Derlin-1 overexpression ameliorates mutant SOD1-induced endoplasmic reticulum stress by reducing mutant SOD1 accumulation

Neurochemistry International

Volumn 58, Issue 3, 2011, Pages 344-353

  Mori, Akira ^a   Yamashita, Satoshi ^a   Uchino, Katsuhisa ^a   Suga, Tomohiro ^a   Ikeda, Tokunori ^a   Takamatsu, Koutaro ^a   Ishizaki, Masatoshi ^a   Koide, Tatsuya ^a   Kimura, En ^a   Mita, Shuji ^b   Maeda, Yasushi ^a   Hirano, Teruyuki ^a   Uchino, Makoto ^a  

^a KUMAMOTO UNIVERSITY   (Japan)

^b Nishi Kumamoto Hospital   (Japan)

Author keywords

Amyotrophic lateral sclerosis (ALS); Autophagy; Cu Zn superoxide dismutase (SOD1); Derlin 1; Endoplasmic reticulum (ER) stress; ER associated degradation (ERAD)

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 6; COPPER ZINC SUPEROXIDE DISMUTASE; DERLIN 1; IMMUNOGLOBULIN; MESSENGER RNA; MUTANT PROTEIN; PROTEASOME; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; APOPTOSIS; ARTICLE; AUTOPHAGY; BIOACCUMULATION; CELL VIABILITY; CONTROLLED STUDY; CYTOTOXICITY; DISEASE ASSOCIATION; ENDOPLASMIC RETICULUM STRESS; EVOKED RESPONSE; GENETIC TRANSFECTION; MICROSOME; MOLECULAR DYNAMICS; MOUSE; NEUROBLASTOMA CELL; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; REAL TIME POLYMERASE CHAIN REACTION; REGULATORY MECHANISM; WILD TYPE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AUTOPHAGY; CELL LINE, TUMOR; DOWN-REGULATION; ENDOPLASMIC RETICULUM; HUMANS; MEMBRANE PROTEINS; MICE; MUTATION; NEURONS; PROTEASOME ENDOPEPTIDASE COMPLEX; RNA, MESSENGER; STRESS, PHYSIOLOGICAL; SUPEROXIDE DISMUTASE;

EID: 79951578353     PISSN: 01970186     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neuint.2010.12.010     Document Type: Article

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