The intracellular accumulation of polymeric neuroserpin explains the severity of the dementia FENIB

Human Molecular Genetics

Volumn 17, Issue 11, 2008, Pages 1527-1539

  Miranda, Elena ^a   Macleod, Ian ^a   Davies, Mark J ^a,b   Pérez, Juan ^a,b   Römisch, Karin ^c   Crowther, Damian C ^a   Lomas, David A ^a  

^a UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^b UNIVERSITY OF MÁLAGA   (Spain)

^c UNIVERSITY OF TRENTO   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

MONOCLONAL ANTIBODY; NEUROSERPIN; POLYMER;

ANIMAL CELL; ARTICLE; CELL LEVEL; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DEMENTIA; DISEASE SEVERITY; DROSOPHILA MELANOGASTER; FAMILIAL ENCEPHALOPATHY WITH NEUROSERPIN INCLUSION BODIES; FEMALE; GENE MUTATION; GENETIC TRANSFECTION; MOTOR DYSFUNCTION; MUTANT; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN LOCALIZATION;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; ANTIBODIES, MONOCLONAL; CERCOPITHECUS AETHIOPS; COS CELLS; DEMENTIA; DISEASE MODELS, ANIMAL; DROSOPHILA MELANOGASTER; ENDOPLASMIC RETICULUM; HUMANS; NEURONS; NEUROPEPTIDES; PC12 CELLS; POLYMERS; RATS; SERPINS; TRANSFECTION;

DROSOPHILA MELANOGASTER;

EID: 44349122437     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddn041     Document Type: Article

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