The Copper Metabolism MURR1 Domain protein 1 (COMMD1) modulates the aggregation of misfolded protein species in a client-specific manner

PLoS ONE

Volumn 9, Issue 4, 2014, Pages

  Vonk, Willianne I M ^a,d   Kakkar, Vaishali ^b   Bartuzi, Paulina ^b   Jaarsma, Dick ^c   Berger, Ruud ^a   Hofker, Marten H ^b   Klomp, Leo W J ^a   Wijmenga, Cisca ^a,b   Kampinga, Harm H ^b   Van De Sluis, Bart ^b  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^b UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^c ERASMUS MEDICAL CENTER   (Netherlands)

^d STANFORD UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; CYSTEINE; HUNTINGTIN; MUTANT PROTEIN; PARKIN; PEPTIDES AND PROTEINS; POLYGLUTAMINE; PROTEIN COMMD1; UNCLASSIFIED DRUG; COMMD1 PROTEIN, HUMAN; PEPTIDE; PROTEIN AGGREGATE; PROTEIN BINDING; SIGNAL TRANSDUCING ADAPTOR PROTEIN; SUPEROXIDE DISMUTASE; UBIQUITIN PROTEIN LIGASE;

AMINO ACID SUBSTITUTION; ARTICLE; COMPLEX FORMATION; CONTROLLED STUDY; EMBRYO; HUMAN; HUMAN CELL; MOLECULAR WEIGHT; PROTEIN AGGREGATION; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN LOCALIZATION; PROTEIN MODIFICATION; PROTEIN PROTEIN INTERACTION; PROTEIN UNFOLDING; WILD TYPE; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL; CHEMISTRY; HEK293 CELL LINE; HELA CELL LINE; METABOLISM; MOUSE; PROTEIN FOLDING; PROTEIN MULTIMERIZATION;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; HEK293 CELLS; HELA CELLS; HUMANS; MICE; MOLECULAR WEIGHT; MUTANT PROTEINS; PEPTIDES; PROTEIN AGGREGATES; PROTEIN BINDING; PROTEIN FOLDING; PROTEIN MULTIMERIZATION; SUPEROXIDE DISMUTASE; UBIQUITIN-PROTEIN LIGASES;

EID: 84898862914     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0092408     Document Type: Article

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