An enhanced integrated stress response ameliorates mutant SOD1-induced ALS

Human Molecular Genetics

Volumn 23, Issue 10, 2014, Pages 2629-2638

  Wang, Lijun ^a   Popko, Brian ^a,b   Roos, Raymond P ^a,b  

^a UNIVERSITY OF CHICAGO   (United States)

^b The University of Chicago Pritzker School of Medicine   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; GROWTH ARREST AND DNA DAMAGE INDUCIBLE PROTEIN 153; GROWTH ARREST AND DNA DAMAGE INDUCIBLE PROTEIN 34; INITIATION FACTOR 2ALPHA; PKR LIKE LOCALIZED EIF2 KINASE; PROTEIN KINASE; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG; BIOLOGICAL MARKER; INITIATION FACTOR 2; PHOSPHOPROTEIN PHOSPHATASE 1; PPP1R15A PROTEIN, MOUSE; SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISEASE DURATION; ENDOPLASMIC RETICULUM; ENZYME PHOSPHORYLATION; INTEGRATED STRESS RESPONSE; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEPHOSPHORYLATION; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN SYNTHESIS INHIBITION; SIGNAL TRANSDUCTION; STRESS; SURVIVAL TIME; TRANSGENIC MOUSE; ANIMAL; C57BL MOUSE; CELL CULTURE; ENDOPLASMIC RETICULUM STRESS; GENETICS; METABOLISM; MISSENSE MUTATION; PROTEIN PROCESSING;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; BIOLOGICAL MARKERS; CELLS, CULTURED; ENDOPLASMIC RETICULUM STRESS; EUKARYOTIC INITIATION FACTOR-2; MICE, INBRED C57BL; MICE, TRANSGENIC; MUTATION, MISSENSE; PROTEIN PHOSPHATASE 1; PROTEIN PROCESSING, POST-TRANSLATIONAL; SUPEROXIDE DISMUTASE;

EID: 84898817967     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddt658     Document Type: Article

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