Enhanced expression of manganese-dependent superoxide dismutase in human and sheep CLN6 tissues

Biochemical Journal

Volumn 376, Issue 2, 2003, Pages 369-376

  Heine, Claudia ^a   Tyynelä, Jaana ^b   Cooper, Jonathan D ^c   Palmer, David N ^d   Elleder, Milan ^e   Kohlschütter, Alfried ^a   Braulke, Thomas ^a  

^a UNIVERSITY OF HAMBURG   (Germany)

^b UNIVERSITY OF HELSINKI   (Finland)

^c KING'S COLLEGE LONDON   (United Kingdom)

^d LINCOLN UNIVERSITY   (New Zealand)

^e Charles University in Prague and General University Hospital in Prague   (Czech Republic)

Author keywords

Fluorescence microscopy; Lysosomal storage disorder; Manganese dependent superoxide dismutase (MnSOD); Neurodegeneration; Neuronal ceroid lipofuscinosis; Oxidative stress

Indexed keywords

CELLS; DEGRADATION; DISEASES; FLUORESCENCE; GENES; IMMUNOLOGY; MANGANESE; PATHOLOGY; PROTEINS;

IMMUNOBLOTTING;

HUMAN ENGINEERING;

CYTOKINE; GENE PRODUCT; MANGANESE SUPEROXIDE DISMUTASE; MESSENGER RNA; PROTEIN;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; BRAIN; CONTROLLED STUDY; CYTOKINE PRODUCTION; FIBROBLAST; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOFLUORESCENCE MICROSCOPY; IMMUNOHISTOCHEMISTRY; MUTATION; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; OXIDATIVE STRESS; PHOSPHORYLATION; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SHEEP; TWO DIMENSIONAL ELECTROPHORESIS;

ANIMALS; BRAIN; CELLS, CULTURED; FIBROBLASTS; HUMANS; IMMUNOHISTOCHEMISTRY; MEMBRANE PROTEINS; MITOCHONDRIA; MUTATION; NEURONAL CEROID-LIPOFUSCINOSES; RNA, MESSENGER; SUPEROXIDE DISMUTASE;

ANIMALIA; OVIS ARIES;

EID: 0346887114     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/BJ20030598     Document Type: Article

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