FUS-related proteinopathies: Lessons from animal models

Brain Research

Volumn 1462, Issue , 2012, Pages 44-60

  Lanson Jr , Nicholas A ^a   Pandey, Udai Bhan ^a  

^a LOUISIANA STATE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Amyotrophic lateral sclerosis; Animal models; FUS; Neurodegeneration; TDP 43

Indexed keywords

FUSED IN SARCOMA PROTEIN; MESSENGER RNA; MICRORNA; PRION PROTEIN; RNA; RNA BINDING PROTEIN; RNA BINDING PROTEIN EWS; TAR DNA BINDING PROTEIN; TATA BINDING PROTEIN ASSOCIATED FACTOR 15; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; AMYOTROPHIC LATERAL SCLEROSIS; BIOGENESIS; CAENORHABDITIS ELEGANS; CELL NUCLEUS; CYTOPLASM; CYTOTOXICITY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; DROSOPHILA; EXPERIMENTAL MODEL; EXPERIMENTAL MOUSE; EXPERIMENTAL RAT; FRONTOTEMPORAL DEMENTIA; FUS RELATED PROTEINOPATHY; GAIN OF FUNCTION MUTATION; GENE FUNCTION; GENE STRUCTURE; HUMAN; LOSS OF FUNCTION MUTATION; NEUROPATHOLOGY; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN METHYLATION; PROTEIN MODIFICATION; PROTEIN MOTIF; PROTEIN PHOSPHORYLATION; PROTEIN RNA BINDING; REGULATORY MECHANISM; REVIEW; RNA METABOLISM; RNA PROCESSING; RNA SPLICING; RNA TRANSPORT; SPLICING DEFECT; TRANSCRIPTION REGULATION; YEAST; ZEBRA FISH;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CAENORHABDITIS ELEGANS; DISEASE MODELS, ANIMAL; DROSOPHILA; FRONTOTEMPORAL LOBAR DEGENERATION; HUMANS; MICE; NERVOUS SYSTEM DISEASES; PROTEIN PROCESSING, POST-TRANSLATIONAL; RATS; RNA-BINDING PROTEIN FUS; TDP-43 PROTEINOPATHIES; YEASTS; ZEBRAFISH;

ANIMALIA;

EID: 84862149644     PISSN: 00068993     EISSN: 18726240     Source Type: Journal    
DOI: 10.1016/j.brainres.2012.01.039     Document Type: Review

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