Airway surface liquid homeostasis in cystic fibrosis: Pathophysiology and therapeutic targets

Thorax

Volumn 71, Issue 3, 2016, Pages 284-287

  Haq, Iram J ^a,b   Gray, Michael A ^c   Garnett, James P ^a   Ward, Christopher ^a,c   Brodlie, Malcolm ^a,b  

^a NEWCASTLE UNIVERSITY   (United Kingdom)

^b Newcastle Upon Tyne Hospitals NHS Foundation Trust   (United Kingdom)

^c NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ANOCTAMIN 1 PROTEIN; CARRIER PROTEINS AND BINDING PROTEINS; CHLORIDE CHANNEL; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL SODIUM CHANNEL; SHORT PALATE LUNG AND NASAL EPITHELIAL CLONE 1 PROTEIN; UNCLASSIFIED DRUG; BICARBONATE;

AIRWAY SURFACE LIQUID; CYSTIC FIBROSIS; DEHYDRATION; DISEASE ASSOCIATION; HOMEOSTASIS; HUMAN; MUCUS; NONHUMAN; PATHOPHYSIOLOGY; PH; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN TARGETING; PROTEIN TRANSPORT; RESPIRATORY SYSTEM; REVIEW; UPREGULATION; DISEASE MANAGEMENT; ION TRANSPORT; METABOLISM; MUCOCILIARY CLEARANCE; PHYSIOLOGY; RESPIRATORY TRACT MUCOSA;

BICARBONATES; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DISEASE MANAGEMENT; HOMEOSTASIS; HUMANS; ION TRANSPORT; MUCOCILIARY CLEARANCE; RESPIRATORY MUCOSA;

EID: 84954285138     PISSN: 00406376     EISSN: 14683296     Source Type: Journal    
DOI: 10.1136/thoraxjnl-2015-207588     Document Type: Review

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