First characterization of platelet secretion defect in patients with familial hemophagocytic lymphohistiocytosis type 3 (FHL-3)

Blood

Volumn 125, Issue 2, 2015, Pages 412-414

  Nakamura, Lea ^a   Bertling, Anne ^b   Brodde, Martin F ^b   Stadt, Udo Zur ^c   Schulz, Ansgar S ^d   Ammann, Sandra ^e   Sandrock Lang, Kirstin ^a   Beutel, Karin ^f   Zieger, Barbara ^a   Kehrel, Beate E ^b  

^a UNIVERSITY OF FREIBURG   (Germany)

^b UNIVERSITY OF MÜNSTER   (Germany)

^c UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

^d UNIVERSITY HOSPITAL ULM   (Germany)

^e UNIVERSITY OF FREIBURG   (Germany)

^f UNIVERSITY HOSPITAL MÜNSTER   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; COLLAGEN; THROMBIN; THROMBIN RECEPTOR ACTIVATING PEPTIDE; MEMBRANE PROTEIN; UNC13D PROTEIN, HUMAN;

ARTICLE; CASE REPORT; CYTOTOXIC T LYMPHOCYTE; FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS TYPE 3; FLOW CYTOMETRY; GENE; GENE MUTATION; GRAFT FAILURE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HEMOPHAGOCYTIC SYNDROME; HUMAN; MALE; NATURAL KILLER CELL; PLATELET-RICH PLASMA CELL; PRIORITY JOURNAL; PROTEIN DEPLETION; PROTEIN SECRETION; THROMBOCYTE ANOMALY; THROMBOCYTE COUNT; THROMBOCYTE FUNCTION; THROMBOCYTE RELEASE REACTION; UNC13D GENE; GENETICS; INFANT; METABOLISM; MUTATION; PATHOLOGY; SECRETION (PROCESS); THROMBOCYTE;

BLOOD PLATELETS; FLOW CYTOMETRY; HUMANS; INFANT; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MEMBRANE PROTEINS; MUTATION;

EID: 84920973155     PISSN: 00064971     EISSN: 15280020     Source Type: Journal    
DOI: 10.1182/blood-2014-07-587568     Document Type: Article

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