Mutant SOD1 linked to familial amyotrophic lateral sclerosis, but not wild-type SOD1, induces ER stress in COS7 cells and transgenic mice

Biochemical and Biophysical Research Communications

Volumn 303, Issue 2, 2003, Pages 496-503

  Tobisawa, Shinsuke ^a   Hozumi, Yasukazu ^a   Arawaka, Shigeki ^a   Koyama, Shingo ^a   Wada, Manabu ^a   Nagai, Makiko ^b   Aoki, Masashi ^b   Itoyama, Yasuto ^b   Goto, Kaoru ^a   Kato, Takeo ^a  

^a YAMAGATA UNIVERSITY   (Japan)

^b TOHOKU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Endoplasmic reticulum; Superoxide dismutase 1

Indexed keywords

CHAPERONE; COMPLEMENTARY DNA; GLUCOSE REGULATED PROTEIN 78; ISOENZYME; MUTANT PROTEIN; SUPEROXIDE DISMUTASE; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL FUNCTION; CELL STRAIN COS7; CONTROLLED STUDY; DISEASE ASSOCIATION; ENDOPLASMIC RETICULUM; FAMILIAL DISEASE; GENE MUTATION; GENETIC TRANSFECTION; MICROTUBULE; MITOCHONDRION; MOTONEURON; MOUSE; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN AGGREGATION; SPINAL CORD; SYMPTOM; TRANSGENIC MOUSE; WILD TYPE;

MUS MUSCULUS;

EID: 0346034856     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0006-291X(03)00353-X     Document Type: Article

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