-
1
-
-
0032926368
-
Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis
-
Al-Chalabi, A., Andersen, P.M., Nilsson, P., Chioza, B., Andersson, J.L., Russ, C., Shaw, C.E., Powell, J.F., and Leigh, P.N. (1999). Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis. Hum. Mol. Genet. 8, 157-164.
-
(1999)
Hum. Mol. Genet.
, vol.8
, pp. 157-164
-
-
Al-Chalabi, A.1
Andersen, P.M.2
Nilsson, P.3
Chioza, B.4
Andersson, J.L.5
Russ, C.6
Shaw, C.E.7
Powell, J.F.8
Leigh, P.N.9
-
2
-
-
0031784348
-
Protein oxidative damage in a transgenic mouse model of familial amyotrophic lateral sclerosis
-
Andrus, P.K., Fleck, T.J., Gurney, M.E., and Hall, E.D. (1998). Protein oxidative damage in a transgenic mouse model of familial amyotrophic lateral sclerosis. J. Neurochem. 71, 2041-2048.
-
(1998)
J. Neurochem.
, vol.71
, pp. 2041-2048
-
-
Andrus, P.K.1
Fleck, T.J.2
Gurney, M.E.3
Hall, E.D.4
-
3
-
-
0027293275
-
ALS, SOD and peroxynitrite
-
Beckman, J.S., Carson, M., Smith, C.D., and Koppenol, W.H. (1993). ALS, SOD and peroxynitrite. Nature 364, 584.
-
(1993)
Nature
, vol.364
, pp. 584
-
-
Beckman, J.S.1
Carson, M.2
Smith, C.D.3
Koppenol, W.H.4
-
4
-
-
0027965073
-
Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity
-
Borchelt, D.R., Lee, M.K., Slunt, H.S., Guarnieri, M., Xu, Z.S., Wong, P.C., Brown, R.H., Jr., Price, D.L., Sisodia, S.S., and Cleveland, D.W. (1994). Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity. Proc. Natl. Acad. Sci. USA 91, 8292-8296.
-
(1994)
Proc. Natl. Acad. Sci. USA
, vol.91
, pp. 8292-8296
-
-
Borchelt, D.R.1
Lee, M.K.2
Slunt, H.S.3
Guarnieri, M.4
Xu, Z.S.5
Wong, P.C.6
Brown R.H., Jr.7
Price, D.L.8
Sisodia, S.S.9
Cleveland, D.W.10
-
5
-
-
0027359334
-
Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis
-
Bowling, A.C., Schulz, J.B., Brown, R.H., Jr., and Beal, M.F. (1993). Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis. J. Neurochem. 61, 2322-2325.
-
(1993)
J. Neurochem.
, vol.61
, pp. 2322-2325
-
-
Bowling, A.C.1
Schulz, J.B.2
Brown R.H., Jr.3
Beal, M.F.4
-
6
-
-
0028960506
-
Amyotrophic lateral sclerosis: Recent insights from genetics and transgenic mice
-
Brown, R.H. (1995). Amyotrophic lateral sclerosis: recent insights from genetics and transgenic mice. Cell 80, 687-692.
-
(1995)
Cell
, vol.80
, pp. 687-692
-
-
Brown, R.H.1
-
7
-
-
0344507132
-
Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis
-
Bruening, W., Roy, J., Giasson, B., Figlewicz, D.A., Mushynski, W.E., and Durham, H.D. (1999). Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis. J. Neurochem. 72, 693-699.
-
(1999)
J. Neurochem.
, vol.72
, pp. 693-699
-
-
Bruening, W.1
Roy, J.2
Giasson, B.3
Figlewicz, D.A.4
Mushynski, W.E.5
Durham, H.D.6
-
8
-
-
0030806228
-
Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superoxidase dismutase 1 mutant
-
Bruijn, L.I., Beal, M.F., Becher, M.W., Schulz, J.B., Wong, P.C., Price, D.L., and Cleveland, D.W. (1997a). Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superoxidase dismutase 1 mutant. Proc. Natl. Acad. Sci. USA 94, 7606-7611.
-
(1997)
Proc. Natl. Acad. Sci. USA
, vol.94
, pp. 7606-7611
-
-
Bruijn, L.I.1
Beal, M.F.2
Becher, M.W.3
Schulz, J.B.4
Wong, P.C.5
Price, D.L.6
Cleveland, D.W.7
-
9
-
-
0031051485
-
ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions
-
Bruijn, L.I., Becher, M.W., Lee, M.K., Anderson, K.L., Jenkins, N.A., Copeland, N.G., Sisodia, S.S., Rothstein, J.D., Borchelt, D.R., Price, D.L., and Cleveland, D.W. (1997b). ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions. Neuron 18, 327-338.
-
(1997)
Neuron
, vol.18
, pp. 327-338
-
-
Bruijn, L.I.1
Becher, M.W.2
Lee, M.K.3
Anderson, K.L.4
Jenkins, N.A.5
Copeland, N.G.6
Sisodia, S.S.7
Rothstein, J.D.8
Borchelt, D.R.9
Price, D.L.10
Cleveland, D.W.11
-
10
-
-
0032544674
-
Aggregation and motor neuron toxicity of an ALS-linked SOD1 mutant independent from wild-type SOD1
-
Bruijn, L.I., Houseweart, M.K., Kato, S., Anderson, K.A., Anderson, S.D., Ohama, E., Reaume, A.G., Scott, R.W., and Cleveland, D.W. (1998). Aggregation and motor neuron toxicity of an ALS-linked SOD1 mutant independent from wild-type SOD1. Science 281, 1851 -1854.
-
(1998)
Science
, vol.281
, pp. 1851-1854
-
-
Bruijn, L.I.1
Houseweart, M.K.2
Kato, S.3
Anderson, K.A.4
Anderson, S.D.5
Ohama, E.6
Reaume, A.G.7
Scott, R.W.8
Cleveland, D.W.9
-
11
-
-
0032568546
-
Chaperone-facilitated loading of copper is a common in vivo property of familial ALS-linked SOD1 mutants
-
Corson, L.B., Strain, J., Culotta, V.C., and Cleveland, D.W. (1998). Chaperone-facilitated loading of copper is a common in vivo property of familial ALS-linked SOD1 mutants. Proc. Natl. Acad. Sci. USA 95, 6361-6366.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 6361-6366
-
-
Corson, L.B.1
Strain, J.2
Culotta, V.C.3
Cleveland, D.W.4
-
12
-
-
0032483016
-
Protective effect of neurofilament NF-H overexpression in motor neuron disease induced by mutant superoxide dismutase
-
Couillard-Despres, S., Zhu, Q., Wong, P., Price, D.L., Cleveland, D.W., and Julien, J.-P. (1998). Protective effect of neurofilament NF-H overexpression in motor neuron disease induced by mutant superoxide dismutase. Proc. Natl. Acad. Sci. USA 95, 9626-9630.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 9626-9630
-
-
Couillard-Despres, S.1
Zhu, Q.2
Wong, P.3
Price, D.L.4
Cleveland, D.W.5
Julien, J.-P.6
-
13
-
-
0031057003
-
Epidemiology of mutations in superoxide dismutase in amyotrophic lateral sclerosis
-
Cudkowicz, M.E., McKenna-Yasek, D., Sapp, P.E., Chin, W., Geller, B., Hayden, D.L., Schoenfeld, D.A., Hosler, B.A., Horvitz, H.R., and Brown, R.H. (1997). Epidemiology of mutations in superoxide dismutase in amyotrophic lateral sclerosis. Ann. Neurol. 41, 210-221.
-
(1997)
Ann. Neurol.
, vol.41
, pp. 210-221
-
-
Cudkowicz, M.E.1
McKenna-Yasek, D.2
Sapp, P.E.3
Chin, W.4
Geller, B.5
Hayden, D.L.6
Schoenfeld, D.A.7
Hosler, B.A.8
Horvitz, H.R.9
Brown, R.H.10
-
14
-
-
0030802648
-
The copper chaperone for superoxide dismutase
-
Culotta, V.C., Klomp, L.W.J., Strain, J., Casaren, R.L.B., Krems, B., and Gitlin, J.D. (1997). The copper chaperone for superoxide dismutase. J. Biol. Chem. 272, 23469-23472.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 23469-23472
-
-
Culotta, V.C.1
Klomp, L.W.J.2
Strain, J.3
Casaren, R.L.B.4
Krems, B.5
Gitlin, J.D.6
-
15
-
-
0030777650
-
Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS
-
Durham, H.D., Roy, J., Dong, L., and Figlewicz, D.A. (1997). Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS. J. Neuropathol. Exp. Neurol. 56, 52-56.
-
(1997)
J. Neuropathol. Exp. Neurol.
, vol.56
, pp. 52-56
-
-
Durham, H.D.1
Roy, J.2
Dong, L.3
Figlewicz, D.A.4
-
16
-
-
0030813067
-
Evidence of increased oxidative damage in both sporadic and familial amyotrophic lateral sclerosis
-
Ferrante, R.J., Browne, S.E., Shinobu, L.A., Bowling, A.C., Baik, M.J., MacGarvey, U., Kowall, N.W., Brown, R.H., Jr., and Beal, M.F. (1997). Evidence of increased oxidative damage in both sporadic and familial amyotrophic lateral sclerosis. J. Neurochem. 69, 2064-2074.
-
(1997)
J. Neurochem.
, vol.69
, pp. 2064-2074
-
-
Ferrante, R.J.1
Browne, S.E.2
Shinobu, L.A.3
Bowling, A.C.4
Baik, M.J.5
MacGarvey, U.6
Kowall, N.W.7
Brown R.H., Jr.8
Beal, M.F.9
-
17
-
-
0028001606
-
Variants of the heavy neurofilament subunit are associated with the development of amyotrophic lateral sclerosis
-
Figlewicz, D.A., Krizus, A., Martinoli, M.G., Meininger, V., Dib, M., Rouleau, G.A., and Julien, J.P. (1994). Variants of the heavy neurofilament subunit are associated with the development of amyotrophic lateral sclerosis. Hum. Mol. Genet. 3, 1757-1761.
-
(1994)
Hum. Mol. Genet.
, vol.3
, pp. 1757-1761
-
-
Figlewicz, D.A.1
Krizus, A.2
Martinoli, M.G.3
Meininger, V.4
Dib, M.5
Rouleau, G.A.6
Julien, J.P.7
-
18
-
-
1842407161
-
Inhibition of ICE slows ALS in mice
-
Friedlander, R.M., Brown, R.H., Gagliardini, V., Wang, J., and Yuan, J. (1997). Inhibition of ICE slows ALS in mice. Nature 388, 31.
-
(1997)
Nature
, vol.388
, pp. 31
-
-
Friedlander, R.M.1
Brown, R.H.2
Gagliardini, V.3
Wang, J.4
Yuan, J.5
-
19
-
-
0028284779
-
Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation
-
Gurney, M.E., Pu, H., Chiu, A.Y., Dal Canto, M.C., Polchow, C.Y., Alexander, D.D., Caliendo, J., Hentati, A., Kwon, Y.W., and Deng, H.X. (1994). Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation. Science 264, 1772-1775.
-
(1994)
Science
, vol.264
, pp. 1772-1775
-
-
Gurney, M.E.1
Pu, H.2
Chiu, A.Y.3
Dal Canto, M.C.4
Polchow, C.Y.5
Alexander, D.D.6
Caliendo, J.7
Hentati, A.8
Kwon, Y.W.9
Deng, H.X.10
-
20
-
-
0030050727
-
Benefit of vitamin E, riluzole, and gabapentin in a transgenic model of familial amyotrophic lateral sclerosis
-
Gurney, M.E., Cutting, F.B., Zhai, P., Doble, A., Taylor, C.P., Andrus, P.K., and Hall, E.D. (1996). Benefit of vitamin E, riluzole, and gabapentin in a transgenic model of familial amyotrophic lateral sclerosis. Ann. Neurol. 39, 147-157.
-
(1996)
Ann. Neurol.
, vol.39
, pp. 147-157
-
-
Gurney, M.E.1
Cutting, F.B.2
Zhai, P.3
Doble, A.4
Taylor, C.P.5
Andrus, P.K.6
Hall, E.D.7
-
21
-
-
0021167918
-
Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis
-
Hirano, A., Donnenfeld, H., Sasaki, S., and Nakano, I. (1984a). Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis. J. Neuropathol. Exp. Neurol. 43, 461-470.
-
(1984)
J. Neuropathol. Exp. Neurol.
, vol.43
, pp. 461-470
-
-
Hirano, A.1
Donnenfeld, H.2
Sasaki, S.3
Nakano, I.4
-
22
-
-
0021157469
-
Fine structural study of neurofibrillary changes in a family with amyotrophic lateral sclerosis
-
Hirano, A., Nakano, I., Kurland, L.T., Mulder, D.W., Holley, P.W., and Saccomanno, G. (1984b). Fine structural study of neurofibrillary changes in a family with amyotrophic lateral sclerosis. J. Neuropathol. Exp. Neurol. 43, 471-480.
-
(1984)
J. Neuropathol. Exp. Neurol.
, vol.43
, pp. 471-480
-
-
Hirano, A.1
Nakano, I.2
Kurland, L.T.3
Mulder, D.W.4
Holley, P.W.5
Saccomanno, G.6
-
23
-
-
0019784990
-
Morphometric comparison of the vulnerability of peripheral motor and sensory neurons in amyotrophic lateral sclerosis
-
Kawamura, Y., Dyck, P.J., Shimono, M., Okazaki, H., Tateishi, J., and Doi, H. (1981). Morphometric comparison of the vulnerability of peripheral motor and sensory neurons in amyotrophic lateral sclerosis. J. Neuropathol. Exp. Neurol. 40, 667-675.
-
(1981)
J. Neuropathol. Exp. Neurol.
, vol.40
, pp. 667-675
-
-
Kawamura, Y.1
Dyck, P.J.2
Shimono, M.3
Okazaki, H.4
Tateishi, J.5
Doi, H.6
-
24
-
-
0033051815
-
Neuroprotective effects of creatin in a transgenic animal model of amyotrophic lateral sclerosis
-
Klivenyi, P., Ferrante, R.J., Matthews, R.T., Bogdanov, M.B., Klein, A.M., Andreassen, O.A., Meuller, G., Wermer, M., Kaddurah-Daouk, R., and Beal, M.F. (1999). Neuroprotective effects of creatin in a transgenic animal model of amyotrophic lateral sclerosis. Nat. Med. 5, 347-350.
-
(1999)
Nat. Med.
, vol.5
, pp. 347-350
-
-
Klivenyi, P.1
Ferrante, R.J.2
Matthews, R.T.3
Bogdanov, M.B.4
Klein, A.M.5
Andreassen, O.A.6
Meuller, G.7
Wermer, M.8
Kaddurah-Daouk, R.9
Beal, M.F.10
-
25
-
-
0030756459
-
Bcl-2 prolonging life in a transgenic mouse model of familial amyotrophic lateral sclerosis
-
Kostic, V., Jackson-Lewis, V., deBilbao, F., Dubois-Dauphin, M., and Przedborski, S. (1997). Bcl-2 prolonging life in a transgenic mouse model of familial amyotrophic lateral sclerosis. Science 277, 559-562.
-
(1997)
Science
, vol.277
, pp. 559-562
-
-
Kostic, V.1
Jackson-Lewis, V.2
DeBilbao, F.3
Dubois-Dauphin, M.4
Przedborski, S.5
-
26
-
-
0029977337
-
Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II
-
Lacomblez, L., Bensimon, G., Leigh, P.N., Guillet, P., and Meininger, V. (1996). Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II. Lancet 347, 1425-1431.
-
(1996)
Lancet
, vol.347
, pp. 1425-1431
-
-
Lacomblez, L.1
Bensimon, G.2
Leigh, P.N.3
Guillet, P.4
Meininger, V.5
-
27
-
-
0032032013
-
Aberrant RNA processing in a neurodegenerative disease: The cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis
-
Lin, C.L., Bristol, L.A., Jin, L., Dykes-Hoberg, M., Crawford, T., Clawson, L., and Rothstein, J.D. (1998). Aberrant RNA processing in a neurodegenerative disease: the cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis. Neuron 20, 589-602.
-
(1998)
Neuron
, vol.20
, pp. 589-602
-
-
Lin, C.L.1
Bristol, L.A.2
Jin, L.3
Dykes-Hoberg, M.4
Crawford, T.5
Clawson, L.6
Rothstein, J.D.7
-
28
-
-
0032549709
-
Identification of alternative splicing forms of GLT-1 mRNA in the spinal cord of amyotrophic lateral sclerosis patients
-
Nagai, M., Abe, K., Okamoto, K., and Itoyama, Y. (1998). Identification of alternative splicing forms of GLT-1 mRNA in the spinal cord of amyotrophic lateral sclerosis patients. Neurosci. Lett. 244,165-168.
-
(1998)
Neurosci. Lett.
, vol.244
, pp. 165-168
-
-
Nagai, M.1
Abe, K.2
Okamoto, K.3
Itoyama, Y.4
-
29
-
-
15844393658
-
Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury
-
Reaume, A.B., Elliott, J.L., Hoffman, E.K., Kowall, N.W., Ferrante, R.J., Siwek, D.F., Wilcox, H.M., Flood, D.G., Beal, M.F., Brown, R.H., et al. (1996). Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury. Nat. Genet. 13, 43-47.
-
(1996)
Nat. Genet.
, vol.13
, pp. 43-47
-
-
Reaume, A.B.1
Elliott, J.L.2
Hoffman, E.K.3
Kowall, N.W.4
Ferrante, R.J.5
Siwek, D.F.6
Wilcox, H.M.7
Flood, D.G.8
Beal, M.F.9
Brown, R.H.10
-
30
-
-
0028888945
-
Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis
-
Ripps, M.E., Huntley, G.W., Hof, P.R., Morrison, J.H., and Gordon, J.W. (1995). Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis. Proc. Natl. Acad. Sci. USA 92, 689-693.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 689-693
-
-
Ripps, M.E.1
Huntley, G.W.2
Hof, P.R.3
Morrison, J.H.4
Gordon, J.W.5
-
31
-
-
0027401203
-
Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis
-
Rosen, D.R., Siddique, T., Patterson, D., Figlewicz, D.A., Sapp, P., Hentati, A., Donaldson, D., Goto, J., O'Regan, J.P., Deng, H.X., et al. (1993). Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis. Nature 362, 59-62.
-
(1993)
Nature
, vol.362
, pp. 59-62
-
-
Rosen, D.R.1
Siddique, T.2
Patterson, D.3
Figlewicz, D.A.4
Sapp, P.5
Hentati, A.6
Donaldson, D.7
Goto, J.8
O'Regan, J.P.9
Deng, H.X.10
-
32
-
-
0029030610
-
Selective loss of glial glutamate transporter GLT-1 in amyotrophic lateral sclerosis
-
Rothstein, J.D.,Van Kammen,M., Levey, A.I., Martin, LJ., and Kuncl, R.W. (1995). Selective loss of glial glutamate transporter GLT-1 in amyotrophic lateral sclerosis. Ann. Neurol. 38, 73-84.
-
(1995)
Ann. Neurol.
, vol.38
, pp. 73-84
-
-
Rothstein, J.D.1
Van Kammen, M.2
Levey, A.I.3
Martin, L.J.4
Kuncl, R.W.5
-
33
-
-
0032499788
-
Reexamination of the mechanism of hydroxyl radical adducts formed from the reaction between familial amyotrophic lateral sclerosis-associated Cu,Zn superoxide dismutase mutants and hydrogen peroxide
-
Singh, R.J., Karoui, H., Gunther, M.R., Beckman, J.S., Mason, R.P., and Kalyanaraman, B. (1998). Reexamination of the mechanism of hydroxyl radical adducts formed from the reaction between familial amyotrophic lateral sclerosis-associated Cu,Zn superoxide dismutase mutants and hydrogen peroxide. Proc. Natl. Acad. Sci. USA 95, 6675-6680.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 6675-6680
-
-
Singh, R.J.1
Karoui, H.2
Gunther, M.R.3
Beckman, J.S.4
Mason, R.P.5
Kalyanaraman, B.6
-
34
-
-
0032427646
-
Novel insertion in the KSP repeat region of the neurofilament heavy gene in amyotrophic lateral sclerosis
-
Tomkins, J., Usher, P., Slade, J.Y., Ince, P.G., Curtis, A., Bushby, K., and Shaw, P.J. (1998). Novel insertion in the KSP repeat region of the neurofilament heavy gene in amyotrophic lateral sclerosis. Neuroreport 9, 3967-3970.
-
(1998)
Neuroreport
, vol.9
, pp. 3967-3970
-
-
Tomkins, J.1
Usher, P.2
Slade, J.Y.3
Ince, P.G.4
Curtis, A.5
Bushby, K.6
Shaw, P.J.7
-
35
-
-
0033366461
-
SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter
-
Trotti, D., Rolfs, A., Danbolt, N.C., Brown, R.H., Jr., and Hediger, M.A. (1999). SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter. Nat. Neurosci. 2, 427-433.
-
(1999)
Nat. Neurosci.
, vol.2
, pp. 427-433
-
-
Trotti, D.1
Rolfs, A.2
Danbolt, N.C.3
Brown R.H., Jr.4
Hediger, M.A.5
-
36
-
-
0033585832
-
Selective impairment of fast anterograde axonal transport in the peripheral nerves of asymptomatic transgenic mice with a G93A mutant SOD1 gene
-
Warita, H., Itoyama, Y., and Abe, K. (1999). Selective impairment of fast anterograde axonal transport in the peripheral nerves of asymptomatic transgenic mice with a G93A mutant SOD1 gene. Brain Res. 819, 120-131.
-
(1999)
Brain Res.
, vol.819
, pp. 120-131
-
-
Warita, H.1
Itoyama, Y.2
Abe, K.3
-
37
-
-
0029671220
-
Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis
-
Wiedau-Pazos, M., Goto, J.J., Rabizadeh, S., Gralla, E.D., Roe, J.A., Valentine, J.S., and Bredesen, D.E. (1996). Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis. Science 271, 515-518.
-
(1996)
Science
, vol.271
, pp. 515-518
-
-
Wiedau-Pazos, M.1
Goto, J.J.2
Rabizadeh, S.3
Gralla, E.D.4
Roe, J.A.5
Valentine, J.S.6
Bredesen, D.E.7
-
38
-
-
0033366384
-
Slowing of axonal transport is a very early event in the toxicity of ALS-linked SOD1 mutants to motor neurons
-
Williamson, T.L., and Cleveland, D.W. (1999). Slowing of axonal transport is a very early event in the toxicity of ALS-linked SOD1 mutants to motor neurons. Nat. Neurosci. 2, 50-56.
-
(1999)
Nat. Neurosci.
, vol.2
, pp. 50-56
-
-
Williamson, T.L.1
Cleveland, D.W.2
-
39
-
-
0032482976
-
Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant
-
Williamson, T.L., Bruijn, L.I., Zhu, Q., Anderson, K.L., Anderson, S.D., Julien, J.-P., and Cleveland, D.W. (1998). Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant. Proc. Natl. Acad. Sci. USA 95,2631-2636.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 2631-2636
-
-
Williamson, T.L.1
Bruijn, L.I.2
Zhu, Q.3
Anderson, K.L.4
Anderson, S.D.5
Julien, J.-P.6
Cleveland, D.W.7
-
40
-
-
0029053881
-
An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria
-
Wong, P.C., Pardo, C.A., Borchelt, D.R., Lee, M.K., Copeland, N.G., Jenkins, N.A., Sisodia, S.S., Cleveland, D.W., and Price, D.L. (1995). An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria. Neuron 14, 1105-1116.
-
(1995)
Neuron
, vol.14
, pp. 1105-1116
-
-
Wong, P.C.1
Pardo, C.A.2
Borchelt, D.R.3
Lee, M.K.4
Copeland, N.G.5
Jenkins, N.A.6
Sisodia, S.S.7
Cleveland, D.W.8
Price, D.L.9
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