Sticky DNA, a Self-associated Complex Formed at Long GAA·TTC Repeats in Intron 1 of the Frataxin Gene, Inhibits Transcription

Journal of Biological Chemistry

Volumn 276, Issue 29, 2001, Pages 27171-27177

  Sakamoto, Naoaki ^a   Ohshima, Keiichi ^b   Montermini, Laura ^b   Pandolfo, Massimo ^b   Wells, Robert D ^a  

^a TEXAS A AND M HEALTH SCIENCE CENTER   (United States)

^b CENTRE HOSPITALIER DE L UNIVERSITÉ DE MONTRÉAL   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEXATION; ENZYME INHIBITION; PATIENT TREATMENT; RNA;

TRANSCRIPTION;

DNA;

DNA; FRATAXIN; GLYCYLALANYLALANINE; MESSENGER RNA; NUCLEOTIDE; RNA POLYMERASE; THREONYLTHREONYLCYSTEINE; UNCLASSIFIED DRUG; DNA DIRECTED RNA POLYMERASE; IRON BINDING PROTEIN; PHOSPHOTRANSFERASE;

ARTICLE; AUTOSOMAL RECESSIVE DISORDER; COMPLEX FORMATION; DEGENERATIVE DISEASE; DNA STRUCTURE; DNA TEMPLATE; DNA TRANSCRIPTION; ENZYME BINDING; FRIEDREICH ATAXIA; HUMAN; HUMAN CELL; INTRON; NONHUMAN; NUCLEOTIDE REPEAT; PLASMID; PRIORITY JOURNAL; RNA SYNTHESIS; TRANSCRIPTION REGULATION; DRUG ANTAGONISM; GENETIC TRANSCRIPTION; GENETICS; METABOLISM; PHYSIOLOGY;

ATAXIA;

DNA; DNA-DIRECTED RNA POLYMERASES; INTRONS; IRON-BINDING PROTEINS; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); TRANSCRIPTION, GENETIC;

EID: 0035920101     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M101879200     Document Type: Article

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