SCOPUS 정보 검색 플랫폼

Volumn 256, Issue SUPPL. 1, 2009, Pages 18-24

Multicellular models of Friedreich ataxia

a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE (France)

Author keywords

C. elegans; Disease pathophysiology; Drosophila; Frataxin; Iron sulphur; Mitochondria; Mouse; Pre clinical drug evaluation

Indexed keywords

CREATINE KINASE; FRATAXIN; HISTONE DEACETYLASE INHIBITOR; IDEBENONE; IRON CHELATING AGENT; NEURON SPECIFIC ENOLASE; RECOMBINASE; SUPEROXIDE DISMUTASE;

CAENORHABDITIS ELEGANS; CLINICAL FEATURE; DROSOPHILA; EXPERIMENTAL MODEL; FRIEDREICH ATAXIA; GENE DELETION; GENE EXPRESSION; GENETIC CONSERVATION; HUMAN; HYPERTROPHIC CARDIOMYOPATHY; KNOCKOUT MOUSE; MOLECULAR EVOLUTION; NONHUMAN; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; REVIEW; RNA INTERFERENCE; TRANSGENE; TRINUCLEOTIDE REPEAT;

ANIMALS; CAENORHABDITIS ELEGANS; DISEASE MODELS, ANIMAL; DROSOPHILA; FRIEDREICH ATAXIA; HUMANS; IRON-BINDING PROTEINS; MICE; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 62549107492 PISSN: 03405354 EISSN: 14321459 Source Type: Journal
DOI: 10.1007/s00415-009-1004-1 Document Type: Review

Times cited : (39)

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* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.