Astrocyte loss of mutant SOD1 delays ALS disease onset and progression in G85R transgenic mice

Human Molecular Genetics

Volumn 20, Issue 2, 2011, Pages 286-293

  Wang, Lijun ^a   Gutmann, David H ^b   Roos, Raymond P ^a  

^a UNIVERSITY OF CHICAGO MEDICAL CENTER   (United States)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN; SODIUM GLUCOSE COTRANSPORTER 1;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTE; CELL FUNCTION; CELL LOSS; CELL TYPE; DISEASE COURSE; DISEASE DURATION; FAMILIAL DISEASE; GENE DELETION; GENE MUTATION; GENE SILENCING; GLIOSIS; IMMUNOREACTIVITY; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; ASTROCYTES; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; EXCITATORY AMINO ACID TRANSPORTER 2; GENE EXPRESSION REGULATION, DEVELOPMENTAL; GENE KNOCKDOWN TECHNIQUES; HUMANS; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MUTATION; SPINAL CORD; SUPEROXIDE DISMUTASE; SURVIVAL ANALYSIS;

MUS; MUS MUSCULUS;

EID: 78650550891     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddq463     Document Type: Article

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