Recent studies of ovine neuronal ceroid lipofuscinoses from BARN, the Batten Animal Research Network

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1852, Issue 10, 2015, Pages 2279-2286

  Palmer, David N ^a,e   Neverman, Nicole J ^b,e   Chen, Jarol Z ^a,e   Chang, Chia Tien ^c,e   Houweling, Peter J ^d,e   Barry, Lucy A ^a,e   Tammen, Imke ^c,e   Hughes, Stephanie M ^b,e   Mitchell, Nadia L ^a,e  

^a LINCOLN UNIVERSITY   (New Zealand)

^b UNIVERSITY OF OTAGO   (New Zealand)

^c UNIVERSITY OF SYDNEY   (Australia)

^d ROYAL CHILDREN'S HOSPITAL   (Australia)

^e Batten Animal Research Network (BARN)   (New Zealand)

Author keywords

Animal models; Batten Disease; CLN5; CLN6; Disease associated cardiology; Gene therapy; NCLs; Neural cultures; Neurodegeneration; Neuroinflammation; Neuroinflammatory pathway; Neuronal ceroid lipofuscinoses

Indexed keywords

BIOLOGICAL MARKER; CALNEXIN; CATHEPSIN D; LENTIVIRUS VECTOR; MINOCYCLINE; PARVOVIRUS VECTOR; PROTEIN; PROTEIN CLN6; PROTEIN THIOESTERASE 1; TRIPEPTIDYL PEPTIDASE I; UNCLASSIFIED DRUG;

ANTIINFLAMMATORY ACTIVITY; ASTROCYTOSIS; CELL CULTURE; CELL SURVIVAL; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; GENE MUTATION; GENE THERAPY; GLIA CELL; HISTOPATHOLOGY; HUMAN; IMMUNOPATHOLOGY; IN VITRO STUDY; IN VIVO STUDY; LYMPHOCYTIC INFILTRATION; LYSOSOME; NERVE CELL; NERVE CELL LESION; NERVE CELL NECROSIS; NERVOUS SYSTEM INFLAMMATION; NEURONAL CEROID LIPOFUSCINOSIS; NEUROPATHOLOGY; NONHUMAN; OVINE MODEL; OXIDATIVE STRESS; PRIORITY JOURNAL; PROMOTER REGION; REVIEW; RNA SEQUENCE; TRANSCRIPTOMICS;

EID: 84940793201     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2015.06.013     Document Type: Review

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