Progressive conduction defects and cardiac death in late infantile neuronal ceroid lipofuscinosis

Developmental Medicine and Child Neurology

Volumn 54, Issue 7, 2012, Pages 663-666

  Fukumura, Shinobu ^a   Saito, Yoshiaki ^a   Saito, Takashi ^a   Komaki, Hirofumi ^a   Nakagawa, Eiji ^a   Sugai, Kenji ^a   Sasaki, Masayuki ^a   Oka, Akira ^b   Takamisawa, Itaru ^c  

^a NATIONAL INSTITUTE OF MENTAL HEALTH   (Japan)

^b KYORIN UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^c SAKAKIBARA HEART INSTITUTE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ATROPINE; ISOPRENALINE; POTASSIUM; SELENIUM;

ADULT; ARTICLE; ATAXIA; ATRIOVENTRICULAR BLOCK; BRADYCARDIA; BRAIN ATROPHY; BRONCHITIS; CASE REPORT; CEREBELLUM ATROPHY; COGNITIVE DEFECT; DISEASE COURSE; ELECTROCARDIOGRAPHY; ELECTROENCEPHALOGRAPHY; FEMALE; GENERALIZED EPILEPSY; HEART ATRIUM FIBRILLATION; HEART DEATH; HEART LEFT ANTERIOR BUNDLE BRANCH BLOCK; HEART MUSCLE CONDUCTION DISTURBANCE; HEART RIGHT BUNDLE BRANCH BLOCK; HEART VENTRICLE FIBRILLATION; HUMAN; HYPOKALEMIA; INTELLECTUAL IMPAIRMENT; MENTAL DETERIORATION; MYOCLONUS; NEURONAL CEROID LIPOFUSCINOSIS; NEURONAL CEROID LIPOFUSCINOSIS LATE INFANTILE TYPE; PHOTOSENSITIVITY; PRIORITY JOURNAL; SKIN BIOPSY; SUPRAVENTRICULAR TACHYCARDIA;

ADULT; ARRHYTHMIAS, CARDIAC; ATRIAL FIBRILLATION; ATRIOVENTRICULAR BLOCK; BRADYCARDIA; CHILD; DISEASE PROGRESSION; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAPHY; ELECTROENCEPHALOGRAPHY; ENTERAL NUTRITION; FATAL OUTCOME; FEMALE; HEART CONDUCTION SYSTEM; HUMANS; LIPIDS; MALE; MYOCARDIUM; NEURONAL CEROID-LIPOFUSCINOSES; TACHYCARDIA, SUPRAVENTRICULAR; VENTRICULAR FIBRILLATION;

EID: 84862320992     PISSN: 00121622     EISSN: 14698749     Source Type: Journal    
DOI: 10.1111/j.1469-8749.2011.04170.x     Document Type: Article

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