Neurodegeneration as a consequence of failed mitochondrial maintenance

Acta Neuropathologica

Volumn 123, Issue 2, 2012, Pages 157-171

  Karbowski, Mariusz ^a   Neutzner, Albert ^b  

^a UNIVERSITY OF MARYLAND SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF BASEL   (Switzerland)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; LIGASE; MITOCHONDRIAL DNA; MITOCHONDRIAL PROTEIN; MITOFUSIN 2; PROTEIN MARCH5; PROTEIN OPA1; REACTIVE OXYGEN METABOLITE; UBIQUITIN; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; AUTOSOMAL DOMINANT OPTIC ATROPHY; CELL DAMAGE; ENERGY YIELD; HEREDITARY MOTOR SENSORY NEUROPATHY; HEREDITARY MOTOR SENSORY NEUROPATHY TYPE 2A; HUMAN; MITOCHONDRIAL ENERGY TRANSFER; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; MITOPHAGY; MOLECULAR DYNAMICS; MUTATIONAL ANALYSIS; NERVE DEGENERATION; NONHUMAN; OPTIC NERVE DISEASE; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN PROCESSING; REVIEW; UBIQUITINATION;

ANIMALS; DNA, MITOCHONDRIAL; ENERGY METABOLISM; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MITOCHONDRIAL PROTEINS; NEURODEGENERATIVE DISEASES;

EID: 84857030799     PISSN: 00016322     EISSN: 14320533     Source Type: Journal    
DOI: 10.1007/s00401-011-0921-0     Document Type: Review

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