Adrenoleukodystrophy protein-deficient mice represent abnormality of very long chain fatty acid metabolism

Biochemical and Biophysical Research Communications

Volumn 232, Issue 3, 1997, Pages 631-636

  Kobayashi, Takuro ^a   Shinnoh, Nobue ^a   Kondo, Akira ^b   Yamada, Takeshi ^a  

^a KYUSHU UNIVERSITY   (Japan)

^b Kikuchi National Hospital Division of Clinical Research   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN; CONTROLLED STUDY; ELECTRON MICROSCOPY; FATTY ACID METABOLISM; FIBROBLAST; GENE TARGETING; IMMUNOBLOTTING; KIDNEY; LIVER; LIVER CELL; LUNG; MICROSCOPY; MOUSE; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SPINAL CORD;

EID: 0031587790     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1006/bbrc.1997.6340     Document Type: Article

References (16)

1. Moser H. W., Moser A. B. The Metabolic Basis of Inherited Disease. 1989;McGraw-Hill, New York. p. 1511-1532.
2. Igarashi M., Schaumburg H. H., Powers J., Kishimoto Y., Kolodny E., Suzuki K. J. Neurochem. 26:1976;851-860.
3. Mosser J., Douar A-M., Sarde C-O., Kioschis P., Feil R., Moser H., Poustka A-M., Mandel J-L., Aubourg P. Nature. 361:1993;726-730.
4. Laemmli U. K. Nature. 227:1970;680-685.
5. Yasutake T., Yamada T., Furuya H., Shinnoh N., Goto I., Kobayashi T. Molecular analysis of X-linked adrenoleukodystrophy patients. J. Neurol. Sci. 131:1995;58-64.
6. Hashimoto T., Kuwabara T., Usuda N., Nagata T. J. Biochem. 100:1986;301-310.
7. Shinnoh N., Yamada T., Yoshimura T., Furuya H., Yoshida Y., Suzuki Y., Shimozawa N., Orii T., Kobayashi T. Biochem. Biophys. Res. Commun. 210:1995;830-836.
8. Kobayashi T., Katayama M., Suzuki S., Tomoda H., Goto I., Kuroiwa Y. J. Neurol. 230:1983;209-215.
9. Folch J., Lees M., Sloane Stanley G. H. J. Biol. Chem. 226:1957;497-509.
10. Suzuki Y., Shimozawa N., Yajima S., Yamaguchi S., Orii T., Hashimoto T. Biochem. Pharmacol. 41:1991;453-456.
11. Mosser J., Lutz Y., Stoeckel M. E., Sarde C. O., Kretz C., Douar A. M., Lopez J., Aubourg P., Mandel J.-L. Hum. Mol. Genet. 3:1994;265-271.
12. Kobayashi T., Yamada T., Yasutake T, Shinnoh N., Goto I., Iwaki T. Biochem. Biophys. Res. Commun. 201:1994;1029-1034.
13. Contreras M., Mosser J., Mandel J. L., Aubourg P., Singh I. FEBS lett. 344:1994;211-215.
14. Cartier N., Lopez J., Moullier P., Rocchiccioli F., Rolland M.-O., Jorge P., Mosser J., Mandel J.-L., Bougneres P.-F., Danos O., Aubourg P. Proc. Natl. Acad. Sci. USA. 92:1995;1674-1678.
15. Fan C.-Y., Pan J., Chu R., Lee D., Kluckman K. D., Usuda N., Singh I., Yeldandi A. V., Rao M. S., Maeda N., Reddy J. K. J. Biol. Chem. 271:1996;24698-24710.
16. Shani N., Valle D. Proc. Natl. Acad. Sci. USA. 93:1996;11901-11906.