Frataxin: A protein in search for a function

Journal of Neurochemistry

Volumn 126, Issue SUPPL.1, 2013, Pages 43-52

  Pastore, Annalisa ^a   Puccio, Helene ^b,c,d,e  

^a NATIONAL INSTITUTE FOR MEDICAL RESEARCH   (United Kingdom)

^b INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^c INSERM   (France)

^d UNIVERSITÉ DE STRASBOURG   (France)

^e The Collège de France   (France)

Author keywords

Friedreich's ataxia; iron metabolism; mitochondria; oxidative stress

Indexed keywords

FRATAXIN; IRON BINDING PROTEIN; IRON SULFUR PROTEIN; MUTANT PROTEIN;

CELLULAR DISTRIBUTION; FRIEDREICH ATAXIA; HUMAN; IRON METABOLISM; MITOCHONDRION; MOLECULAR MECHANICS; NEUROPATHOLOGY; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; PROTEIN STRUCTURE; PROTEIN SYNTHESIS; REVIEW;

FRIEDREICH'S ATAXIA; IRON METABOLISM; MITOCHONDRIA; OXIDATIVE STRESS;

AMINO ACID SEQUENCE; ANIMALS; HUMANS; IRON; IRON-BINDING PROTEINS; MITOCHONDRIA; MOLECULAR CHAPERONES; MOLECULAR SEQUENCE DATA; MUTATION; PROTEIN CONFORMATION; SULFUR;

EID: 84880346984     PISSN: 00223042     EISSN: 14714159     Source Type: Journal    
DOI: 10.1111/jnc.12220     Document Type: Review

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