kershaw, O.3
Gruber, A.D.4
Rueckert, J.5
Neudecker, J.6
-
137
-
-
0036260880
-
Airways inflammation and COPD: Epithelial-neutrophil interactions
-
Pettersen, C.A., Adler, K.B., Airways inflammation and COPD: Epithelial-neutrophil interactions. Chest 121:5 Suppl (2002), 142S–150S.
-
(2002)
Chest
, vol.121
, Issue.5
, pp. 142S-150S
-
-
Pettersen, C.A.1
Adler, K.B.2
-
138
-
-
84863476402
-
Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung
-
Pezzulo, A.A., Tang, X.X., Hoegger, M.J., Abou Alaiwa, M.H., Ramachandran, S., Moninger, T.O., et al. Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung. Nature 487:7405 (2012), 109–113.
-
(2012)
Nature
, vol.487
, Issue.7405
, pp. 109-113
-
-
Pezzulo, A.A.1
Tang, X.X.2
Hoegger, M.J.3
Abou Alaiwa, M.H.4
Ramachandran, S.5
Moninger, T.O.6
-
139
-
-
0026681083
-
Phosphorylation of the cystic fibrosis transmembrane conductance regulator
-
Picciotto, M.R., Cohn, J.A., Bertuzzi, G., Greengard, P., Nairn, A.C., Phosphorylation of the cystic fibrosis transmembrane conductance regulator. Journal of Biological Chemistry 267:18 (1992), 12742–12752.
-
(1992)
Journal of Biological Chemistry
, vol.267
, Issue.18
, pp. 12742-12752
-
-
Picciotto, M.R.1
Cohn, J.A.2
Bertuzzi, G.3
Greengard, P.4
Nairn, A.C.5
-
140
-
-
0028232830
-
Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator
-
Poulsen, J.H., Fischer, H., Illek, B., Machen, T.E., Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator. Proc Natl Acad Sci U S A 91:12 (1994), 5340–5344.
-
(1994)
Proc Natl Acad Sci U S A
, vol.91
, Issue.12
, pp. 5340-5344
-
-
Poulsen, J.H.1
Fischer, H.2
Illek, B.3
Machen, T.E.4
-
141
-
-
0020700816
-
Chloride impermeability in cystic fibrosis
-
Quinton, P.M., Chloride impermeability in cystic fibrosis. Nature 301:5899 (1983), 421–422.
-
(1983)
Nature
, vol.301
, Issue.5899
, pp. 421-422
-
-
Quinton, P.M.1
-
142
-
-
48149090717
-
Cystic fibrosis: Impaired bicarbonate secretion and mucoviscidosis
-
Quinton, P.M., Cystic fibrosis: Impaired bicarbonate secretion and mucoviscidosis. The Lancet 372:9636 (2008), 415–417.
-
(2008)
The Lancet
, vol.372
, Issue.9636
, pp. 415-417
-
-
Quinton, P.M.1
-
143
-
-
85027302463
-
Both ways at once: Keeping small airways clean
-
Quinton, P.M., Both ways at once: Keeping small airways clean. Physiology 32:5 (2017), 380–390.
-
(2017)
Physiology
, vol.32
, Issue.5
, pp. 380-390
-
-
Quinton, P.M.1
-
144
-
-
85021161375
-
Early lung disease in infants and preschool children with cystic fibrosis. What have we learned and what should we do about it?
-
Ranganathan, S.C., Hall, G.L., Sly, P.D., Stick, S.M., Douglas, T.A., Early lung disease in infants and preschool children with cystic fibrosis. What have we learned and what should we do about it?. American Journal of Respiratory and Critical Care Medicine 195:12 (2017), 1567–1575.
-
(2017)
American Journal of Respiratory and Critical Care Medicine
, vol.195
, Issue.12
, pp. 1567-1575
-
-
Ranganathan, S.C.1
Hall, G.L.2
Sly, P.D.3
Stick, S.M.4
Douglas, T.A.5
-
145
-
-
33746413027
-
Epithelial stem cells of the lung: Privileged few or opportunities for many?
-
Rawlins, E.L., Hogan, B.L., Epithelial stem cells of the lung: Privileged few or opportunities for many?. Development 133:13 (2006), 2455–2465.
-
(2006)
Development
, vol.133
, Issue.13
, pp. 2455-2465
-
-
Rawlins, E.L.1
Hogan, B.L.2
-
146
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan, J.R., Rommens, J.M., Kerem, B., Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA. Science, 245(4925), 1989, 1437.
-
(1989)
Science
, vol.245
, Issue.4925
, pp. 1437
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.3
-
147
-
-
64149083549
-
Activation of the epithelial sodium channel (ENaC) by serine proteases
-
Rossier, B.C., Stutts, M.J., Activation of the epithelial sodium channel (ENaC) by serine proteases. Annual Review of Physiology 71:1 (2009), 361–379.
-
(2009)
Annual Review of Physiology
, vol.71
, Issue.1
, pp. 361-379
-
-
Rossier, B.C.1
Stutts, M.J.2
-
148
-
-
52449131279
-
ENaC and its regulatory proteins as drug targets for blood pressure control
-
Rotin, D., Schild, L., ENaC and its regulatory proteins as drug targets for blood pressure control. Current Drug Targets 9:8 (2008), 709–716.
-
(2008)
Current Drug Targets
, vol.9
, Issue.8
, pp. 709-716
-
-
Rotin, D.1
Schild, L.2
-
149
-
-
85047507011
-
Editorial focus: CFTR-dependent bicarbonate secretion by Calu-3 cells
-
Rubenstein, R.C., Editorial focus: CFTR-dependent bicarbonate secretion by Calu-3 cells. Physiol Rep, 6(10), 2018, e13691.
-
(2018)
Physiol Rep
, vol.6
, Issue.10
-
-
Rubenstein, R.C.1
-
150
-
-
78650657069
-
Regulation of endogenous ENaC functional expression by CFTR and DeltaF508-CFTR in airway epithelial cells
-
Rubenstein, R.C., Lockwood, S.R., Lide, E., Bauer, R., Suaud, L., Grumbach, Y., Regulation of endogenous ENaC functional expression by CFTR and DeltaF508-CFTR in airway epithelial cells. American Journal of physiology. Lung Cellular and Molecular Physiology 300:1 (2011), L88–L101.
-
(2011)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.300
, Issue.1
, pp. L88-L101
-
-
Rubenstein, R.C.1
Lockwood, S.R.2
Lide, E.3
Bauer, R.4
Suaud, L.5
Grumbach, Y.6
-
151
-
-
28144447727
-
Comparative effects of salmeterol, albuterol, and ipratropium on normal and impaired mucociliary function in sheep
-
Sabater, J.R., Lee, T.A., Abraham, W.M., Comparative effects of salmeterol, albuterol, and ipratropium on normal and impaired mucociliary function in sheep. Chest 128:5 (2005), 3743–3749.
-
(2005)
Chest
, vol.128
, Issue.5
, pp. 3743-3749
-
-
Sabater, J.R.1
Lee, T.A.2
Abraham, W.M.3
-
152
-
-
84929006176
-
Polymorphisms associated with expression of BPIFA1/BPIFB1 and lung disease severity in cystic fibrosis
-
Saferali, A., Obeidat, M., Berube, J.C., Lamontagne, M., Bosse, Y., Laviolette, M., et al. Polymorphisms associated with expression of BPIFA1/BPIFB1 and lung disease severity in cystic fibrosis. American Journal of Respiratory Cell and Molecular Biology 53:5 (2015), 607–614.
-
(2015)
American Journal of Respiratory Cell and Molecular Biology
, vol.53
, Issue.5
, pp. 607-614
-
-
Saferali, A.1
Obeidat, M.2
Berube, J.C.3
Lamontagne, M.4
Bosse, Y.5
Laviolette, M.6
-
153
-
-
84990988081
-
Role of CFTR in epithelial physiology
-
Saint-Criq, V., Gray, M.A., Role of CFTR in epithelial physiology. Cellular and Molecular Life Sciences: CMLS 74:1 (2017), 93–115.
-
(2017)
Cellular and Molecular Life Sciences: CMLS
, vol.74
, Issue.1
, pp. 93-115
-
-
Saint-Criq, V.1
Gray, M.A.2
-
154
-
-
84907100425
-
Epithelial anion transporter pendrin contributes to inflammatory lung pathology in mouse models of Bordetella pertussis infection
-
Scanlon, K.M., Gau, Y., Zhu, J., Skerry, C., Wall, S.M., Soleimani, M., et al. Epithelial anion transporter pendrin contributes to inflammatory lung pathology in mouse models of Bordetella pertussis infection. Infection and Immunity 82:10 (2014), 4212–4221.
-
(2014)
Infection and Immunity
, vol.82
, Issue.10
, pp. 4212-4221
-
-
Scanlon, K.M.1
Gau, Y.2
Zhu, J.3
Skerry, C.4
Wall, S.M.5
Soleimani, M.6
-
155
-
-
0030063844
-
Aquaporin-1 in plasma membrane and caveolae provides mercury-sensitive water channels across lung endothelium
-
Schnitzer, J.E., Oh, P., Aquaporin-1 in plasma membrane and caveolae provides mercury-sensitive water channels across lung endothelium. American Journal of Physiology - heart and Circulatory Physiology 270:1 (1996), H416–H422.
-
(1996)
American Journal of Physiology - heart and Circulatory Physiology
, vol.270
, Issue.1
, pp. H416-H422
-
-
Schnitzer, J.E.1
Oh, P.2
-
156
-
-
51549120559
-
Expression cloning of TMEM16A as a calcium-activated chloride channel subunit
-
Schroeder, B.C., Cheng, T., Jan, Y.N., Jan, L.Y., Expression cloning of TMEM16A as a calcium-activated chloride channel subunit. Cell 134:6 (2008), 1019–1029.
-
(2008)
Cell
, vol.134
, Issue.6
, pp. 1019-1029
-
-
Schroeder, B.C.1
Cheng, T.2
Jan, Y.N.3
Jan, L.Y.4
-
157
-
-
85033662713
-
Airway surface liquid pH is not acidic in children with cystic fibrosis
-
Schultz, A., Puvvadi, R., Borisov, S.M., Shaw, N.C., Klimant, I., Berry, L.J., et al. Airway surface liquid pH is not acidic in children with cystic fibrosis. Nature Communications, 8(1), 2017, 1409.
-
(2017)
Nature Communications
, vol.8
, Issue.1
, pp. 1409
-
-
Schultz, A.1
Puvvadi, R.2
Borisov, S.M.3
Shaw, N.C.4
Klimant, I.5
Berry, L.J.6
-
158
-
-
85029682826
-
SPX-101 is a novel epithelial sodium channel-targeted therapeutic for cystic fibrosis that restores mucus transport
-
Scott, D.W., Walker, M.P., Sesma, J., Wu, B., Stuhlmiller, T.J., Sabater, J.R., et al. SPX-101 is a novel epithelial sodium channel-targeted therapeutic for cystic fibrosis that restores mucus transport. American Journal of Respiratory and Critical Care Medicine 196:6 (2017), 734–744.
-
(2017)
American Journal of Respiratory and Critical Care Medicine
, vol.196
, Issue.6
, pp. 734-744
-
-
Scott, D.W.1
Walker, M.P.2
Sesma, J.3
Wu, B.4
Stuhlmiller, T.J.5
Sabater, J.R.6
-
159
-
-
84864298301
-
Surface fluid absorption and secretion in small airways
-
Shamsuddin, A.K., Quinton, P.M., Surface fluid absorption and secretion in small airways. J Physiol 590:15 (2012), 3561–3574.
-
(2012)
J Physiol
, vol.590
, Issue.15
, pp. 3561-3574
-
-
Shamsuddin, A.K.1
Quinton, P.M.2
-
160
-
-
0028307695
-
Calu-3: A human airway epithelial cell line that shows cAMP-dependent Cl- secretion
-
Shen, B.Q., Finkbeiner, W.E., Wine, J.J., Mrsny, R.J., Widdicombe, J.H., Calu-3: A human airway epithelial cell line that shows cAMP-dependent Cl- secretion. American Journal of Physiology 266:5 Pt 1 (1994), L493–L501.
-
(1994)
American Journal of Physiology
, vol.266
, Issue.5
, pp. L493-L501
-
-
Shen, B.Q.1
Finkbeiner, W.E.2
Wine, J.J.3
Mrsny, R.J.4
Widdicombe, J.H.5
-
161
-
-
0035941353
-
Second transmembrane domains of ENaC subunits contribute to ion permeation and selectivity
-
Sheng, S., McNulty, K.A., Harvey, J.M., Kleyman, T.R., Second transmembrane domains of ENaC subunits contribute to ion permeation and selectivity. Journal of Biological Chemistry 276:47 (2001), 44091–44098.
-
(2001)
Journal of Biological Chemistry
, vol.276
, Issue.47
, pp. 44091-44098
-
-
Sheng, S.1
McNulty, K.A.2
Harvey, J.M.3
Kleyman, T.R.4
-
162
-
-
0032912589
-
Structure and function of the CFTR chloride channel
-
Sheppard, D.N., Welsh, M.J., Structure and function of the CFTR chloride channel. Physiological Reviews 79:1 (1999), S23–S45.
-
(1999)
Physiological Reviews
, vol.79
, Issue.1
, pp. S23-S45
-
-
Sheppard, D.N.1
Welsh, M.J.2
-
163
-
-
78651384517
-
Characterization of the oligomeric structure of the Ca(2+)-activated Cl- channel Ano1/TMEM16A
-
Sheridan, J.T., Worthington, E.N., Yu, K., Gabriel, S.E., Hartzell, H.C., Tarran, R., Characterization of the oligomeric structure of the Ca(2+)-activated Cl- channel Ano1/TMEM16A. Journal of Biological Chemistry 286:2 (2011), 1381–1388.
-
(2011)
Journal of Biological Chemistry
, vol.286
, Issue.2
, pp. 1381-1388
-
-
Sheridan, J.T.1
Worthington, E.N.2
Yu, K.3
Gabriel, S.E.4
Hartzell, H.C.5
Tarran, R.6
-
164
-
-
0028102539
-
Membrane topology of the amiloride-sensitive epithelial sodium channel
-
Snyder, P.M., McDonald, F.J., Stokes, J.B., Welsh, M.J., Membrane topology of the amiloride-sensitive epithelial sodium channel. Journal of Biological Chemistry 269:39 (1994), 24379–24383.
-
(1994)
Journal of Biological Chemistry
, vol.269
, Issue.39
, pp. 24379-24383
-
-
Snyder, P.M.1
McDonald, F.J.2
Stokes, J.B.3
Welsh, M.J.4
-
165
-
-
0033638126
-
Role of aquaporin water channels in pleural fluid dynamics
-
Song, Y., Yang, B., Matthay, M.A., Ma, T., Verkman, A.S., Role of aquaporin water channels in pleural fluid dynamics. American Journal of Physiology. Cell Physiology 279:6 (2000), C1744–C1750.
-
(2000)
American Journal of Physiology. Cell Physiology
, vol.279
, Issue.6
, pp. C1744-C1750
-
-
Song, Y.1
Yang, B.2
Matthay, M.A.3
Ma, T.4
Verkman, A.S.5
-
166
-
-
85050934776
-
CrossTalk opposing view: mucosal acidification does not drive early progressive lung disease in cystic fibrosis
-
Stick, S.M., Schultz, A., CrossTalk opposing view: mucosal acidification does not drive early progressive lung disease in cystic fibrosis. Journal of Physiology 596:16 (2018), 3439–3441, 10.1113/JP275426.
-
(2018)
Journal of Physiology
, vol.596
, Issue.16
, pp. 3439-3441
-
-
Stick, S.M.1
Schultz, A.2
-
167
-
-
56149115546
-
Insight toward epithelial Na+ channel mechanism revealed by the acid-sensing ion channel 1 structure
-
Stockand, J.D., Staruschenko, A., Pochynyuk, O., Booth, R.E., Silverthorn, D.U., Insight toward epithelial Na+ channel mechanism revealed by the acid-sensing ion channel 1 structure. IUBMB Life 60:9 (2008), 620–628.
-
(2008)
IUBMB Life
, vol.60
, Issue.9
, pp. 620-628
-
-
Stockand, J.D.1
Staruschenko, A.2
Pochynyuk, O.3
Booth, R.E.4
Silverthorn, D.U.5
-
168
-
-
84921455260
-
Origins of cystic fibrosis lung disease
-
Stoltz, D.A., Meyerholz, D.K., Welsh, M.J., Origins of cystic fibrosis lung disease. New England Journal of Medicine 372:4 (2015), 351–362.
-
(2015)
New England Journal of Medicine
, vol.372
, Issue.4
, pp. 351-362
-
-
Stoltz, D.A.1
Meyerholz, D.K.2
Welsh, M.J.3
-
169
-
-
0023039339
-
Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium
-
Stutts, M.J., Knowles, M.R., Gatzy, J.T., Boucher, R.C., Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium. Pediatric Research 20:12 (1986), 1316–1320.
-
(1986)
Pediatric Research
, vol.20
, Issue.12
, pp. 1316-1320
-
-
Stutts, M.J.1
Knowles, M.R.2
Gatzy, J.T.3
Boucher, R.C.4
-
170
-
-
0030970422
-
Cystic fibrosis transmembrane conductance regulator inverts protein kinase a-mediated regulation of epithelial sodium channel single channel kinetics
-
Stutts, M.J., Rossier, B.C., Boucher, R.C., Cystic fibrosis transmembrane conductance regulator inverts protein kinase a-mediated regulation of epithelial sodium channel single channel kinetics. Journal of Biological Chemistry 272:22 (1997), 14037–14040.
-
(1997)
Journal of Biological Chemistry
, vol.272
, Issue.22
, pp. 14037-14040
-
-
Stutts, M.J.1
Rossier, B.C.2
Boucher, R.C.3
-
171
-
-
84918789823
-
Cathepsin B contributes to Na+ hyperabsorption in cystic fibrosis airway epithelial cultures
-
Tan, C.D., Hobbs, C., Sameni, M., Sloane, B.F., Stutts, M.J., Tarran, R., Cathepsin B contributes to Na+ hyperabsorption in cystic fibrosis airway epithelial cultures. J Physiol 592:23 (2014), 5251–5268.
-
(2014)
J Physiol
, vol.592
, Issue.23
, pp. 5251-5268
-
-
Tan, C.D.1
Hobbs, C.2
Sameni, M.3
Sloane, B.F.4
Stutts, M.J.5
Tarran, R.6
-
172
-
-
33645964965
-
Regulation of normal and cystic fibrosis airway surface liquid volume by phasic shear stress
-
Tarran, R., Button, B., Boucher, R.C., Regulation of normal and cystic fibrosis airway surface liquid volume by phasic shear stress. Annual Review of Physiology 68 (2006), 543–561.
-
(2006)
Annual Review of Physiology
, vol.68
, pp. 543-561
-
-
Tarran, R.1
Button, B.2
Boucher, R.C.3
-
173
-
-
27444444705
-
Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections
-
Tarran, R., Button, B., Picher, M., Paradiso, A.M., Ribeiro, C.M., Lazarowski, E.R., et al. Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections. Journal of Biological Chemistry 280:42 (2005), 35751–35759.
-
(2005)
Journal of Biological Chemistry
, vol.280
, Issue.42
, pp. 35751-35759
-
-
Tarran, R.1
Button, B.2
Picher, M.3
Paradiso, A.M.4
Ribeiro, C.M.5
Lazarowski, E.R.6
-
174
-
-
0031969149
-
Basal chloride currents in murine airway epithelial cells: Modulation by CFTR
-
Tarran, R., Gray, M.A., Evans, M.J., Colledge, W.H., Ratcliff, R., Argent, B.E., Basal chloride currents in murine airway epithelial cells: Modulation by CFTR. American Journal of Physiology 274:4 Pt 1 (1998), C904–C913.
-
(1998)
American Journal of Physiology
, vol.274
, Issue.4
, pp. C904-C913
-
-
Tarran, R.1
Gray, M.A.2
Evans, M.J.3
Colledge, W.H.4
Ratcliff, R.5
Argent, B.E.6
-
175
-
-
0034885192
-
The relative roles of passive surface forces and active ion transport in the modulation of airway surface liquid volume and composition
-
Tarran, R., Grubb, B.R., Gatzy, J.T., Davis, C.W., Boucher, R.C., The relative roles of passive surface forces and active ion transport in the modulation of airway surface liquid volume and composition. The Journal of General Physiology 118:2 (2001), 223–236.
-
(2001)
The Journal of General Physiology
, vol.118
, Issue.2
, pp. 223-236
-
-
Tarran, R.1
Grubb, B.R.2
Gatzy, J.T.3
Davis, C.W.4
Boucher, R.C.5
-
176
-
-
0034885663
-
The CF salt controversy: In vivo observations and therapeutic approaches
-
Tarran, R., Grubb, B.R., Parsons, D., Picher, M., Hirsh, A.J., Davis, C.W., et al. The CF salt controversy: In vivo observations and therapeutic approaches. Molecular Cell 8:1 (2001), 149–158.
-
(2001)
Molecular Cell
, vol.8
, Issue.1
, pp. 149-158
-
-
Tarran, R.1
Grubb, B.R.2
Parsons, D.3
Picher, M.4
Hirsh, A.J.5
Davis, C.W.6
-
177
-
-
0036712439
-
Regulation of murine airway surface liquid volume by CFTR and Ca2+-activated Cl- conductances
-
Tarran, R., Loewen, M.E., Paradiso, A.M., Olsen, J.C., Gray, M.A., Argent, B.E., et al. Regulation of murine airway surface liquid volume by CFTR and Ca2+-activated Cl- conductances. The Journal of General Physiology 120:3 (2002), 407–418.
-
(2002)
The Journal of General Physiology
, vol.120
, Issue.3
, pp. 407-418
-
-
Tarran, R.1
Loewen, M.E.2
Paradiso, A.M.3
Olsen, J.C.4
Gray, M.A.5
Argent, B.E.6
-
178
-
-
33646138489
-
Soluble mediators, not cilia, determine airway surface liquid volume in normal and cystic fibrosis superficial airway epithelia
-
Tarran, R., Trout, L., Donaldson, S.H., Boucher, R.C., Soluble mediators, not cilia, determine airway surface liquid volume in normal and cystic fibrosis superficial airway epithelia. The Journal of General Physiology 127:5 (2006), 591–604.
-
(2006)
The Journal of General Physiology
, vol.127
, Issue.5
, pp. 591-604
-
-
Tarran, R.1
Trout, L.2
Donaldson, S.H.3
Boucher, R.C.4
-
179
-
-
84888204096
-
Chloride channel-targeted therapy for secretory diarrheas
-
Thiagarajah, J.R., Verkman, A.S., Chloride channel-targeted therapy for secretory diarrheas. Current Opinion in Pharmacology 13:6 (2013), 888–894.
-
(2013)
Current Opinion in Pharmacology
, vol.13
, Issue.6
, pp. 888-894
-
-
Thiagarajah, J.R.1
Verkman, A.S.2
-
180
-
-
85041219723
-
Nominal carbonic anhydrase activity minimizes airway-surface liquid pH changes during breathing
-
Thornell, I.M., Li, X., Tang, X.X., Brommel, C.M., Karp, P.H., Welsh, M.J., et al. Nominal carbonic anhydrase activity minimizes airway-surface liquid pH changes during breathing. Physiol Rep, 6(2), 2018.
-
(2018)
Physiol Rep
, vol.6
, Issue.2
-
-
Thornell, I.M.1
Li, X.2
Tang, X.X.3
Brommel, C.M.4
Karp, P.H.5
Welsh, M.J.6
-
181
-
-
0018823482
-
Micropipette measurement of airway submucosal gland secretion. Autonomic effects
-
Ueki, I., German, V.F., Nadel, J.A., Micropipette measurement of airway submucosal gland secretion. Autonomic effects. American Review of Respiratory Disease 121:2 (1980), 351–357.
-
(1980)
American Review of Respiratory Disease
, vol.121
, Issue.2
, pp. 351-357
-
-
Ueki, I.1
German, V.F.2
Nadel, J.A.3
-
182
-
-
0030879756
-
An epithelial serine protease activates the amiloride-sensitive sodium channel
-
Vallet, V., Chraibi, A., Gaeggeler, H.P., Horisberger, J.D., Rossier, B.C., An epithelial serine protease activates the amiloride-sensitive sodium channel. Nature 389:6651 (1997), 607–610.
-
(1997)
Nature
, vol.389
, Issue.6651
, pp. 607-610
-
-
Vallet, V.1
Chraibi, A.2
Gaeggeler, H.P.3
Horisberger, J.D.4
Rossier, B.C.5
-
183
-
-
4143102440
-
The role of claudins in determining paracellular charge selectivity
-
Van Itallie, C.M., Anderson, J.M., The role of claudins in determining paracellular charge selectivity. Proceedings of the American Thoracic Society 1:1 (2004), 38–41.
-
(2004)
Proceedings of the American Thoracic Society
, vol.1
, Issue.1
, pp. 38-41
-
-
Van Itallie, C.M.1
Anderson, J.M.2
-
185
-
-
0023283053
-
Molecular mechanism of mucin secretion: I. The role of intragranular charge shielding
-
Verdugo, P., Deyrup-Olsen, I., Aitken, M., Villalon, M., Johnson, D., Molecular mechanism of mucin secretion: I. The role of intragranular charge shielding. Journal of Dental Research 66:2 (1987), 506–508.
-
(1987)
Journal of Dental Research
, vol.66
, Issue.2
, pp. 506-508
-
-
Verdugo, P.1
Deyrup-Olsen, I.2
Aitken, M.3
Villalon, M.4
Johnson, D.5
-
186
-
-
0036319341
-
Aquaporin water channels and endothelial cell function
-
Verkman, A.S., Aquaporin water channels and endothelial cell function. Journal of Anatomy 200:6 (2002), 617–627.
-
(2002)
Journal of Anatomy
, vol.200
, Issue.6
, pp. 617-627
-
-
Verkman, A.S.1
-
187
-
-
36148946059
-
Role of aquaporins in lung liquid physiology
-
Verkman, A.S., Role of aquaporins in lung liquid physiology. Respiratory Physiology & Neurobiology 159:3 (2007), 324–330.
-
(2007)
Respiratory Physiology & Neurobiology
, vol.159
, Issue.3
, pp. 324-330
-
-
Verkman, A.S.1
-
188
-
-
36148946059
-
Role of aquaporins in lung liquid physiology
-
Verkman, A.S., Role of aquaporins in lung liquid physiology. Respiratory Physiology & Neurobiology 159:3 (2007), 324–330.
-
(2007)
Respiratory Physiology & Neurobiology
, vol.159
, Issue.3
, pp. 324-330
-
-
Verkman, A.S.1
-
189
-
-
0034078270
-
Aquaporin water channels and lung physiology
-
Verkman, A.S., Matthay, M.A., Song, Y., Aquaporin water channels and lung physiology. American Journal of physiology. Lung Cellular and Molecular Physiology 278:5 (2000), L867–L879.
-
(2000)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.278
, Issue.5
, pp. L867-L879
-
-
Verkman, A.S.1
Matthay, M.A.2
Song, Y.3
-
190
-
-
0037213623
-
Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease
-
Verkman, A.S., Song, Y., Thiagarajah, J.R., Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease. American Journal of Physiology. Cell Physiology 284:1 (2003), C2–C15.
-
(2003)
American Journal of Physiology. Cell Physiology
, vol.284
, Issue.1
, pp. C2-C15
-
-
Verkman, A.S.1
Song, Y.2
Thiagarajah, J.R.3
-
191
-
-
0028057974
-
The lung amiloride-sensitive Na+ channel: Biophysical properties, pharmacology, ontogenesis, and molecular cloning
-
Voilley, N., Lingueglia, E., Champigny, G., Mattéi, M.G., Waldmann, R., Lazdunski, M., et al. The lung amiloride-sensitive Na+ channel: Biophysical properties, pharmacology, ontogenesis, and molecular cloning. Proceedings of the National Academy of Sciences of the United States of America 91:1 (1994), 247–251.
-
(1994)
Proceedings of the National Academy of Sciences of the United States of America
, vol.91
, Issue.1
, pp. 247-251
-
-
Voilley, N.1
Lingueglia, E.2
Champigny, G.3
Mattéi, M.G.4
Waldmann, R.5
Lazdunski, M.6
-
192
-
-
43049135102
-
Proteases and cystic fibrosis
-
Voynow, J.A., Fischer, B.M., Zheng, S., Proteases and cystic fibrosis. Int J Biochem Cell Biol 40:6–7 (2008), 1238–1245.
-
(2008)
Int J Biochem Cell Biol
, vol.40
, Issue.6-7
, pp. 1238-1245
-
-
Voynow, J.A.1
Fischer, B.M.2
Zheng, S.3
-
193
-
-
60249095813
-
Mucins, mucus, and sputum
-
Voynow, J.A., Rubin, B.K., Mucins, mucus, and sputum. Chest 135:2 (2009), 505–512.
-
(2009)
Chest
, vol.135
, Issue.2
, pp. 505-512
-
-
Voynow, J.A.1
Rubin, B.K.2
-
194
-
-
0036773382
-
Regulation of the depth and composition of airway surface liquid
-
Widdicombe, J.H., Regulation of the depth and composition of airway surface liquid. Journal of Anatomy 201:4 (2002), 313–318.
-
(2002)
Journal of Anatomy
, vol.201
, Issue.4
, pp. 313-318
-
-
Widdicombe, J.H.1
-
195
-
-
84940884841
-
Airway gland structure and function
-
Widdicombe, J.H., Wine, J.J., Airway gland structure and function. Physiological Reviews 95:4 (2015), 1241–1319.
-
(2015)
Physiological Reviews
, vol.95
, Issue.4
, pp. 1241-1319
-
-
Widdicombe, J.H.1
Wine, J.J.2
-
196
-
-
84879004810
-
The cystic fibrosis of exocrine pancreas
-
Wilschanski, M., Novak, I., The cystic fibrosis of exocrine pancreas. Cold Spring Harb Perspect Med, 3(5), 2013, a009746.
-
(2013)
Cold Spring Harb Perspect Med
, vol.3
, Issue.5
, pp. a009746
-
-
Wilschanski, M.1
Novak, I.2
-
197
-
-
0030931648
-
Stimulation of CFTR activity by its phosphorylated R domain
-
Winter, M.C., Welsh, M.J., Stimulation of CFTR activity by its phosphorylated R domain. Nature, 389, 1997, 294.
-
(1997)
Nature
, vol.389
, pp. 294
-
-
Winter, M.C.1
Welsh, M.J.2
-
198
-
-
85002214717
-
Tight junctions in pulmonary epithelia during lung inflammation
-
Wittekindt, O.H., Tight junctions in pulmonary epithelia during lung inflammation. Pflügers Archiv 469:1 (2017), 135–147.
-
(2017)
Pflügers Archiv
, vol.469
, Issue.1
, pp. 135-147
-
-
Wittekindt, O.H.1
-
199
-
-
85011932669
-
Identification of BPIFA1/SPLUNC1 as an epithelium-derived smooth muscle relaxing factor
-
Wu, T., Huang, J., Moore, P.J., Little, M.S., Walton, W.G., Fellner, R.C., et al. Identification of BPIFA1/SPLUNC1 as an epithelium-derived smooth muscle relaxing factor. Nature Communications, 8, 2017, 14118.
-
(2017)
Nature Communications
, vol.8
, pp. 14118
-
-
Wu, T.1
Huang, J.2
Moore, P.J.3
Little, M.S.4
Walton, W.G.5
Fellner, R.C.6
-
200
-
-
85056746783
-
Airway epithelial cell cilia and obstructive lung disease
-
Yaghi, A., Dolovich, M.B., Airway epithelial cell cilia and obstructive lung disease. Cells, 5(4), 2016, 40.
-
(2016)
Cells
, vol.5
, Issue.4
, pp. 40
-
-
Yaghi, A.1
Dolovich, M.B.2
-
201
-
-
55249091085
-
TMEM16A confers receptor-activated calcium-dependent chloride conductance
-
Yang, Y.D., Cho, H., Koo, J.Y., Tak, M.H., Cho, Y., Shim, W.S., et al. TMEM16A confers receptor-activated calcium-dependent chloride conductance. Nature 455:7217 (2008), 1210–1215.
-
(2008)
Nature
, vol.455
, Issue.7217
, pp. 1210-1215
-
-
Yang, Y.D.1
Cho, H.2
Koo, J.Y.3
Tak, M.H.4
Cho, Y.5
Shim, W.S.6
-
202
-
-
2542500548
-
Cystic fibrosis transmembrane conductance regulator differentially regulates human and mouse epithelial sodium channels in Xenopus oocytes
-
Yan, W., Samaha, F.F., Ramkumar, M., Kleyman, T.R., Rubenstein, R.C., Cystic fibrosis transmembrane conductance regulator differentially regulates human and mouse epithelial sodium channels in Xenopus oocytes. Journal of Biological Chemistry 279:22 (2004), 23183–23192.
-
(2004)
Journal of Biological Chemistry
, vol.279
, Issue.22
, pp. 23183-23192
-
-
Yan, W.1
Samaha, F.F.2
Ramkumar, M.3
Kleyman, T.R.4
Rubenstein, R.C.5
-
203
-
-
0026511839
-
Antibiotic peptides as mediators of innate immunity
-
Zasloff, M., Antibiotic peptides as mediators of innate immunity. Current Opinion in Immunology 4:1 (1992), 3–7.
-
(1992)
Current Opinion in Immunology
, vol.4
, Issue.1
, pp. 3-7
-
-
Zasloff, M.1
-
204
-
-
84885430741
-
Neutrophil extracellular traps (NETs) - formation and implications
-
Zawrotniak, M., Rapala-Kozik, M., Neutrophil extracellular traps (NETs) - formation and implications. Acta Biochimica Polonica 60:3 (2013), 277–284.
-
(2013)
Acta Biochimica Polonica
, vol.60
, Issue.3
, pp. 277-284
-
-
Zawrotniak, M.1
Rapala-Kozik, M.2
-
205
-
-
83755173577
-
A role for two-pore K(+) channels in modulating Na(+) absorption and Cl(-) secretion in normal human bronchial epithelial cells
-
Zhao, K.Q., Xiong, G., Wilber, M., Cohen, N.A., Kreindler, J.L., A role for two-pore K(+) channels in modulating Na(+) absorption and Cl(-) secretion in normal human bronchial epithelial cells. American Journal of physiology. Lung Cellular and Molecular Physiology 302:1 (2012), L4–L12.
-
(2012)
American Journal of physiology. Lung Cellular and Molecular Physiology
, vol.302
, Issue.1
, pp. L4-L12
-
-
Zhao, K.Q.1
Xiong, G.2
Wilber, M.3
Cohen, N.A.4
Kreindler, J.L.5
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