Mitochondrial Lon protease in human disease and aging: Including an etiologic classification of Lon-related diseases and disorders

Free Radical Biology and Medicine

Volumn 100, Issue , 2016, Pages 188-198

  Bota, Daniela A ^a   Davies, Kelvin J A ^b,c  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF SOUTHERN CALIFORNIA   (United States)

^c UNIVERSITY OF SOUTHERN CALIFORNIA   (United States)

Author keywords

Aging; Cancer; Lon; Mitochondria; Mitochondrial diseases; Mitochondrial DNA; Neurodegeneration; Proteolysis

Indexed keywords

5 AMINOLEVULINATE SYNTHASE; ANTI HUMAN IMMUNODEFICIENCY VIRUS AGENT; CHAPERONE; DNA BINDING PROTEIN; ENDOPEPTIDASE LA; MITOCHONDRIAL DNA; MITOCHONDRIAL ENZYME; STEROIDOGENIC ACUTE REGULATORY PROTEIN; TOXIN; ADENOSINE TRIPHOSPHATE DEPENDENT PROTEINASE; LONP1 PROTEIN, HUMAN; MITOCHONDRIAL PROTEIN;

AGING; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; BLADDER CANCER; BRAIN ISCHEMIA; BRAIN MALFORMATION; CANCER THERAPY; CEREBRAL OCULAR DENTAL AURICULAR SKELETAL ANOMALIES SYNDROME; CEREBROVASCULAR ACCIDENT; COLON CANCER; DRUG EXPOSURE; DRUG INDUCED DISEASE; ENVIRONMENTAL EXPOSURE; ENZYME ANALYSIS; ENZYME REGULATION; ENZYME STRUCTURE; EXTERNAL EAR MALFORMATION; EYE MALFORMATION; FAMILIAL DISEASE; FRIEDREICH ATAXIA; GENETIC DISORDER; GLIOBLASTOMA; HEART FAILURE; HEART MUSCLE ISCHEMIA; HELA CELL LINE; HIGHLY ACTIVE ANTIRETROVIRAL THERAPY; HINDLIMB UNLOADING; HUMAN; HUMAN IMMUNODEFICIENCY VIRUS INFECTION; INSULIN RESISTANCE; LEUKEMIA; LIPODYSTROPHY; LIVER DISEASE; MALIGNANT TRANSFORMATION; MELAS SYNDROME; MUSCLE DENERVATION; MUSCLE REGENERATION; NEUROLOGIC DISEASE; NONHUMAN; PARKINSON DISEASE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN METABOLISM; PROTEIN STRUCTURE; SKELETON MALFORMATION; STEROIDOGENESIS; TOOTH MALFORMATION; UTERINE CERVIX CANCER; METABOLISM; MITOCHONDRION; PHYSIOLOGY;

AGING; ATP-DEPENDENT PROTEASES; DNA, MITOCHONDRIAL; HUMANS; MITOCHONDRIA; MITOCHONDRIAL PROTEINS;

EID: 84979231413     PISSN: 08915849     EISSN: 18734596     Source Type: Journal    
DOI: 10.1016/j.freeradbiomed.2016.06.031     Document Type: Review

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