Location and connectivity determine GABAergic interneuron survival in the brains of South Hampshire sheep with CLN6 neuronal ceroid lipofuscinosis

Neurobiology of Disease

Volumn 32, Issue 1, 2008, Pages 50-65

  Oswald, Manfred J ^a,b   Palmer, David N ^a   Kay, Graham W ^a   Barwell, Karen J ^a   Cooper, Jonathan D ^b  

^a LINCOLN UNIVERSITY   (New Zealand)

^b Centre for the Cellular Basis of Behaviour   (United Kingdom)

Author keywords

Batten disease; CLN6; GABAergic interneurons; Lysosomal storage disease; Neuronal ceroid lipofuscinosis; Ovine model

Indexed keywords

4 AMINOBUTYRIC ACID RECEPTOR; NEUROPEPTIDE Y; PARVALBUMIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ARTICLE; BRAIN DISEASE; BRAIN REGION; CELL LOSS; CELL SURVIVAL; CONTROLLED STUDY; IMMUNOHISTOCHEMISTRY; LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; SHEEP;

ANIMALS; BRAIN; CELL SURVIVAL; GAMMA-AMINOBUTYRIC ACID; INTERNEURONS; MEMBRANE PROTEINS; NEURAL PATHWAYS; NEURONAL CEROID-LIPOFUSCINOSES; NEW ZEALAND; PHENOTYPE; SHEEP, DOMESTIC;

EID: 51549114197     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2008.06.004     Document Type: Article

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