The serpinopathies: Studying serpin polymerization in vivo

Methods in Enzymology

Volumn 501, Issue , 2011, Pages 421-466

  Irving, James A ^a   Ekeowa, Ugo I ^a   Belorgey, Didier ^a   Haq, Imran ^a   Gooptu, Bibek ^b   Miranda, Elena ^c   Pérez, Juan ^d   Roussel, Benoit D ^a   Ordóñez, Adriana ^a   Dalton, Lucy E ^a   Thomas, Sally E ^a   Marciniak, Stefan J ^a,e   Parfrey, Helen ^e   Chilvers, Edwin R ^e   Teckman, Jeffrey H ^f   Alam, Sam ^e   Mahadeva, Ravi ^e   Rashid, S Tamir ^a,g   Vallier, Ludovic ^g   Lomas, David A ^a,e  

^a UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^b UNIVERSITY OF LONDON   (United Kingdom)

^c SAPIENZA UNIVERSITY OF ROME   (Italy)

^d UNIVERSITY OF MÁLAGA   (Spain)

^e UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^f SAINT LOUIS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^g UNIVERSITY OF CAMBRIDGE   (United Kingdom)

Author keywords

Animal models; Antitrypsin; Biochemistry; Cell biology; Cirrhosis; FENIB; Monoclonal antibodies; Neuroserpin; Serpin polymerization; Stem cell technology

Indexed keywords

ALPHA 1 ANTITRYPSIN; MONOCLONAL ANTIBODY; MUTANT PROTEIN; NEUROSERPIN; SERINE PROTEINASE INHIBITOR;

ARTICLE; AUTOSOMAL DOMINANT DISORDER; CYTOLOGY; DEMENTIA; ENDOPLASMIC RETICULUM; GENETIC DISORDER; HUMAN; LIVER CELL; LIVER CELL CARCINOMA; LIVER CIRRHOSIS; NEWBORN HEPATITIS; NONHUMAN; POINT MUTATION; POLYMERIZATION; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN FAMILY; PROTEIN POLYMERIZATION; PROTEIN STRUCTURE; STEM CELL;

ANIMALIA;

EID: 80955167666     PISSN: 00766879     EISSN: 15577988     Source Type: Book Series    
DOI: 10.1016/B978-0-12-385950-1.00018-3     Document Type: Chapter

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