The m-AAA protease defective in hereditary spastic paraplegia controls ribosome assembly in mitochondria

Cell

Volumn 123, Issue 2, 2005, Pages 277-289

  Nolden, Mark ^a   Ehses, Sarah ^a   Koppen, Mirko ^a   Bernacchia, Andrea ^b,c   Rugarli, Elena I ^b,c   Langer, Thomas ^a  

^a UNIVERSITY OF COLOGNE   (Germany)

^b TELETHON INSTITUTE OF GENETICS AND MEDICINE TIGEM   (Italy)

^c DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ISOENZYME; MITOCHONDRIAL PROTEIN; PARAPLEGIN; PROTEINASE; RIBOSOME PROTEIN; UNCLASSIFIED DRUG;

ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; ENZYME DEFECT; HEREDITARY MOTOR SENSORY NEUROPATHY; MITOCHONDRION; MOUSE; MUTANT; NERVE FIBER DEGENERATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN PROCESSING; PROTEIN SYNTHESIS; REGULATORY MECHANISM; RIBOSOME; YEAST;

EID: 26844484821     PISSN: 00928674     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cell.2005.08.003     Document Type: Article

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