The syndrome of hemophagocytic lymphohistiocytosis in primary immunodeficiencies: Implications for differential diagnosis and pathogenesis

Haematologica

Volumn 100, Issue 7, 2015, Pages 978-988

  Bode, Sebastian F N ^a   Ammann, Sandra ^a,b   Al Herz, Waleed ^c   Bataneant, Mihaela ^d   Dvorak, Christopher C ^e   Gehring, Stephan ^f   Gennery, Andrew ^g   Gilmour, Kimberly C ^h   Gonzalez Granado, Luis I ⁱ   Groß Wieltsch, Ute ^j   Ifversen, Marianne ^k   Lingman Framme, Jenny ^l   Matthes Martin, Susanne ^m   Mesters, Rolf ⁿ   Meyts, Isabelle ^o   Van Montfrans, Joris M ^p   Schmid, Jana Pachlopnik ^q   Pai, Sung Yun ^r   Soler Palacin, Pere ^s   Schuermann, Uta ^t   Schuster, Volker ^u   Seidel, Markus G ^v   Speckmann, Carsten ^a   Stepensky, Polina ^w   Sykora, Karl Walter ^x   Tesi, Bianca ^y   Vraetz, Thomas ^a   Waruiru, Catherine ^z   Bryceson, Yenan T ^y   Moshous, Despina ^aa   Lehmberg, Kai ^ab   Jordan, Michael B ^ac   Ehl, Stephan ^a   more..

^a UNIVERSITY OF FREIBURG   (Germany)

^b UNIVERSITY OF FREIBURG   (Germany)

^c KUWAIT UNIVERSITY   (Kuwait)

^d VICTOR BABES UNIVERSITY OF MEDICINE AND PHARMACY   (Romania)

^e UNIVERSITY OF CALIFORNIA   (United States)

^f Center for Pediatrics and Adolescent Medicine   (Germany)

^g NEWCASTLE UNIVERSITY   (United Kingdom)

^h GREAT ORMOND STREET HOSPITAL   (United Kingdom)

ⁱ HOSPITAL UNIVERSITARIO 12 DE OCTUBRE   (Spain)

^j OLGAHOSPITAL   (Germany)

^k University of Copenhagen   (Denmark)

^l Maxillofacial Unit   (Sweden)

^m ST ANNA CHILDREN S HOSPITAL   (Austria)

ⁿ UNIVERSITY HOSPITAL MÜNSTER   (Germany)

^o UNIVERSITY HOSPITALS LEUVEN   (Belgium)

^p UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^q UNIVERSITY CHILDREN S HOSPITAL   (Switzerland)

^r BOSTON CHILDREN S HOSPITAL   (United States)

^s HOSPITAL UNIVERSITARI VALL D HEBRON   (Spain)

^t UNIVERSITY OF WITTEN HERDECKE   (Germany)

^u UNIVERSITY OF LEIPZIG   (Germany)

^v MEDICAL UNIVERSITY OF GRAZ   (Austria)

^w HADASSAH HEBREW UNIVERSITY MEDICAL CENTER   (Israel)

^x HANNOVER MEDICAL SCHOOL   (Germany)

^y KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^z SHEFFIELD CHILDREN S HOSPITAL   (United Kingdom)

^aa HÔPITAL NECKER ENFANTS MALADES   (France)

^ab UNIVERSITY OF HAMBURG   (Germany)

^ac UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

more..

Author keywords

[No Author keywords available]

Indexed keywords

CORTICOSTEROID; CYCLOSPORIN; FERRITIN; IMMUNOGLOBULIN; RITUXIMAB; IMMUNOLOGIC FACTOR; STEROID;

ARTICLE; BACTERIAL INFECTION; CD25 T LYMPHOCYTE; CHRONIC GRANULOMATOUS DISEASE; CONTROLLED STUDY; GENETIC ANALYSIS; HEMOPHAGOCYTIC SYNDROME; HUMAN; IMMUNE DEFICIENCY; INFECTION; MAJOR CLINICAL STUDY; NATURAL KILLER CELL; T LYMPHOCYTE; TREATMENT OUTCOME; VIRUS INFECTION; ADOLESCENT; ADULT; BACTERIAL INFECTIONS; CHILD; CLINICAL TRIAL; COMPLICATION; DIFFERENTIAL DIAGNOSIS; DRUG EFFECTS; EUROPE; FEMALE; IMMUNOLOGIC DEFICIENCY SYNDROMES; IMMUNOLOGY; INFANT; LEISHMANIASIS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; LYMPHOPROLIFERATIVE DISORDERS; MALE; MULTICENTER STUDY; MYCOSES; NEWBORN; NOMENCLATURE; OPPORTUNISTIC INFECTIONS; PATHOLOGY; PRESCHOOL CHILD; REGISTER; VIRUS DISEASES;

ADOLESCENT; ADULT; BACTERIAL INFECTIONS; CHILD; CHILD, PRESCHOOL; DIAGNOSIS, DIFFERENTIAL; EUROPE; FEMALE; HUMANS; IMMUNOGLOBULINS, INTRAVENOUS; IMMUNOLOGIC DEFICIENCY SYNDROMES; IMMUNOLOGIC FACTORS; INFANT; INFANT, NEWBORN; KILLER CELLS, NATURAL; LEISHMANIASIS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; LYMPHOPROLIFERATIVE DISORDERS; MALE; MYCOSES; OPPORTUNISTIC INFECTIONS; REGISTRIES; STEROIDS; T-LYMPHOCYTES; TERMINOLOGY AS TOPIC; VIRUS DISEASES;

EID: 84936095269     PISSN: 03906078     EISSN: 15928721     Source Type: Journal    
DOI: 10.3324/haematol.2014.121608     Document Type: Article

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