Identification and Characterization of a Common Set of Complex I Assembly Intermediates in Mitochondria from Patients with Complex I Deficiency

Journal of Biological Chemistry

Volumn 278, Issue 44, 2003, Pages 43081-43088

  Antonicka, Hana ^a   Ogilvie, Isla ^a   Taivassalo, Tanja ^b   Anitori, Roberto P ^e   Haller, Ronald G ^b,c   Vissing, John ^d   Kennaway, Nancy G ^e   Shoubridge, Eric A ^a  

^a MCGILL UNIVERSITY   (Canada)

^b PRESBYTERIAN HOSPITAL OF DALLAS   (United States)

^c UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^d UNIVERSITY OF COPENHAGEN   (Denmark)

^e OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CATALYSIS; CELLS; DNA; ENZYMES; PATIENT MONITORING;

ENZYME DEFICIENCY;

BIOLOGICAL ORGANS;

HOLOENZYME; MITOCHONDRIAL DNA; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE);

ADULT; ARTICLE; CASE REPORT; COMPLEX 1 DEFICIENCY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME DEFICIENCY; ENZYME SUBUNIT; FIBROBLAST; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOBLOTTING; MALE; MITOCHONDRION; NEUROSPORA; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL;

ADULT; ANIMALS; CATALYSIS; CELL NUCLEUS; CELLS, CULTURED; ELECTRON TRANSPORT COMPLEX I; ELECTROPHORESIS, GEL, TWO-DIMENSIONAL; ELECTROPHORESIS, POLYACRYLAMIDE GEL; FIBROBLASTS; HUMANS; HYBRID CELLS; IMMUNOBLOTTING; MALE; MICE; MITOCHONDRIA; MODELS, BIOLOGICAL; MUSCLES; NEUROSPORA; PROTEIN STRUCTURE, TERTIARY;

NEUROSPORA;

EID: 0242353332     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M304998200     Document Type: Article

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