Superoxide dismutase 1 and tgSOD1G93A mouse spinal cord seed fibrils, suggesting a propagative cell death mechanism in amyotrophic lateral sclerosis

PLoS ONE

Volumn 5, Issue 5, 2010, Pages

  Chia, Ruth ^a   Tattum, M Howard ^a   Jones, Samantha ^a   Collinge, John ^a   Fisher, Elizabeth M C ^a   Jackson, Graham S ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

AMYLOID; COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN; MUTANT SUPEROXIDE DISMUTASE 1; UNCLASSIFIED DRUG; SUPEROXIDE DISMUTASE; THIAZOLE DERIVATIVE; THIOFLAVINE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL TISSUE; ARTICLE; CATALYSIS; CELL DEATH; CONTROLLED STUDY; GENE OVEREXPRESSION; IN VITRO STUDY; MOLECULAR STABILITY; MOUSE; NEUROPATHOLOGY; NONHUMAN; PROTEIN FOLDING; PROTEIN PHOSPHORYLATION; PROTEIN SYNTHESIS; SPINAL CORD; TRANSGENIC MOUSE; WILD TYPE; ANIMAL; CELL FRACTIONATION; ELECTRON MICROSCOPY; ENZYMOLOGY; HUMAN; KINETICS; METABOLISM; PATHOLOGY; PROTEIN STABILITY; TIME; ULTRASTRUCTURE;

MUS MUSCULUS;

AMYLOID; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL DEATH; HUMANS; KINETICS; MICE; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; PROTEIN STABILITY; SPINAL CORD; SUBCELLULAR FRACTIONS; SUPEROXIDE DISMUTASE; THIAZOLES; TIME FACTORS;

EID: 77956270117     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0010627     Document Type: Article

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