Defective mitochondrial disulfide relay system, altered mitochondrial morphology and function in Huntington's disease

Human Molecular Genetics

Volumn 22, Issue 5, 2013, Pages 989-1004

  Napoli, Eleonora ^a   Wong, Sarah ^a   Hung, Connie ^a   Ross Inta, Catherine ^a   Bomdica, Prithvi ^a   Giulivi, Cecilia ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; HUNTINGTIN; MITOCHONDRIAL DNA; MITOCHONDRIAL PROTEIN; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE);

ALLELE; ARTICLE; BIOLOGICAL MODEL; CELL FUNCTION; CELL STRUCTURE; CELLULAR, SUBCELLULAR AND MOLECULAR BIOLOGICAL PHENOMENA AND FUNCTIONS; COPY NUMBER VARIATION; ENZYME ACTIVITY; GENE DOSAGE; GENE EXPRESSION; GENE MUTATION; HETEROZYGOSITY; HOMOZYGOSITY; HUNTINGTON CHOREA; MITOCHONDRIAL DISULFIDE RELAY SYSTEM; MITOCHONDRIAL DNA REPLICATION; MITOPHAGY; NERVE CELL DIFFERENTIATION; NERVE DEGENERATION; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; SELECTIVE AUTOPHAGY; STEM CELL;

ANIMALS; CELL DIFFERENTIATION; CORPUS STRIATUM; DNA, MITOCHONDRIAL; HUMANS; HUNTINGTON DISEASE; MALE; MICE; MITOCHONDRIA; MUTATION; NERVE TISSUE PROTEINS; NEURONS; NUCLEAR PROTEINS; OXIDATIVE PHOSPHORYLATION; OXIDOREDUCTASES ACTING ON SULFUR GROUP DONORS; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 84873446708     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/dds503     Document Type: Article

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