Robust reprogramming of Ataxia-Telangiectasia patient and carrier erythroid cells to induced pluripotent stem cells

Stem Cell Research

Volumn 17, Issue 2, 2016, Pages 296-305

  Bhatt, Niraj ^a   Ghosh, Rajib ^a   Roy, Sanchita ^a   Gao, Yongxing ^b   Armanios, Mary ^a   Cheng, Linzhao ^b   Franco, Sonia ^a  

^a JOHNS HOPKINS UNIVERSITY   (United States)

^b JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Ataxia Telangiectasia; ATM; induced pluripotent stem cells; radiation; telomere; teratoma

Indexed keywords

ATM PROTEIN; PROTEIN BCL XL; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG; YAMANAKA FACTOR; ATM PROTEIN, HUMAN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; ATAXIA TELANGIECTASIA; CASE REPORT; CELL DIVISION; CELL ELONGATION; CELL LINEAGE; CHILD; CONTROLLED STUDY; EPISOME; ERYTHROBLAST; ERYTHROID CELL; FEEDER CELL; FEMALE; GENE EXPRESSION; HAPLOINSUFFICIENCY; HUMAN; HUMAN CELL; IN VITRO STUDY; IN VIVO STUDY; INDUCED PLURIPOTENT STEM CELL; KARYOTYPE; MALE; MOUSE; NERVE CELL DIFFERENTIATION; NEURAL STEM CELL; NONHUMAN; NUCLEAR REPROGRAMMING; PRIORITY JOURNAL; SCHOOL CHILD; TELOMERE; TELOMERE LENGTH; TERATOMA; XENOGRAFT; ADOLESCENT; ANIMAL; C57BL MOUSE; CELL DIFFERENTIATION; CELL LINE; CYTOLOGY; DNA MUTATIONAL ANALYSIS; GENETICS; INDIRECT FLUORESCENT ANTIBODY TECHNIQUE; METABOLISM; NUCLEOTIDE SEQUENCE; PATHOLOGY; TELOMERE SHORTENING; TRANSPLANTATION;

ADOLESCENT; ANIMALS; ATAXIA TELANGIECTASIA; ATAXIA TELANGIECTASIA MUTATED PROTEINS; BASE SEQUENCE; CELL DIFFERENTIATION; CELL LINE; CELL LINEAGE; CELLULAR REPROGRAMMING; DNA MUTATIONAL ANALYSIS; ERYTHROID CELLS; FLUORESCENT ANTIBODY TECHNIQUE, INDIRECT; HUMANS; INDUCED PLURIPOTENT STEM CELLS; KARYOTYPE; MALE; MICE; MICE, INBRED C57BL; NEURAL STEM CELLS; TELOMERE; TELOMERE SHORTENING; TERATOMA; TRANSCRIPTION FACTORS;

EID: 84985021251     PISSN: 18735061     EISSN: 18767753     Source Type: Journal    
DOI: 10.1016/j.scr.2016.08.006     Document Type: Article

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