Advances in the pathogenesis of primary and secondary haemophagocytic lymphohistiocytosis: Differences and similarities

British Journal of Haematology

Volumn 174, Issue 2, 2016, Pages 203-217

  Brisse, Ellen ^a   Wouters, Carine H ^b   Matthys, Patrick ^a  

^a REGA INSTITUTE FOR MEDICAL RESEARCH   (Belgium)

^b UNIVERSITY OF LEUVEN   (Belgium)

Author keywords

Genetics; Haemophagocytic lymphohistiocytosis; Haemophagocytic syndrome; Macrophage activation syndrome; Pathogenesis

Indexed keywords

ALARMIN;

ANTIGEN PRESENTATION; AUTOIMMUNE DISEASE; AUTOINFLAMMATORY DISEASE; BACTERIAL INFECTION; CD8+ T LYMPHOCYTE; CELL MEDIATED CYTOTOXICITY; CYTOKINE STORM; FAMILIAL DISEASE; GENOTYPE PHENOTYPE CORRELATION; HEMOPHAGOCYTIC SYNDROME; HUMAN; IMMUNE DEFICIENCY; IMMUNOPATHOGENESIS; LYMPHOPROLIFERATIVE DISEASE; MALIGNANT NEOPLASTIC DISEASE; MYCOSIS; NATURAL KILLER CELL; NONHUMAN; PARASITOSIS; PRIMARY HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; PRIORITY JOURNAL; REGULATORY T LYMPHOCYTE; REVIEW; SECONDARY HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; VIRUS INFECTION; X CHROMOSOME LINKED DISORDER;

EID: 84978152261     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/bjh.14147     Document Type: Review

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