Generation and characterisation of Friedreich ataxia YG8R mouse fibroblast and neural stem cell models

PLoS ONE

Volumn 9, Issue 2, 2014, Pages

  Sandi, Chiranjeevi ^a   Sandi, Madhavi ^a   Jassal, Harvinder ^a   Ezzatizadeh, Vahid ^a   Anjomani Virmouni, Sara ^a   Al Mahdawi, Sahar ^a   Pook, Mark A ^a  

^a BRUNEL UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ACONITATE HYDRATASE; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA;

ADULT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; ASTROCYTE; CELL DIFFERENTIATION; CELL VIABILITY; CONTROLLED STUDY; DISEASE COURSE; DNA METHYLATION; DOWN REGULATION; FIBROBLAST; FRIEDREICH ATAXIA; FXN GENE; GENE; IMMUNOCYTOCHEMISTRY; MISMATCH REPAIR; MOLECULAR DYNAMICS; MOLECULAR PATHOLOGY; MOUSE; NERVE CELL; NEURAL STEM CELL; NONHUMAN; OLIGODENDROGLIA; OXIDATIVE STRESS; PGC 1ALPHA GENE; PHENOTYPE; POLYMERASE CHAIN REACTION; PROTEIN FUNCTION; SOD2 GENE; TRINUCLEOTIDE REPEAT;

ACONITATE HYDRATASE; ANIMALS; CELL DIFFERENTIATION; CELL SURVIVAL; CELLS, CULTURED; DISEASE MODELS, ANIMAL; DNA METHYLATION; DNA MISMATCH REPAIR; FIBROBLASTS; FRIEDREICH ATAXIA; HUMANS; MICE; MICE, TRANSGENIC; NEURAL STEM CELLS; OXIDATIVE STRESS; PRIMARY CELL CULTURE; TRANSCRIPTION FACTORS; TRANSCRIPTOME; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 84896741146     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0089488     Document Type: Article

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